A primary intestinal lymphangiectasia hiding the diagnosis of pleural and pericardial tuberculosis: a clinical observation
Primary intestinal lymphangiectasia (Waldmannï's disease) is an exudative enteropathy characterized by lymph leakage into the small bowel lumen leading to hypoalbuminemia, hypogammaglobulinemia and lymphopenia (particularly T-cell). The diagnosis is based on viewing the duodenal lymphangiectasi...
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Format: | Article |
Language: | English |
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The Pan African Medical Journal
2017-02-01
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Series: | The Pan African Medical Journal |
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https://www.panafrican-med-journal.com/content/article/26/89/pdf/89.pdf
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author | Sanaa Hammi Hajar Berrani Thami Benouchen Naima Lamlami Imane Elkhiyat Jamal Eddine Bourkadi |
author_facet | Sanaa Hammi Hajar Berrani Thami Benouchen Naima Lamlami Imane Elkhiyat Jamal Eddine Bourkadi |
author_sort | Sanaa Hammi |
collection | DOAJ |
description | Primary intestinal lymphangiectasia (Waldmannï's disease) is an exudative enteropathy characterized by lymph leakage into the small bowel lumen leading to hypoalbuminemia, hypogammaglobulinemia and lymphopenia (particularly T-cell). The diagnosis is based on viewing the duodenal lymphangiectasia. A 20 years old female patient, treated for a primary intestinal lymphangiectasia, has consulted for anasarca. Etiological work-up reveals pleural and pericardial tuberculosis. The clinical aggravation of an enteropathy, particularly in adulthood, requires a search for a secondary etiology. Tuberculosis should be sought systematically. |
first_indexed | 2024-12-20T15:59:17Z |
format | Article |
id | doaj.art-dc520dbde8574055b6c55acf77d54fb1 |
institution | Directory Open Access Journal |
issn | 1937-8688 1937-8688 |
language | English |
last_indexed | 2024-12-20T15:59:17Z |
publishDate | 2017-02-01 |
publisher | The Pan African Medical Journal |
record_format | Article |
series | The Pan African Medical Journal |
spelling | doaj.art-dc520dbde8574055b6c55acf77d54fb12022-12-21T19:34:20ZengThe Pan African Medical JournalThe Pan African Medical Journal1937-86881937-86882017-02-01268910.11604/pamj.2017.26.89.1112511125A primary intestinal lymphangiectasia hiding the diagnosis of pleural and pericardial tuberculosis: a clinical observationSanaa Hammi0Hajar Berrani1Thami Benouchen2Naima Lamlami3Imane Elkhiyat4Jamal Eddine Bourkadi5 Medicine and Pharmacy University Tangier, Abdelmalek Essaadi University, Tetouan 93000, Maroc Pediatric Department, General Pediatric Department IV, Rabat Children's Hospital, Rabat, Maroc Pediatric Department, General Pediatric Department IV, Rabat Children's Hospital, Rabat, Maroc Pathological Anatomy Department, Rabat Children's Hospital, Rabat, Maroc Pathological Anatomy Department, Rabat Children's Hospital, Rabat, Maroc Tuberculosis Department, Moulay Youssef University Hospital, Rabat, Maroc Primary intestinal lymphangiectasia (Waldmannï's disease) is an exudative enteropathy characterized by lymph leakage into the small bowel lumen leading to hypoalbuminemia, hypogammaglobulinemia and lymphopenia (particularly T-cell). The diagnosis is based on viewing the duodenal lymphangiectasia. A 20 years old female patient, treated for a primary intestinal lymphangiectasia, has consulted for anasarca. Etiological work-up reveals pleural and pericardial tuberculosis. The clinical aggravation of an enteropathy, particularly in adulthood, requires a search for a secondary etiology. Tuberculosis should be sought systematically. https://www.panafrican-med-journal.com/content/article/26/89/pdf/89.pdf waldmannï's diseaseprimary intestinal lymphangiectasiaintestinalmalabsorption |
spellingShingle | Sanaa Hammi Hajar Berrani Thami Benouchen Naima Lamlami Imane Elkhiyat Jamal Eddine Bourkadi A primary intestinal lymphangiectasia hiding the diagnosis of pleural and pericardial tuberculosis: a clinical observation The Pan African Medical Journal waldmannï's disease primary intestinal lymphangiectasia intestinal malabsorption |
title | A primary intestinal lymphangiectasia hiding the diagnosis of pleural and pericardial tuberculosis: a clinical observation |
title_full | A primary intestinal lymphangiectasia hiding the diagnosis of pleural and pericardial tuberculosis: a clinical observation |
title_fullStr | A primary intestinal lymphangiectasia hiding the diagnosis of pleural and pericardial tuberculosis: a clinical observation |
title_full_unstemmed | A primary intestinal lymphangiectasia hiding the diagnosis of pleural and pericardial tuberculosis: a clinical observation |
title_short | A primary intestinal lymphangiectasia hiding the diagnosis of pleural and pericardial tuberculosis: a clinical observation |
title_sort | primary intestinal lymphangiectasia hiding the diagnosis of pleural and pericardial tuberculosis a clinical observation |
topic | waldmannï's disease primary intestinal lymphangiectasia intestinal malabsorption |
url |
https://www.panafrican-med-journal.com/content/article/26/89/pdf/89.pdf
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