Renal lymphangiomatosis, a rare differential diagnosis for autosomal recessive polycystic kidney disease in pediatric patients
Renal lymphangiomatosis is a rare, benign malformation, characterized by developmental malformation of the perirenal, peripelvic, and intrarenal lymphatics. Radiologist knowledge of the unique radiological features of this entity helps patient's safety in terms of management. We study the case...
| Main Authors: | , , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Elsevier
2017-03-01
|
| Series: | Radiology Case Reports |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S193004331630276X |
| _version_ | 1818618748213395456 |
|---|---|
| author | Amna A. Kashgari, MD Nabil Ozair, MD Amin Al Zahrani, MD Mohammed O. Al Otibi, MD Khalid Al Fakeeh, MD |
| author_facet | Amna A. Kashgari, MD Nabil Ozair, MD Amin Al Zahrani, MD Mohammed O. Al Otibi, MD Khalid Al Fakeeh, MD |
| author_sort | Amna A. Kashgari, MD |
| collection | DOAJ |
| description | Renal lymphangiomatosis is a rare, benign malformation, characterized by developmental malformation of the perirenal, peripelvic, and intrarenal lymphatics. Radiologist knowledge of the unique radiological features of this entity helps patient's safety in terms of management. We study the case of a 27-month-old boy presented to the emergency department with upper respiratory tract infection. He had a high blood pressure and had been diagnosed earlier with autosomal recessive polycystic kidney disease based on renal ultrasound findings. Because the clinical presentation and laboratory work of the patient did not support the diagnosis of autosomal recessive polycystic kidney disease, further, extensive work-up was performed, which confirmed the diagnosis of renal lymphangiomatosis. This case report emphasizes the imaging features of this rare entity to promote early diagnosis and better patient care. |
| first_indexed | 2024-12-16T17:26:31Z |
| format | Article |
| id | doaj.art-d32894b177bd47cdb326d0dfea22337b |
| institution | Directory Open Access Journal |
| issn | 1930-0433 |
| language | English |
| last_indexed | 2024-12-16T17:26:31Z |
| publishDate | 2017-03-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Radiology Case Reports |
| spelling | doaj.art-d32894b177bd47cdb326d0dfea22337b2022-12-21T22:23:02ZengElsevierRadiology Case Reports1930-04332017-03-01121707210.1016/j.radcr.2016.11.016Renal lymphangiomatosis, a rare differential diagnosis for autosomal recessive polycystic kidney disease in pediatric patientsAmna A. Kashgari, MD0Nabil Ozair, MD1Amin Al Zahrani, MD2Mohammed O. Al Otibi, MD3Khalid Al Fakeeh, MD4Department of Medical Imaging, King Abdullah Specialized Children's Hospital, King Abdulaziz Medical City, Ministry of National Guard, PO Box 22490, Riyadh, KSADepartment of Medical Imaging, King Abdullah Specialized Children's Hospital, King Abdulaziz Medical City, Ministry of National Guard, PO Box 22490, Riyadh, KSADepartment of Medical Imaging, Intervention Radiology Section, King Abdullah Specialized Children's Hospital, King Abdulaziz Medical City, Ministry of National Guard, PO Box 22490, Riyadh, KSADepartment of Medical Imaging, Intervention Radiology Section, King Abdullah Specialized Children's Hospital, King Abdulaziz Medical City, Ministry of National Guard, PO Box 22490, Riyadh, KSADepartment of Pediatric, King Abdullah Specialized Children's Hospital, King Abdulaziz Medical City, Ministry of National Guard, PO Box 22490, Riyadh, KSARenal lymphangiomatosis is a rare, benign malformation, characterized by developmental malformation of the perirenal, peripelvic, and intrarenal lymphatics. Radiologist knowledge of the unique radiological features of this entity helps patient's safety in terms of management. We study the case of a 27-month-old boy presented to the emergency department with upper respiratory tract infection. He had a high blood pressure and had been diagnosed earlier with autosomal recessive polycystic kidney disease based on renal ultrasound findings. Because the clinical presentation and laboratory work of the patient did not support the diagnosis of autosomal recessive polycystic kidney disease, further, extensive work-up was performed, which confirmed the diagnosis of renal lymphangiomatosis. This case report emphasizes the imaging features of this rare entity to promote early diagnosis and better patient care.http://www.sciencedirect.com/science/article/pii/S193004331630276XUltrasoundMagnetic resonance imagingLymphangiomatosisKidney |
| spellingShingle | Amna A. Kashgari, MD Nabil Ozair, MD Amin Al Zahrani, MD Mohammed O. Al Otibi, MD Khalid Al Fakeeh, MD Renal lymphangiomatosis, a rare differential diagnosis for autosomal recessive polycystic kidney disease in pediatric patients Radiology Case Reports Ultrasound Magnetic resonance imaging Lymphangiomatosis Kidney |
| title | Renal lymphangiomatosis, a rare differential diagnosis for autosomal recessive polycystic kidney disease in pediatric patients |
| title_full | Renal lymphangiomatosis, a rare differential diagnosis for autosomal recessive polycystic kidney disease in pediatric patients |
| title_fullStr | Renal lymphangiomatosis, a rare differential diagnosis for autosomal recessive polycystic kidney disease in pediatric patients |
| title_full_unstemmed | Renal lymphangiomatosis, a rare differential diagnosis for autosomal recessive polycystic kidney disease in pediatric patients |
| title_short | Renal lymphangiomatosis, a rare differential diagnosis for autosomal recessive polycystic kidney disease in pediatric patients |
| title_sort | renal lymphangiomatosis a rare differential diagnosis for autosomal recessive polycystic kidney disease in pediatric patients |
| topic | Ultrasound Magnetic resonance imaging Lymphangiomatosis Kidney |
| url | http://www.sciencedirect.com/science/article/pii/S193004331630276X |
| work_keys_str_mv | AT amnaakashgarimd renallymphangiomatosisararedifferentialdiagnosisforautosomalrecessivepolycystickidneydiseaseinpediatricpatients AT nabilozairmd renallymphangiomatosisararedifferentialdiagnosisforautosomalrecessivepolycystickidneydiseaseinpediatricpatients AT aminalzahranimd renallymphangiomatosisararedifferentialdiagnosisforautosomalrecessivepolycystickidneydiseaseinpediatricpatients AT mohammedoalotibimd renallymphangiomatosisararedifferentialdiagnosisforautosomalrecessivepolycystickidneydiseaseinpediatricpatients AT khalidalfakeehmd renallymphangiomatosisararedifferentialdiagnosisforautosomalrecessivepolycystickidneydiseaseinpediatricpatients |