Evaluation of Coronary Arteries in Non-Ischemic Cardiomyopathies: A Case Report

Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) is a congenital cardiac disease with myocardial involvement, most probably right ventricular (RV) dysfunction, accounting for 20% of sudden cardiac deaths. Characterized by the fibro-fatty infiltration of the RV free wall, ARVD/C pre...

Full description

Bibliographic Details
Main Authors: Farveh Vakilian, Mahmood Mohamadzadeh Shabestari, Ahmad Amin, Soheila Chamanian, Toktam Moghiman
Format: Article
Language:English
Published: Tehran University of Medical Sciences 2017-02-01
Series:Journal of Tehran University Heart Center
Subjects:
Online Access:https://jthc.tums.ac.ir/index.php/jthc/article/view/649
_version_ 1811271447866245120
author Farveh Vakilian
Mahmood Mohamadzadeh Shabestari
Ahmad Amin
Soheila Chamanian
Toktam Moghiman
author_facet Farveh Vakilian
Mahmood Mohamadzadeh Shabestari
Ahmad Amin
Soheila Chamanian
Toktam Moghiman
author_sort Farveh Vakilian
collection DOAJ
description Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) is a congenital cardiac disease with myocardial involvement, most probably right ventricular (RV) dysfunction, accounting for 20% of sudden cardiac deaths. Characterized by the fibro-fatty infiltration of the RV free wall, ARVD/C presents in adolescents with ventricular arrhythmias and heart failure symptoms and as biventricular failure in adults. The coronary risk in these patients is not clear. We present an incidental finding: the left anterior descending artery cut-off in a middle-aged man with ARVD/C. He had been under treatment for heart failure symptoms, which had decompensated frequently commencing 6 months earlier, and therefore he was scheduled for stem cell injection. He had no chest pain or coronary artery disease risk factors. Two-dimensional transthoracic echocardiography demonstrated RV enlargement with moderate to severe dysfunction and left ventricular ejection fraction (LVEF) of 35-40%, which was 45-50% two years before. Selective coronary angiography performed 8 years previously was normal but a new one revealed the cut-off of the left anterior descending artery at the proximal portion, for which percutaneous coronary intervention was performed and showed no significant lesion in the other vessels. One should consider coronary artery disease in uncontrolled heart failure with LVEF reduction, even in the absence of typical chest pain. It may not be the natural course of the underlying disease.
first_indexed 2024-04-12T22:21:08Z
format Article
id doaj.art-d5e2d04186204f2692db2df20ef1eedd
institution Directory Open Access Journal
issn 1735-8620
2008-2371
language English
last_indexed 2024-04-12T22:21:08Z
publishDate 2017-02-01
publisher Tehran University of Medical Sciences
record_format Article
series Journal of Tehran University Heart Center
spelling doaj.art-d5e2d04186204f2692db2df20ef1eedd2022-12-22T03:14:22ZengTehran University of Medical SciencesJournal of Tehran University Heart Center1735-86202008-23712017-02-01114449Evaluation of Coronary Arteries in Non-Ischemic Cardiomyopathies: A Case ReportFarveh Vakilian0Mahmood Mohamadzadeh Shabestari1Ahmad Amin2Soheila Chamanian3Toktam Moghiman4Atherosclerosis Prevention Research Center, Imam Reza Hospital, Mashhad University of Medical Sciences, Mashhad, Iran.Atherosclerosis Prevention Research Center, Imam Reza Hospital, Mashhad University of Medical Sciences, Mashhad, Iran.Rajaie Cardiovascular, Medical and Research Center, Iran University of Medical Sciences, Tehran, Iran.Atherosclerosis Prevention Research Center, Imam Reza Hospital, Mashhad University of Medical Sciences, Mashhad, Iran.Atherosclerosis Prevention Research Center, Imam Reza Hospital, Mashhad University of Medical Sciences, Mashhad, Iran.Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) is a congenital cardiac disease with myocardial involvement, most probably right ventricular (RV) dysfunction, accounting for 20% of sudden cardiac deaths. Characterized by the fibro-fatty infiltration of the RV free wall, ARVD/C presents in adolescents with ventricular arrhythmias and heart failure symptoms and as biventricular failure in adults. The coronary risk in these patients is not clear. We present an incidental finding: the left anterior descending artery cut-off in a middle-aged man with ARVD/C. He had been under treatment for heart failure symptoms, which had decompensated frequently commencing 6 months earlier, and therefore he was scheduled for stem cell injection. He had no chest pain or coronary artery disease risk factors. Two-dimensional transthoracic echocardiography demonstrated RV enlargement with moderate to severe dysfunction and left ventricular ejection fraction (LVEF) of 35-40%, which was 45-50% two years before. Selective coronary angiography performed 8 years previously was normal but a new one revealed the cut-off of the left anterior descending artery at the proximal portion, for which percutaneous coronary intervention was performed and showed no significant lesion in the other vessels. One should consider coronary artery disease in uncontrolled heart failure with LVEF reduction, even in the absence of typical chest pain. It may not be the natural course of the underlying disease.https://jthc.tums.ac.ir/index.php/jthc/article/view/649Coronary vessels • Cardiomyopathies • Heart ventricles • Diagnosis
spellingShingle Farveh Vakilian
Mahmood Mohamadzadeh Shabestari
Ahmad Amin
Soheila Chamanian
Toktam Moghiman
Evaluation of Coronary Arteries in Non-Ischemic Cardiomyopathies: A Case Report
Journal of Tehran University Heart Center
Coronary vessels • Cardiomyopathies • Heart ventricles • Diagnosis
title Evaluation of Coronary Arteries in Non-Ischemic Cardiomyopathies: A Case Report
title_full Evaluation of Coronary Arteries in Non-Ischemic Cardiomyopathies: A Case Report
title_fullStr Evaluation of Coronary Arteries in Non-Ischemic Cardiomyopathies: A Case Report
title_full_unstemmed Evaluation of Coronary Arteries in Non-Ischemic Cardiomyopathies: A Case Report
title_short Evaluation of Coronary Arteries in Non-Ischemic Cardiomyopathies: A Case Report
title_sort evaluation of coronary arteries in non ischemic cardiomyopathies a case report
topic Coronary vessels • Cardiomyopathies • Heart ventricles • Diagnosis
url https://jthc.tums.ac.ir/index.php/jthc/article/view/649
work_keys_str_mv AT farvehvakilian evaluationofcoronaryarteriesinnonischemiccardiomyopathiesacasereport
AT mahmoodmohamadzadehshabestari evaluationofcoronaryarteriesinnonischemiccardiomyopathiesacasereport
AT ahmadamin evaluationofcoronaryarteriesinnonischemiccardiomyopathiesacasereport
AT soheilachamanian evaluationofcoronaryarteriesinnonischemiccardiomyopathiesacasereport
AT toktammoghiman evaluationofcoronaryarteriesinnonischemiccardiomyopathiesacasereport