A rare case of scimitar syndrome with pulmonary arterial hypertension in an adult female
Abstract Scimitar syndrome is a rare congenital anomaly characterized by partial or total anomalous pulmonary venous drainage of the right lung to the inferior vena cava. We report a case of a 67‐year‐old female who presented with cough and dyspnea and was diagnosed with scimitar syndrome and pulmon...
| Main Authors: | , , , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Wiley
2024-01-01
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| Series: | Pulmonary Circulation |
| Subjects: | |
| Online Access: | https://doi.org/10.1002/pul2.12332 |
| _version_ | 1797236752332619776 |
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| author | Yang Liu Weiliang Ruan Ziye Li Hua Wang Shenghai Chen Yuhong Ding Jianfeng Jin |
| author_facet | Yang Liu Weiliang Ruan Ziye Li Hua Wang Shenghai Chen Yuhong Ding Jianfeng Jin |
| author_sort | Yang Liu |
| collection | DOAJ |
| description | Abstract Scimitar syndrome is a rare congenital anomaly characterized by partial or total anomalous pulmonary venous drainage of the right lung to the inferior vena cava. We report a case of a 67‐year‐old female who presented with cough and dyspnea and was diagnosed with scimitar syndrome and pulmonary arterial hypertension based on comprehensive imaging and hemodynamic evaluation. This case highlights the importance of considering scimitar syndrome as a cause of pulmonary hypertension even in adult patients. |
| first_indexed | 2024-04-24T17:08:51Z |
| format | Article |
| id | doaj.art-d922a3b17a2b4fe59911a9ac5e1a2820 |
| institution | Directory Open Access Journal |
| issn | 2045-8940 |
| language | English |
| last_indexed | 2024-04-24T17:08:51Z |
| publishDate | 2024-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Pulmonary Circulation |
| spelling | doaj.art-d922a3b17a2b4fe59911a9ac5e1a28202024-03-28T19:28:30ZengWileyPulmonary Circulation2045-89402024-01-01141n/an/a10.1002/pul2.12332A rare case of scimitar syndrome with pulmonary arterial hypertension in an adult femaleYang Liu0Weiliang Ruan1Ziye Li2Hua Wang3Shenghai Chen4Yuhong Ding5Jianfeng Jin6Respiratory Department Shaoxing City Keqiao District Hospital of Traditional Chinese Medicine Shaoxing ChinaRespiratory Department Shaoxing City Keqiao District Hospital of Traditional Chinese Medicine Shaoxing ChinaRespiratory Department Shaoxing City Keqiao District Hospital of Traditional Chinese Medicine Shaoxing ChinaSpecial Inspection Department Shaoxing City Keqiao District Hospital of traditional Chinese Medicine Shaoxing ChinaRespiratory Department Shaoxing City Keqiao District Hospital of Traditional Chinese Medicine Shaoxing ChinaRespiratory Department Shaoxing City Keqiao District Hospital of Traditional Chinese Medicine Shaoxing ChinaRespiratory Department Shaoxing City Keqiao District Hospital of Traditional Chinese Medicine Shaoxing ChinaAbstract Scimitar syndrome is a rare congenital anomaly characterized by partial or total anomalous pulmonary venous drainage of the right lung to the inferior vena cava. We report a case of a 67‐year‐old female who presented with cough and dyspnea and was diagnosed with scimitar syndrome and pulmonary arterial hypertension based on comprehensive imaging and hemodynamic evaluation. This case highlights the importance of considering scimitar syndrome as a cause of pulmonary hypertension even in adult patients.https://doi.org/10.1002/pul2.12332computed tomography angiographypulmonary arterial hypertensionscimitar syndrome |
| spellingShingle | Yang Liu Weiliang Ruan Ziye Li Hua Wang Shenghai Chen Yuhong Ding Jianfeng Jin A rare case of scimitar syndrome with pulmonary arterial hypertension in an adult female Pulmonary Circulation computed tomography angiography pulmonary arterial hypertension scimitar syndrome |
| title | A rare case of scimitar syndrome with pulmonary arterial hypertension in an adult female |
| title_full | A rare case of scimitar syndrome with pulmonary arterial hypertension in an adult female |
| title_fullStr | A rare case of scimitar syndrome with pulmonary arterial hypertension in an adult female |
| title_full_unstemmed | A rare case of scimitar syndrome with pulmonary arterial hypertension in an adult female |
| title_short | A rare case of scimitar syndrome with pulmonary arterial hypertension in an adult female |
| title_sort | rare case of scimitar syndrome with pulmonary arterial hypertension in an adult female |
| topic | computed tomography angiography pulmonary arterial hypertension scimitar syndrome |
| url | https://doi.org/10.1002/pul2.12332 |
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