Behçet’s disease presenting with Budd–Chiari syndrome and intracardial thrombus: a case report

Minji Jennifer Kim1, Yong Suk Jo2, Jee Hyun Kim2, Yong-Jin Kim3, Kyung Hwan Kim4, Eun Bong Lee2, Yeong Wook Song2, Eun Young Lee21School of Medicine, University of Manchester, Manchester, UK; 2Division of Rheumatology, 3Division of Cardiology, Department of Internal Medicine, 4Department of Thoracic...

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Main Authors: Kim MJ, Jo YS, Kim JH, Kim YJ, Kim KH, Lee EB, Song YW, Lee EY
Format: Article
Language:English
Published: Dove Medical Press 2011-11-01
Series:International Medical Case Reports Journal
Online Access:http://www.dovepress.com/behccediletrsquos-disease-presenting-with-buddndashchiari-syndrome-and-a8603
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author Kim MJ
Jo YS
Kim JH
Kim YJ
Kim KH
Lee EB
Song YW
Lee EY
author_facet Kim MJ
Jo YS
Kim JH
Kim YJ
Kim KH
Lee EB
Song YW
Lee EY
author_sort Kim MJ
collection DOAJ
description Minji Jennifer Kim1, Yong Suk Jo2, Jee Hyun Kim2, Yong-Jin Kim3, Kyung Hwan Kim4, Eun Bong Lee2, Yeong Wook Song2, Eun Young Lee21School of Medicine, University of Manchester, Manchester, UK; 2Division of Rheumatology, 3Division of Cardiology, Department of Internal Medicine, 4Department of Thoracic Surgery, Seoul National University College of Medicine, Seoul, Republic of KoreaAbstract: Budd–Chiari syndrome has been described as a late complication of Behçet’s disease. Although the mortality rate associated with Behçet’s disease is low, it can escalate in the presence of Budd–Chiari syndrome and may be further complicated by intracardial thrombus formation. It is therefore important to detect and initiate management early in the disease course. The imaging modalities of choice should be minimally invasive as certain procedures may aggravate Behçet’s disease by initiating a thrombosis or aggravating an existing one. In Behçet’s disease-induced Budd–Chiari syndrome, cardiac investigation is crucial in the work-up in order to identify any cardiac involvement and determine the etiology of intracardial thrombus. Furthermore, the treatment should ultimately focus on controlling the activity of Behçet’s disease. We report an unusual case of Behçet’s disease presenting with Budd–Chiari syndrome complicated by intracardial thrombus in a young Korean man.Keywords: Behçet’s disease, Budd–Chiari syndrome, intracardial thrombus
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spelling doaj.art-d43066ac3d3a4a329d7f6b0f82732d6f2022-12-22T00:44:32ZengDove Medical PressInternational Medical Case Reports Journal1179-142X2011-11-012011default6771Behçet’s disease presenting with Budd–Chiari syndrome and intracardial thrombus: a case reportKim MJJo YSKim JHKim YJKim KHLee EBSong YWLee EYMinji Jennifer Kim1, Yong Suk Jo2, Jee Hyun Kim2, Yong-Jin Kim3, Kyung Hwan Kim4, Eun Bong Lee2, Yeong Wook Song2, Eun Young Lee21School of Medicine, University of Manchester, Manchester, UK; 2Division of Rheumatology, 3Division of Cardiology, Department of Internal Medicine, 4Department of Thoracic Surgery, Seoul National University College of Medicine, Seoul, Republic of KoreaAbstract: Budd–Chiari syndrome has been described as a late complication of Behçet’s disease. Although the mortality rate associated with Behçet’s disease is low, it can escalate in the presence of Budd–Chiari syndrome and may be further complicated by intracardial thrombus formation. It is therefore important to detect and initiate management early in the disease course. The imaging modalities of choice should be minimally invasive as certain procedures may aggravate Behçet’s disease by initiating a thrombosis or aggravating an existing one. In Behçet’s disease-induced Budd–Chiari syndrome, cardiac investigation is crucial in the work-up in order to identify any cardiac involvement and determine the etiology of intracardial thrombus. Furthermore, the treatment should ultimately focus on controlling the activity of Behçet’s disease. We report an unusual case of Behçet’s disease presenting with Budd–Chiari syndrome complicated by intracardial thrombus in a young Korean man.Keywords: Behçet’s disease, Budd–Chiari syndrome, intracardial thrombushttp://www.dovepress.com/behccediletrsquos-disease-presenting-with-buddndashchiari-syndrome-and-a8603
spellingShingle Kim MJ
Jo YS
Kim JH
Kim YJ
Kim KH
Lee EB
Song YW
Lee EY
Behçet’s disease presenting with Budd–Chiari syndrome and intracardial thrombus: a case report
International Medical Case Reports Journal
title Behçet’s disease presenting with Budd–Chiari syndrome and intracardial thrombus: a case report
title_full Behçet’s disease presenting with Budd–Chiari syndrome and intracardial thrombus: a case report
title_fullStr Behçet’s disease presenting with Budd–Chiari syndrome and intracardial thrombus: a case report
title_full_unstemmed Behçet’s disease presenting with Budd–Chiari syndrome and intracardial thrombus: a case report
title_short Behçet’s disease presenting with Budd–Chiari syndrome and intracardial thrombus: a case report
title_sort beh amp ccedil et amp rsquo s disease presenting with budd amp ndash chiari syndrome and intracardial thrombus a case report
url http://www.dovepress.com/behccediletrsquos-disease-presenting-with-buddndashchiari-syndrome-and-a8603
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