Ebstein Anomaly in Pregnancy

A 27-year-old primiparous woman with 28 weeks gestational age was admitted to our hospital with worsening shortness of breath. She was diagnosed with Ebstein’s anomaly three years ago, but preferred to be left untreated. The patient was not cyanotic and her vital signs were stable. Her ECG showed in...

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Main Authors: Lusiani Rusdi, Syahrir Azizi, Christopher Suwita, Astrid Karina, Sally A Nasution
Format: Article
Language:English
Published: Interna Publishing 2017-02-01
Series:Acta Medica Indonesiana
Subjects:
Online Access:http://www.actamedindones.org/index.php/ijim/article/view/300
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author Lusiani Rusdi
Syahrir Azizi
Christopher Suwita
Astrid Karina
Sally A Nasution
author_facet Lusiani Rusdi
Syahrir Azizi
Christopher Suwita
Astrid Karina
Sally A Nasution
author_sort Lusiani Rusdi
collection DOAJ
description A 27-year-old primiparous woman with 28 weeks gestational age was admitted to our hospital with worsening shortness of breath. She was diagnosed with Ebstein’s anomaly three years ago, but preferred to be left untreated. The patient was not cyanotic and her vital signs were stable. Her ECG showed incomplete RBBB and prolonged PR-interval. Blood tests revealed mild anemia. Observation of two-dimensional echo with color flow Doppler study showed Ebstein’s anomaly with PFO as additional defects, EF of 57%, LV and LA dilatation, RV atrialization, severe TR, and moderate PH with RVSP of 44.3 mmHg. The patient then underwent elective sectio caesaria at 30 weeks of gestational age; both the mother and her baby were alive and were in good conditions. Problem: there was an increasing breathlessness in this patient so that there was an increasing need to take a decision for her pregnancy. Ebstein’s anomaly is a complicated congenital anomaly. Medical treatment may be followed for many years in patients with mild forms of Ebstein’s anomaly. Surgery should be considered if there is objective evidence of debasement such as significant enlargement of heart size, reduction of systolic function in echocardiography.
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spelling doaj.art-d72d8c96f0b94fa78e5614777fbabd7c2022-12-22T01:36:42ZengInterna PublishingActa Medica Indonesiana0125-93262338-27322017-02-01484325326180Ebstein Anomaly in PregnancyLusiani Rusdi0Syahrir Azizi1Christopher Suwita2Astrid Karina3Sally A Nasution4Department of Internal Medicine, Faculty of Medicine Universitas Indonesia - Cipto Mangunkusumo Hospital, Jakarta, IndonesiaDepartment of Internal Medicine, Faculty of Medicine Universitas Indonesia - Cipto Mangunkusumo Hospital, Jakarta, IndonesiaDepartment of Internal Medicine, Faculty of Medicine Universitas Indonesia - Cipto Mangunkusumo Hospital, Jakarta, IndonesiaDepartment of Internal Medicine, Faculty of Medicine Universitas Indonesia - Cipto Mangunkusumo Hospital, Jakarta, IndonesiaDepartment of Internal Medicine, Faculty of Medicine Universitas Indonesia - Cipto Mangunkusumo Hospital, Jakarta, IndonesiaA 27-year-old primiparous woman with 28 weeks gestational age was admitted to our hospital with worsening shortness of breath. She was diagnosed with Ebstein’s anomaly three years ago, but preferred to be left untreated. The patient was not cyanotic and her vital signs were stable. Her ECG showed incomplete RBBB and prolonged PR-interval. Blood tests revealed mild anemia. Observation of two-dimensional echo with color flow Doppler study showed Ebstein’s anomaly with PFO as additional defects, EF of 57%, LV and LA dilatation, RV atrialization, severe TR, and moderate PH with RVSP of 44.3 mmHg. The patient then underwent elective sectio caesaria at 30 weeks of gestational age; both the mother and her baby were alive and were in good conditions. Problem: there was an increasing breathlessness in this patient so that there was an increasing need to take a decision for her pregnancy. Ebstein’s anomaly is a complicated congenital anomaly. Medical treatment may be followed for many years in patients with mild forms of Ebstein’s anomaly. Surgery should be considered if there is objective evidence of debasement such as significant enlargement of heart size, reduction of systolic function in echocardiography.http://www.actamedindones.org/index.php/ijim/article/view/300ebstein anomalypregnancyechocardiography
spellingShingle Lusiani Rusdi
Syahrir Azizi
Christopher Suwita
Astrid Karina
Sally A Nasution
Ebstein Anomaly in Pregnancy
Acta Medica Indonesiana
ebstein anomaly
pregnancy
echocardiography
title Ebstein Anomaly in Pregnancy
title_full Ebstein Anomaly in Pregnancy
title_fullStr Ebstein Anomaly in Pregnancy
title_full_unstemmed Ebstein Anomaly in Pregnancy
title_short Ebstein Anomaly in Pregnancy
title_sort ebstein anomaly in pregnancy
topic ebstein anomaly
pregnancy
echocardiography
url http://www.actamedindones.org/index.php/ijim/article/view/300
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AT syahrirazizi ebsteinanomalyinpregnancy
AT christophersuwita ebsteinanomalyinpregnancy
AT astridkarina ebsteinanomalyinpregnancy
AT sallyanasution ebsteinanomalyinpregnancy