Variation of usual interstitial pneumonia using HRCT in Scleroderma Patients

Progressive Systemic Sclerosis or Scleroderma is a systemic inflammation marked by endothelial damaged, fibrosis, and inflammation in skin, joints, and visceral organs. Pulmonary hypertension and interstitial pulmonary disease (Ssc-ILD) are the most reported pulmonary complications in scleroderma pa...

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Main Authors: Vally Wulani, Taufik Budianto, Mohamad Yanuar Amal
Format: Article
Language:English
Published: Elsevier 2022-02-01
Series:Radiology Case Reports
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S1930043321007731
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author Vally Wulani
Taufik Budianto
Mohamad Yanuar Amal
author_facet Vally Wulani
Taufik Budianto
Mohamad Yanuar Amal
author_sort Vally Wulani
collection DOAJ
description Progressive Systemic Sclerosis or Scleroderma is a systemic inflammation marked by endothelial damaged, fibrosis, and inflammation in skin, joints, and visceral organs. Pulmonary hypertension and interstitial pulmonary disease (Ssc-ILD) are the most reported pulmonary complications in scleroderma patients. The pathogenesis of SSc- ILD is not well understood and the spectrum of SSc-ILD ranges from minimal lung involvement, which is often non-progressive, to severe illnesses. Usual Interstitial Pneumonia's (UIP) is one pattern of Ssc-ILD, marked in one-third of the patients with characteristic of honeycomb appearance and bronchiectasis. It is very important to determine the UIP based on radiology imaging especially with the presence of a poor prognosis in patients with UIP. This case report will discuss the importance of finding UIP-type ILD patterns based on HRCT in patients with scleroderma and different outcome.
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spelling doaj.art-d3a8e070c875418b9b6f0f68e6f360652022-12-21T16:58:37ZengElsevierRadiology Case Reports1930-04332022-02-01172336339Variation of usual interstitial pneumonia using HRCT in Scleroderma PatientsVally Wulani0Taufik Budianto1Mohamad Yanuar Amal2Corresponding author.; Department of Radiology, Faculty of Medicine, University of Indonesia- Dr. Cipto Mangunkusumo Hospital, Jakarta, IndonesiaDepartment of Radiology, Faculty of Medicine, University of Indonesia- Dr. Cipto Mangunkusumo Hospital, Jakarta, IndonesiaDepartment of Radiology, Faculty of Medicine, University of Indonesia- Dr. Cipto Mangunkusumo Hospital, Jakarta, IndonesiaProgressive Systemic Sclerosis or Scleroderma is a systemic inflammation marked by endothelial damaged, fibrosis, and inflammation in skin, joints, and visceral organs. Pulmonary hypertension and interstitial pulmonary disease (Ssc-ILD) are the most reported pulmonary complications in scleroderma patients. The pathogenesis of SSc- ILD is not well understood and the spectrum of SSc-ILD ranges from minimal lung involvement, which is often non-progressive, to severe illnesses. Usual Interstitial Pneumonia's (UIP) is one pattern of Ssc-ILD, marked in one-third of the patients with characteristic of honeycomb appearance and bronchiectasis. It is very important to determine the UIP based on radiology imaging especially with the presence of a poor prognosis in patients with UIP. This case report will discuss the importance of finding UIP-type ILD patterns based on HRCT in patients with scleroderma and different outcome.http://www.sciencedirect.com/science/article/pii/S1930043321007731Systemic SclerosisSclerodermaUsual Interstitial PneumoniaHRCT
spellingShingle Vally Wulani
Taufik Budianto
Mohamad Yanuar Amal
Variation of usual interstitial pneumonia using HRCT in Scleroderma Patients
Radiology Case Reports
Systemic Sclerosis
Scleroderma
Usual Interstitial Pneumonia
HRCT
title Variation of usual interstitial pneumonia using HRCT in Scleroderma Patients
title_full Variation of usual interstitial pneumonia using HRCT in Scleroderma Patients
title_fullStr Variation of usual interstitial pneumonia using HRCT in Scleroderma Patients
title_full_unstemmed Variation of usual interstitial pneumonia using HRCT in Scleroderma Patients
title_short Variation of usual interstitial pneumonia using HRCT in Scleroderma Patients
title_sort variation of usual interstitial pneumonia using hrct in scleroderma patients
topic Systemic Sclerosis
Scleroderma
Usual Interstitial Pneumonia
HRCT
url http://www.sciencedirect.com/science/article/pii/S1930043321007731
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