Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome: A case report
Background: Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) or Herlyn-Werner-Wunderlich syndrome, is a rare Mullerian duct anomaly with uterus didelphys, unilateral obstructed hemivagina, and ipsilateral renal agenesis. Patients with this anomaly usually present after menarche with pelv...
| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
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Elsevier
2023-08-01
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| Series: | Journal of Pediatric Surgery Case Reports |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S221357662300088X |
| _version_ | 1797801072370122752 |
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| author | Mohamed Amin Elgohary Rushikesh Naik Mohamed Elkafafi Hussein Hamed Yaser Ali |
| author_facet | Mohamed Amin Elgohary Rushikesh Naik Mohamed Elkafafi Hussein Hamed Yaser Ali |
| author_sort | Mohamed Amin Elgohary |
| collection | DOAJ |
| description | Background: Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) or Herlyn-Werner-Wunderlich syndrome, is a rare Mullerian duct anomaly with uterus didelphys, unilateral obstructed hemivagina, and ipsilateral renal agenesis. Patients with this anomaly usually present after menarche with pelvic pain and/or an abdominal mass. Case presentation: We are reporting a case of an 11-year-old girl with lower abdominal pain and lower abdominal tenderness in whom radiological investigations confirmed the diagnosis of OHVIRA syndrome. The case was managed successfully by excision of the vaginal septum. Conclusion: The triad of uterine didelphys, obstructed hemivagina, and ipsilateral renal anomaly, known as OHVIRA syndrome, is a rare congenital anomaly. It represents a diagnostic dilemma because of the regular menstruation and nonspecific lower abdominal pain. Health care providers should be aware of the presentation and diagnosis of this condition to facilitate early and accurate management. |
| first_indexed | 2024-03-13T04:44:52Z |
| format | Article |
| id | doaj.art-d4597c2777c944b0b181b8155b963c63 |
| institution | Directory Open Access Journal |
| issn | 2213-5766 |
| language | English |
| last_indexed | 2024-03-13T04:44:52Z |
| publishDate | 2023-08-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Journal of Pediatric Surgery Case Reports |
| spelling | doaj.art-d4597c2777c944b0b181b8155b963c632023-06-19T04:27:58ZengElsevierJournal of Pediatric Surgery Case Reports2213-57662023-08-0195102662Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome: A case reportMohamed Amin Elgohary0Rushikesh Naik1Mohamed Elkafafi2Hussein Hamed3Yaser Ali4Corresponding author.; Burjeel Hospital, Abu Dhabi, United Arab EmiratesBurjeel Hospital, Abu Dhabi, United Arab EmiratesBurjeel Hospital, Abu Dhabi, United Arab EmiratesBurjeel Hospital, Abu Dhabi, United Arab EmiratesBurjeel Hospital, Abu Dhabi, United Arab EmiratesBackground: Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) or Herlyn-Werner-Wunderlich syndrome, is a rare Mullerian duct anomaly with uterus didelphys, unilateral obstructed hemivagina, and ipsilateral renal agenesis. Patients with this anomaly usually present after menarche with pelvic pain and/or an abdominal mass. Case presentation: We are reporting a case of an 11-year-old girl with lower abdominal pain and lower abdominal tenderness in whom radiological investigations confirmed the diagnosis of OHVIRA syndrome. The case was managed successfully by excision of the vaginal septum. Conclusion: The triad of uterine didelphys, obstructed hemivagina, and ipsilateral renal anomaly, known as OHVIRA syndrome, is a rare congenital anomaly. It represents a diagnostic dilemma because of the regular menstruation and nonspecific lower abdominal pain. Health care providers should be aware of the presentation and diagnosis of this condition to facilitate early and accurate management.http://www.sciencedirect.com/science/article/pii/S221357662300088XMüllerian anomalyObstructed vaginaOHVIRA syndromeCase report |
| spellingShingle | Mohamed Amin Elgohary Rushikesh Naik Mohamed Elkafafi Hussein Hamed Yaser Ali Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome: A case report Journal of Pediatric Surgery Case Reports Müllerian anomaly Obstructed vagina OHVIRA syndrome Case report |
| title | Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome: A case report |
| title_full | Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome: A case report |
| title_fullStr | Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome: A case report |
| title_full_unstemmed | Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome: A case report |
| title_short | Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome: A case report |
| title_sort | obstructed hemivagina and ipsilateral renal anomaly ohvira syndrome a case report |
| topic | Müllerian anomaly Obstructed vagina OHVIRA syndrome Case report |
| url | http://www.sciencedirect.com/science/article/pii/S221357662300088X |
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