A primary intestinal lymphangiectasia hiding the diagnosis of pleural and pericardial tuberculosis: a clinical observation

Primary intestinal lymphangiectasia (Waldmannï's disease) is an exudative enteropathy characterized by lymph leakage into the small bowel lumen leading to hypoalbuminemia, hypogammaglobulinemia and lymphopenia (particularly T-cell). The diagnosis is based on viewing the duodenal lymphangiectasi...

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Main Authors: Sanaa Hammi, Hajar Berrani, Thami Benouchen, Naima Lamlami, Imane Elkhiyat, Jamal Eddine Bourkadi
Format: Article
Language:English
Published: The Pan African Medical Journal 2017-02-01
Series:The Pan African Medical Journal
Subjects:
Online Access: https://www.panafrican-med-journal.com/content/article/26/89/pdf/89.pdf
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author Sanaa Hammi
Hajar Berrani
Thami Benouchen
Naima Lamlami
Imane Elkhiyat
Jamal Eddine Bourkadi
author_facet Sanaa Hammi
Hajar Berrani
Thami Benouchen
Naima Lamlami
Imane Elkhiyat
Jamal Eddine Bourkadi
author_sort Sanaa Hammi
collection DOAJ
description Primary intestinal lymphangiectasia (Waldmannï's disease) is an exudative enteropathy characterized by lymph leakage into the small bowel lumen leading to hypoalbuminemia, hypogammaglobulinemia and lymphopenia (particularly T-cell). The diagnosis is based on viewing the duodenal lymphangiectasia. A 20 years old female patient, treated for a primary intestinal lymphangiectasia, has consulted for anasarca. Etiological work-up reveals pleural and pericardial tuberculosis. The clinical aggravation of an enteropathy, particularly in adulthood, requires a search for a secondary etiology. Tuberculosis should be sought systematically.
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spelling doaj.art-dc520dbde8574055b6c55acf77d54fb12022-12-21T19:34:20ZengThe Pan African Medical JournalThe Pan African Medical Journal1937-86881937-86882017-02-01268910.11604/pamj.2017.26.89.1112511125A primary intestinal lymphangiectasia hiding the diagnosis of pleural and pericardial tuberculosis: a clinical observationSanaa Hammi0Hajar Berrani1Thami Benouchen2Naima Lamlami3Imane Elkhiyat4Jamal Eddine Bourkadi5 Medicine and Pharmacy University Tangier, Abdelmalek Essaadi University, Tetouan 93000, Maroc Pediatric Department, General Pediatric Department IV, Rabat Children's Hospital, Rabat, Maroc Pediatric Department, General Pediatric Department IV, Rabat Children's Hospital, Rabat, Maroc Pathological Anatomy Department, Rabat Children's Hospital, Rabat, Maroc Pathological Anatomy Department, Rabat Children's Hospital, Rabat, Maroc Tuberculosis Department, Moulay Youssef University Hospital, Rabat, Maroc Primary intestinal lymphangiectasia (Waldmannï's disease) is an exudative enteropathy characterized by lymph leakage into the small bowel lumen leading to hypoalbuminemia, hypogammaglobulinemia and lymphopenia (particularly T-cell). The diagnosis is based on viewing the duodenal lymphangiectasia. A 20 years old female patient, treated for a primary intestinal lymphangiectasia, has consulted for anasarca. Etiological work-up reveals pleural and pericardial tuberculosis. The clinical aggravation of an enteropathy, particularly in adulthood, requires a search for a secondary etiology. Tuberculosis should be sought systematically. https://www.panafrican-med-journal.com/content/article/26/89/pdf/89.pdf waldmannï's diseaseprimary intestinal lymphangiectasiaintestinalmalabsorption
spellingShingle Sanaa Hammi
Hajar Berrani
Thami Benouchen
Naima Lamlami
Imane Elkhiyat
Jamal Eddine Bourkadi
A primary intestinal lymphangiectasia hiding the diagnosis of pleural and pericardial tuberculosis: a clinical observation
The Pan African Medical Journal
waldmannï's disease
primary intestinal lymphangiectasia
intestinal
malabsorption
title A primary intestinal lymphangiectasia hiding the diagnosis of pleural and pericardial tuberculosis: a clinical observation
title_full A primary intestinal lymphangiectasia hiding the diagnosis of pleural and pericardial tuberculosis: a clinical observation
title_fullStr A primary intestinal lymphangiectasia hiding the diagnosis of pleural and pericardial tuberculosis: a clinical observation
title_full_unstemmed A primary intestinal lymphangiectasia hiding the diagnosis of pleural and pericardial tuberculosis: a clinical observation
title_short A primary intestinal lymphangiectasia hiding the diagnosis of pleural and pericardial tuberculosis: a clinical observation
title_sort primary intestinal lymphangiectasia hiding the diagnosis of pleural and pericardial tuberculosis a clinical observation
topic waldmannï's disease
primary intestinal lymphangiectasia
intestinal
malabsorption
url https://www.panafrican-med-journal.com/content/article/26/89/pdf/89.pdf
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