Chylous ascites in an infant – Treated surgically with fibrin glue after failed medical treatment - A case report
Congenital chylous ascites (CCA) is a rare disease that results from mal development of the intra-abdominal lymphatic system and no gold standard treatment described so far. It is defined as the accumulation of triglyceride-rich milky fluid into peritoneal cavity in infant younger than three months....
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Elsevier
2017-04-01
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| Series: | Journal of Pediatric Surgery Case Reports |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S2213576616302469 |
| _version_ | 1818311809450377216 |
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| author | Rasha Kassem Abdullah Rajab Ahamed Faiz Sunil Yadav Kumar Sam Aruputha John Ola Taher |
| author_facet | Rasha Kassem Abdullah Rajab Ahamed Faiz Sunil Yadav Kumar Sam Aruputha John Ola Taher |
| author_sort | Rasha Kassem |
| collection | DOAJ |
| description | Congenital chylous ascites (CCA) is a rare disease that results from mal development of the intra-abdominal lymphatic system and no gold standard treatment described so far. It is defined as the accumulation of triglyceride-rich milky fluid into peritoneal cavity in infant younger than three months.
Medium chain triglyceride (MCT)-based diet or total parental nutrition (TPN) with rest to bowel and abdominal paracentesis is the time honoured conservative management. Due to rare incidence of this disorder, the existing literature includes mainly case reports where TPN was used with or without MCT based formulas along with octreotide. This condition is often refractory to therapy and is responsible for serious malnutrition and immunological deficiency because of loss of proteins and lymphocytes.
Its treatment is often frustrating and challenge to physician. We report an infant with chylous ascites which was refractory to medical treatment in the form of prolonged bowel rest with TPN, Octreotide and repeated paracentesis. Surgical treatment with application of fibrin glue in the area of paradudenal retroperitoneal lymphatics sealed the lymphatic leak and cured the patient. |
| first_indexed | 2024-12-13T08:07:51Z |
| format | Article |
| id | doaj.art-d942656193e947549b188a028531a8ef |
| institution | Directory Open Access Journal |
| issn | 2213-5766 |
| language | English |
| last_indexed | 2024-12-13T08:07:51Z |
| publishDate | 2017-04-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Journal of Pediatric Surgery Case Reports |
| spelling | doaj.art-d942656193e947549b188a028531a8ef2022-12-21T23:54:17ZengElsevierJournal of Pediatric Surgery Case Reports2213-57662017-04-0119C252710.1016/j.epsc.2017.02.002Chylous ascites in an infant – Treated surgically with fibrin glue after failed medical treatment - A case reportRasha Kassem0Abdullah Rajab1Ahamed Faiz2Sunil Yadav Kumar3Sam Aruputha John4Ola Taher5Faculty of Medicine, Pediatric Surgery Department, Zagazig University, EgyptIbn Sina Hospital, Ministry of Health, KuwaitIbn Sina Hospital, Ministry of Health, KuwaitIbn Sina Hospital, Ministry of Health, KuwaitIbn Sina Hospital, Ministry of Health, KuwaitIbn Sina Hospital, Ministry of Health, KuwaitCongenital chylous ascites (CCA) is a rare disease that results from mal development of the intra-abdominal lymphatic system and no gold standard treatment described so far. It is defined as the accumulation of triglyceride-rich milky fluid into peritoneal cavity in infant younger than three months. Medium chain triglyceride (MCT)-based diet or total parental nutrition (TPN) with rest to bowel and abdominal paracentesis is the time honoured conservative management. Due to rare incidence of this disorder, the existing literature includes mainly case reports where TPN was used with or without MCT based formulas along with octreotide. This condition is often refractory to therapy and is responsible for serious malnutrition and immunological deficiency because of loss of proteins and lymphocytes. Its treatment is often frustrating and challenge to physician. We report an infant with chylous ascites which was refractory to medical treatment in the form of prolonged bowel rest with TPN, Octreotide and repeated paracentesis. Surgical treatment with application of fibrin glue in the area of paradudenal retroperitoneal lymphatics sealed the lymphatic leak and cured the patient.http://www.sciencedirect.com/science/article/pii/S2213576616302469 |
| spellingShingle | Rasha Kassem Abdullah Rajab Ahamed Faiz Sunil Yadav Kumar Sam Aruputha John Ola Taher Chylous ascites in an infant – Treated surgically with fibrin glue after failed medical treatment - A case report Journal of Pediatric Surgery Case Reports |
| title | Chylous ascites in an infant – Treated surgically with fibrin glue after failed medical treatment - A case report |
| title_full | Chylous ascites in an infant – Treated surgically with fibrin glue after failed medical treatment - A case report |
| title_fullStr | Chylous ascites in an infant – Treated surgically with fibrin glue after failed medical treatment - A case report |
| title_full_unstemmed | Chylous ascites in an infant – Treated surgically with fibrin glue after failed medical treatment - A case report |
| title_short | Chylous ascites in an infant – Treated surgically with fibrin glue after failed medical treatment - A case report |
| title_sort | chylous ascites in an infant treated surgically with fibrin glue after failed medical treatment a case report |
| url | http://www.sciencedirect.com/science/article/pii/S2213576616302469 |
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