Unilateral pulmonary vein atresia presenting with recurrent hemoptysis and bronchial varices in an Ethiopian adolescent: a case report
Abstract Background Congenital unilateral pulmonary vein atresia is a rare anomaly resulting from failure of the pulmonary vein to incorporate in the left atrium. It is a very rare cause of recurrent respiratory infections and hemoptysis requiring a high index of suspicion for proper diagnosis and m...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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BMC
2023-06-01
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| Series: | Journal of Medical Case Reports |
| Subjects: | |
| Online Access: | https://doi.org/10.1186/s13256-023-03956-4 |
| _version_ | 1797811511671914496 |
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| author | Abate Yeshidinber Weldetsadik Abdi Kebede Binyam Gebremedhin Godu Maru Gama |
| author_facet | Abate Yeshidinber Weldetsadik Abdi Kebede Binyam Gebremedhin Godu Maru Gama |
| author_sort | Abate Yeshidinber Weldetsadik |
| collection | DOAJ |
| description | Abstract Background Congenital unilateral pulmonary vein atresia is a rare anomaly resulting from failure of the pulmonary vein to incorporate in the left atrium. It is a very rare cause of recurrent respiratory infections and hemoptysis requiring a high index of suspicion for proper diagnosis and management in early childhood. Case presentation We report a 13-year old Anuac (Ethiopia, Region of Gambela) male adolescent with a delayed diagnosis of isolated atresia of the left pulmonary veins despite early childhood presentation with recurrent chest infections, hemoptysis and exercise intolerance. Contrast enhanced CT of thorax with reconstructed planes confirmed the diagnosis. He underwent pneumonectomy for severe and recurrent symptoms and did well on subsequent follow ups after 6 months of pneumonectomy. Conclusion Although a rare anomaly, congenital unilateral pulmonary vein atresia should be considered in the differential diagnosis of a child presenting with recurrent chest infections, exercise intolerance and hemoptysis to facilitate early appropriate diagnosis and treatment. |
| first_indexed | 2024-03-13T07:24:47Z |
| format | Article |
| id | doaj.art-dc726331d9e44d66b9c0a358a1df6cf8 |
| institution | Directory Open Access Journal |
| issn | 1752-1947 |
| language | English |
| last_indexed | 2024-03-13T07:24:47Z |
| publishDate | 2023-06-01 |
| publisher | BMC |
| record_format | Article |
| series | Journal of Medical Case Reports |
| spelling | doaj.art-dc726331d9e44d66b9c0a358a1df6cf82023-06-04T11:29:45ZengBMCJournal of Medical Case Reports1752-19472023-06-011711510.1186/s13256-023-03956-4Unilateral pulmonary vein atresia presenting with recurrent hemoptysis and bronchial varices in an Ethiopian adolescent: a case reportAbate Yeshidinber Weldetsadik0Abdi Kebede1Binyam Gebremedhin Godu2Maru Gama3Department of Pediatrics and Child Health, Saint Paul’s Hospital Millennium Medical CollegeDepartment of Pediatrics and Child Health, Saint Paul’s Hospital Millennium Medical CollegePediatric Surgery Unit, Saint Paul’s Hospital Millennium Medical CollegeDepartment of Surgery, Pediatric Surgery Unit, Saint Paul’s Hospital Millennium Medical CollegeAbstract Background Congenital unilateral pulmonary vein atresia is a rare anomaly resulting from failure of the pulmonary vein to incorporate in the left atrium. It is a very rare cause of recurrent respiratory infections and hemoptysis requiring a high index of suspicion for proper diagnosis and management in early childhood. Case presentation We report a 13-year old Anuac (Ethiopia, Region of Gambela) male adolescent with a delayed diagnosis of isolated atresia of the left pulmonary veins despite early childhood presentation with recurrent chest infections, hemoptysis and exercise intolerance. Contrast enhanced CT of thorax with reconstructed planes confirmed the diagnosis. He underwent pneumonectomy for severe and recurrent symptoms and did well on subsequent follow ups after 6 months of pneumonectomy. Conclusion Although a rare anomaly, congenital unilateral pulmonary vein atresia should be considered in the differential diagnosis of a child presenting with recurrent chest infections, exercise intolerance and hemoptysis to facilitate early appropriate diagnosis and treatment.https://doi.org/10.1186/s13256-023-03956-4Pulmonary vein atresiaRecurrent hemoptysisChest infectionCase reportEthiopia |
| spellingShingle | Abate Yeshidinber Weldetsadik Abdi Kebede Binyam Gebremedhin Godu Maru Gama Unilateral pulmonary vein atresia presenting with recurrent hemoptysis and bronchial varices in an Ethiopian adolescent: a case report Journal of Medical Case Reports Pulmonary vein atresia Recurrent hemoptysis Chest infection Case report Ethiopia |
| title | Unilateral pulmonary vein atresia presenting with recurrent hemoptysis and bronchial varices in an Ethiopian adolescent: a case report |
| title_full | Unilateral pulmonary vein atresia presenting with recurrent hemoptysis and bronchial varices in an Ethiopian adolescent: a case report |
| title_fullStr | Unilateral pulmonary vein atresia presenting with recurrent hemoptysis and bronchial varices in an Ethiopian adolescent: a case report |
| title_full_unstemmed | Unilateral pulmonary vein atresia presenting with recurrent hemoptysis and bronchial varices in an Ethiopian adolescent: a case report |
| title_short | Unilateral pulmonary vein atresia presenting with recurrent hemoptysis and bronchial varices in an Ethiopian adolescent: a case report |
| title_sort | unilateral pulmonary vein atresia presenting with recurrent hemoptysis and bronchial varices in an ethiopian adolescent a case report |
| topic | Pulmonary vein atresia Recurrent hemoptysis Chest infection Case report Ethiopia |
| url | https://doi.org/10.1186/s13256-023-03956-4 |
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