Pulmonary agenesis and respiratory failure in childhood
Pulmonary agenesis (PA) is a rare congenital anomaly, which may be unilateral or bilateral. Unilateral PA may be associated with nonspecific respiratory symptoms. We report the case of 5-month-old infant who presented a normal development until the age of 4 months when a respiratory infection caused...
| Main Authors: | , |
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| Format: | Article |
| Language: | English |
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University of São Paulo
2015-03-01
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| Series: | Autopsy and Case Reports |
| Subjects: | |
| Online Access: | http://www.revistas.usp.br/autopsy/article/view/98453 |
| _version_ | 1818390012107948032 |
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| author | Paula Vanessa Valverde Dinamarco Cesar Cilento Ponce |
| author_facet | Paula Vanessa Valverde Dinamarco Cesar Cilento Ponce |
| author_sort | Paula Vanessa Valverde Dinamarco |
| collection | DOAJ |
| description | Pulmonary agenesis (PA) is a rare congenital anomaly, which may be unilateral or bilateral. Unilateral PA may be associated with nonspecific respiratory symptoms. We report the case of 5-month-old infant who presented a normal development until the age of 4 months when a respiratory infection caused an acute respiratory distress syndrome with a fatal outcome. The autopsy findings depicted the right lung agenesis without any other concomitant malformation. Although respiratory symptoms represent frequent complaints in pediatrics, the aim of this study is not only to draw attention to the unilateral pulmonary agenesis as a possible underlying malformation in children who present recurrent and severe respiratory symptoms, but also to report a case diagnosed at autopsy. |
| first_indexed | 2024-12-14T04:50:51Z |
| format | Article |
| id | doaj.art-d3408d7f735c44e28aa1b24554cae5b2 |
| institution | Directory Open Access Journal |
| issn | 2236-1960 |
| language | English |
| last_indexed | 2024-12-14T04:50:51Z |
| publishDate | 2015-03-01 |
| publisher | University of São Paulo |
| record_format | Article |
| series | Autopsy and Case Reports |
| spelling | doaj.art-d3408d7f735c44e28aa1b24554cae5b22022-12-21T23:16:33ZengUniversity of São PauloAutopsy and Case Reports2236-19602015-03-015110.4322/acr.%y.9845388471Pulmonary agenesis and respiratory failure in childhoodPaula Vanessa Valverde Dinamarco0Cesar Cilento Ponce1Office of the Chief Medical Examiner, Santos/SPOffice of the Chief Medical Examiner, Santos/SPPulmonary agenesis (PA) is a rare congenital anomaly, which may be unilateral or bilateral. Unilateral PA may be associated with nonspecific respiratory symptoms. We report the case of 5-month-old infant who presented a normal development until the age of 4 months when a respiratory infection caused an acute respiratory distress syndrome with a fatal outcome. The autopsy findings depicted the right lung agenesis without any other concomitant malformation. Although respiratory symptoms represent frequent complaints in pediatrics, the aim of this study is not only to draw attention to the unilateral pulmonary agenesis as a possible underlying malformation in children who present recurrent and severe respiratory symptoms, but also to report a case diagnosed at autopsy.http://www.revistas.usp.br/autopsy/article/view/98453Lung agenesisRespiratory InsufficiencyAutopsy |
| spellingShingle | Paula Vanessa Valverde Dinamarco Cesar Cilento Ponce Pulmonary agenesis and respiratory failure in childhood Autopsy and Case Reports Lung agenesis Respiratory Insufficiency Autopsy |
| title | Pulmonary agenesis and respiratory failure in childhood |
| title_full | Pulmonary agenesis and respiratory failure in childhood |
| title_fullStr | Pulmonary agenesis and respiratory failure in childhood |
| title_full_unstemmed | Pulmonary agenesis and respiratory failure in childhood |
| title_short | Pulmonary agenesis and respiratory failure in childhood |
| title_sort | pulmonary agenesis and respiratory failure in childhood |
| topic | Lung agenesis Respiratory Insufficiency Autopsy |
| url | http://www.revistas.usp.br/autopsy/article/view/98453 |
| work_keys_str_mv | AT paulavanessavalverdedinamarco pulmonaryagenesisandrespiratoryfailureinchildhood AT cesarcilentoponce pulmonaryagenesisandrespiratoryfailureinchildhood |