Renal artery stenosis: An unusual etiology of hypertensive encephalopathy in a child with fanconi anemia
A 9-year-old girl, diagnosed case of Fanconi anemia, presented with generalized convulsion with altered sensorium. She had fever, severe pallor, sinus tachycardia, blood pressure of 180/120 mmHg in both upper and lower limb, pan-systolic murmur of grade 2/6, abdominal bruit and bilateral papilledema...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2015-01-01
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| Series: | Saudi Journal of Kidney Diseases and Transplantation |
| Online Access: | http://www.sjkdt.org/article.asp?issn=1319-2442;year=2015;volume=26;issue=4;spage=778;epage=782;aulast=Purkait |
| _version_ | 1818109535996346368 |
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| author | Radheshyam Purkait Aritra Mukherji Sucharita Datta Ramchandra Bhadra |
| author_facet | Radheshyam Purkait Aritra Mukherji Sucharita Datta Ramchandra Bhadra |
| author_sort | Radheshyam Purkait |
| collection | DOAJ |
| description | A 9-year-old girl, diagnosed case of Fanconi anemia, presented with generalized convulsion with altered sensorium. She had fever, severe pallor, sinus tachycardia, blood pressure of 180/120 mmHg in both upper and lower limb, pan-systolic murmur of grade 2/6, abdominal bruit and bilateral papilledema. A provisional diagnosis of hypertensive encephalopathy was made and managed with continuous labetalol infusion. Detailed evaluation including magnetic resonance angiography of renal artery detected underlying atrophic and non-functioning right kidney secondary to severe renal artery stenosis on the same side. She was started with multiple antihypertensives, but her blood pressure was maintained poorly. Later on, she underwent rightsided nephrectomy. Following surgery, she was doing well and maintaining normal blood pressure without any antihypertensives. Our child is the second reported case of Fanconi anemia associated with renal artery stenosis presenting with hypertensive encephalopathy. |
| first_indexed | 2024-12-11T02:32:48Z |
| format | Article |
| id | doaj.art-dc3e4a1e7df4400cbc93ab72997665e3 |
| institution | Directory Open Access Journal |
| issn | 1319-2442 |
| language | English |
| last_indexed | 2024-12-11T02:32:48Z |
| publishDate | 2015-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Saudi Journal of Kidney Diseases and Transplantation |
| spelling | doaj.art-dc3e4a1e7df4400cbc93ab72997665e32022-12-22T01:23:48ZengWolters Kluwer Medknow PublicationsSaudi Journal of Kidney Diseases and Transplantation1319-24422015-01-0126477878210.4103/1319-2442.160215Renal artery stenosis: An unusual etiology of hypertensive encephalopathy in a child with fanconi anemiaRadheshyam PurkaitAritra MukherjiSucharita DattaRamchandra BhadraA 9-year-old girl, diagnosed case of Fanconi anemia, presented with generalized convulsion with altered sensorium. She had fever, severe pallor, sinus tachycardia, blood pressure of 180/120 mmHg in both upper and lower limb, pan-systolic murmur of grade 2/6, abdominal bruit and bilateral papilledema. A provisional diagnosis of hypertensive encephalopathy was made and managed with continuous labetalol infusion. Detailed evaluation including magnetic resonance angiography of renal artery detected underlying atrophic and non-functioning right kidney secondary to severe renal artery stenosis on the same side. She was started with multiple antihypertensives, but her blood pressure was maintained poorly. Later on, she underwent rightsided nephrectomy. Following surgery, she was doing well and maintaining normal blood pressure without any antihypertensives. Our child is the second reported case of Fanconi anemia associated with renal artery stenosis presenting with hypertensive encephalopathy.http://www.sjkdt.org/article.asp?issn=1319-2442;year=2015;volume=26;issue=4;spage=778;epage=782;aulast=Purkait |
| spellingShingle | Radheshyam Purkait Aritra Mukherji Sucharita Datta Ramchandra Bhadra Renal artery stenosis: An unusual etiology of hypertensive encephalopathy in a child with fanconi anemia Saudi Journal of Kidney Diseases and Transplantation |
| title | Renal artery stenosis: An unusual etiology of hypertensive encephalopathy in a child with fanconi anemia |
| title_full | Renal artery stenosis: An unusual etiology of hypertensive encephalopathy in a child with fanconi anemia |
| title_fullStr | Renal artery stenosis: An unusual etiology of hypertensive encephalopathy in a child with fanconi anemia |
| title_full_unstemmed | Renal artery stenosis: An unusual etiology of hypertensive encephalopathy in a child with fanconi anemia |
| title_short | Renal artery stenosis: An unusual etiology of hypertensive encephalopathy in a child with fanconi anemia |
| title_sort | renal artery stenosis an unusual etiology of hypertensive encephalopathy in a child with fanconi anemia |
| url | http://www.sjkdt.org/article.asp?issn=1319-2442;year=2015;volume=26;issue=4;spage=778;epage=782;aulast=Purkait |
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