Multiorgan sarcoidosis as a diabetes insipidus mask

Sarcoidosis is an inflammatory, multisystem disease with an undetermined etiology. The presence of noncaseating granulomas in involved organs is a characteristic pathomorphological feature. Sarcoidosis, like a chameleon, can mimic different medical conditions. Although the lungs are most commonly in...

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Main Authors: Katarzyna Guziejko, Łukasz Minarowski, Agata Piłaszewicz-Puza, Anna Szumera-Ciećkiewicz, Robert Marek Mróz
Format: Article
Language:English
Published: Bioscientifica 2022-11-01
Series:Endocrinology, Diabetes & Metabolism Case Reports
Online Access:https://edm.bioscientifica.com/view/journals/edm/2022/1/EDM22-0266.xml
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author Katarzyna Guziejko
Łukasz Minarowski
Agata Piłaszewicz-Puza
Anna Szumera-Ciećkiewicz
Robert Marek Mróz
author_facet Katarzyna Guziejko
Łukasz Minarowski
Agata Piłaszewicz-Puza
Anna Szumera-Ciećkiewicz
Robert Marek Mróz
author_sort Katarzyna Guziejko
collection DOAJ
description Sarcoidosis is an inflammatory, multisystem disease with an undetermined etiology. The presence of noncaseating granulomas in involved organs is a characteristic pathomorphological feature. Sarcoidosis, like a chameleon, can mimic different medical conditions. Although the lungs are most commonly involved, extrapulmonary manifestations can influence any system. The clinical course of the disease may differ. Immediate initiation of glucocorticosteroid therapy is important when critical organs are impaired. A case of a patient with sarcoidosis whose first clinical symptoms were related to diabetes insipidus (DI) was presented. The diagnosis of multiple organ sarcoidosis was delayed because of an adequate response to treatment with vasopressin. The multidisciplinary diagnostic approach validated the involvement of the pituitary gland, lungs, lymph nodes, bones, and subcutaneous tissue. The presented case emphasizes the critical importance of the multifaceted differential diagnosis of patients with DI.
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spelling doaj.art-d6b1502a02fb468880330cc38f363cab2022-12-22T04:39:30ZengBioscientificaEndocrinology, Diabetes & Metabolism Case Reports2052-05732022-11-01111710.1530/EDM-22-0266Multiorgan sarcoidosis as a diabetes insipidus maskKatarzyna Guziejko0Łukasz Minarowski1Agata Piłaszewicz-Puza2Anna Szumera-Ciećkiewicz3Robert Marek Mróz42nd Department of Lung Diseases and Tuberculosis2nd Department of Lung Diseases and TuberculosisDepartment of Medical Pathomorphology, Medical University of Bialystok, Bialystok, PolandDepartment of Pathology, Maria Sklodowska-Curie National Research Institute of Oncology, Warsaw, Poland2nd Department of Lung Diseases and TuberculosisSarcoidosis is an inflammatory, multisystem disease with an undetermined etiology. The presence of noncaseating granulomas in involved organs is a characteristic pathomorphological feature. Sarcoidosis, like a chameleon, can mimic different medical conditions. Although the lungs are most commonly involved, extrapulmonary manifestations can influence any system. The clinical course of the disease may differ. Immediate initiation of glucocorticosteroid therapy is important when critical organs are impaired. A case of a patient with sarcoidosis whose first clinical symptoms were related to diabetes insipidus (DI) was presented. The diagnosis of multiple organ sarcoidosis was delayed because of an adequate response to treatment with vasopressin. The multidisciplinary diagnostic approach validated the involvement of the pituitary gland, lungs, lymph nodes, bones, and subcutaneous tissue. The presented case emphasizes the critical importance of the multifaceted differential diagnosis of patients with DI.https://edm.bioscientifica.com/view/journals/edm/2022/1/EDM22-0266.xml
spellingShingle Katarzyna Guziejko
Łukasz Minarowski
Agata Piłaszewicz-Puza
Anna Szumera-Ciećkiewicz
Robert Marek Mróz
Multiorgan sarcoidosis as a diabetes insipidus mask
Endocrinology, Diabetes & Metabolism Case Reports
title Multiorgan sarcoidosis as a diabetes insipidus mask
title_full Multiorgan sarcoidosis as a diabetes insipidus mask
title_fullStr Multiorgan sarcoidosis as a diabetes insipidus mask
title_full_unstemmed Multiorgan sarcoidosis as a diabetes insipidus mask
title_short Multiorgan sarcoidosis as a diabetes insipidus mask
title_sort multiorgan sarcoidosis as a diabetes insipidus mask
url https://edm.bioscientifica.com/view/journals/edm/2022/1/EDM22-0266.xml
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AT annaszumeracieckiewicz multiorgansarcoidosisasadiabetesinsipidusmask
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