HRCT Diagnosis of Pleuroparenchymal fibroelastosis: Report of two cases
Pleuroparenchymal fibroelastosis (PPFE) is a rare idiopathic interstitial pneumonia that is often underdiagnosed on computed tomography scans. The disease process involves a combination of fibrosis involving the visceral pleura and fibroelastic changes within the subpleural lung parenchyma. Although...
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
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Elsevier
2021-06-01
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| Series: | Radiology Case Reports |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S1930043321001886 |
| _version_ | 1818590555565719552 |
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| author | Ali Morshid Amin Moshksar Aparna Das Alexander G. Duarte Diana Palacio Javier Villanueva-Meyer |
| author_facet | Ali Morshid Amin Moshksar Aparna Das Alexander G. Duarte Diana Palacio Javier Villanueva-Meyer |
| author_sort | Ali Morshid |
| collection | DOAJ |
| description | Pleuroparenchymal fibroelastosis (PPFE) is a rare idiopathic interstitial pneumonia that is often underdiagnosed on computed tomography scans. The disease process involves a combination of fibrosis involving the visceral pleura and fibroelastic changes within the subpleural lung parenchyma. Although definitive diagnosis is based on pathological evaluation, this is often not feasible and pattern recognition on CT as ''definite PPFE'' or ''consistent with PPFE'' is important given that sub group of patients will undergo rapid progression with clinical deterioration. |
| first_indexed | 2024-12-16T09:58:24Z |
| format | Article |
| id | doaj.art-d1242ba4bd1a48d290321602c7093eae |
| institution | Directory Open Access Journal |
| issn | 1930-0433 |
| language | English |
| last_indexed | 2024-12-16T09:58:24Z |
| publishDate | 2021-06-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Radiology Case Reports |
| spelling | doaj.art-d1242ba4bd1a48d290321602c7093eae2022-12-21T22:35:51ZengElsevierRadiology Case Reports1930-04332021-06-0116615641569HRCT Diagnosis of Pleuroparenchymal fibroelastosis: Report of two casesAli Morshid0Amin Moshksar1Aparna Das2Alexander G. Duarte3Diana Palacio4Javier Villanueva-Meyer5Department of Diagnostic Radiology, University of Texas Medical Branch, Galveston TX 77555Department of Diagnostic Radiology, University of Texas Medical Branch, Galveston TX 77555Department of Internal Medicine, University of Texas Medical Branch, Galveston TX 77555Department of Internal Medicine, University of Texas Medical Branch, Galveston TX 77555Department of Diagnostic Radiology, University of Texas Medical Branch, Galveston TX 77555Department of Diagnostic Radiology, University of Texas Medical Branch, Galveston TX 77555; Corresponding author.Pleuroparenchymal fibroelastosis (PPFE) is a rare idiopathic interstitial pneumonia that is often underdiagnosed on computed tomography scans. The disease process involves a combination of fibrosis involving the visceral pleura and fibroelastic changes within the subpleural lung parenchyma. Although definitive diagnosis is based on pathological evaluation, this is often not feasible and pattern recognition on CT as ''definite PPFE'' or ''consistent with PPFE'' is important given that sub group of patients will undergo rapid progression with clinical deterioration.http://www.sciencedirect.com/science/article/pii/S1930043321001886Chest radiologyIdiopathic interstitial pneumoniaPleuro parenchymal fibroelastosis |
| spellingShingle | Ali Morshid Amin Moshksar Aparna Das Alexander G. Duarte Diana Palacio Javier Villanueva-Meyer HRCT Diagnosis of Pleuroparenchymal fibroelastosis: Report of two cases Radiology Case Reports Chest radiology Idiopathic interstitial pneumonia Pleuro parenchymal fibroelastosis |
| title | HRCT Diagnosis of Pleuroparenchymal fibroelastosis: Report of two cases |
| title_full | HRCT Diagnosis of Pleuroparenchymal fibroelastosis: Report of two cases |
| title_fullStr | HRCT Diagnosis of Pleuroparenchymal fibroelastosis: Report of two cases |
| title_full_unstemmed | HRCT Diagnosis of Pleuroparenchymal fibroelastosis: Report of two cases |
| title_short | HRCT Diagnosis of Pleuroparenchymal fibroelastosis: Report of two cases |
| title_sort | hrct diagnosis of pleuroparenchymal fibroelastosis report of two cases |
| topic | Chest radiology Idiopathic interstitial pneumonia Pleuro parenchymal fibroelastosis |
| url | http://www.sciencedirect.com/science/article/pii/S1930043321001886 |
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