Prune belly syndrome: current perspectives
Angela M Arlen,1 Cayce Nawaf,1 Andrew J Kirsch21Yale University School of Medicine, Department of Urology, New Haven, CT 06520, USA; 2Emory University, Children’s Healthcare of Atlanta, Atlanta, GA 30328, USAAbstract: Prune belly syndrome (PBS) is a rare but morbid congenital disease, clas...
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| Format: | Article |
| Language: | English |
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Dove Medical Press
2019-08-01
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| Series: | Pediatric Health, Medicine and Therapeutics |
| Subjects: | |
| Online Access: | https://www.dovepress.com/prune-belly-syndrome-current-perspectives-peer-reviewed-article-PHMT |
| _version_ | 1818561458666995712 |
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| author | Arlen AM Nawaf C Kirsch AJ |
| author_facet | Arlen AM Nawaf C Kirsch AJ |
| author_sort | Arlen AM |
| collection | DOAJ |
| description | Angela M Arlen,1 Cayce Nawaf,1 Andrew J Kirsch21Yale University School of Medicine, Department of Urology, New Haven, CT 06520, USA; 2Emory University, Children’s Healthcare of Atlanta, Atlanta, GA 30328, USAAbstract: Prune belly syndrome (PBS) is a rare but morbid congenital disease, classically defined by a triad of cardinal features that includes cryptorchidism, urinary tract dilation and laxity of the abdominal wall musculature. Children often require numerous surgical interventions including bilateral orchidopexy as well as individually tailored urinary tract and abdominal wall reconstruction. Along with the classic features, patients with PBS often experience gastrointestinal, orthopedic, and cardiopulmonary comorbidities.Keywords: prune-belly syndrome, cryptorchidism, urinary tract dilation, abdominal wall laxity, abdominoplasty |
| first_indexed | 2024-12-14T00:51:07Z |
| format | Article |
| id | doaj.art-dc9600cbe0824962b254bc7170784b9c |
| institution | Directory Open Access Journal |
| issn | 1179-9927 |
| language | English |
| last_indexed | 2024-12-14T00:51:07Z |
| publishDate | 2019-08-01 |
| publisher | Dove Medical Press |
| record_format | Article |
| series | Pediatric Health, Medicine and Therapeutics |
| spelling | doaj.art-dc9600cbe0824962b254bc7170784b9c2022-12-21T23:23:50ZengDove Medical PressPediatric Health, Medicine and Therapeutics1179-99272019-08-01Volume 10758147675Prune belly syndrome: current perspectivesArlen AMNawaf CKirsch AJAngela M Arlen,1 Cayce Nawaf,1 Andrew J Kirsch21Yale University School of Medicine, Department of Urology, New Haven, CT 06520, USA; 2Emory University, Children’s Healthcare of Atlanta, Atlanta, GA 30328, USAAbstract: Prune belly syndrome (PBS) is a rare but morbid congenital disease, classically defined by a triad of cardinal features that includes cryptorchidism, urinary tract dilation and laxity of the abdominal wall musculature. Children often require numerous surgical interventions including bilateral orchidopexy as well as individually tailored urinary tract and abdominal wall reconstruction. Along with the classic features, patients with PBS often experience gastrointestinal, orthopedic, and cardiopulmonary comorbidities.Keywords: prune-belly syndrome, cryptorchidism, urinary tract dilation, abdominal wall laxity, abdominoplastyhttps://www.dovepress.com/prune-belly-syndrome-current-perspectives-peer-reviewed-article-PHMTPrune belly syndromecryptorchidismabdominal wallabdominoplastyhypotonia |
| spellingShingle | Arlen AM Nawaf C Kirsch AJ Prune belly syndrome: current perspectives Pediatric Health, Medicine and Therapeutics Prune belly syndrome cryptorchidism abdominal wall abdominoplasty hypotonia |
| title | Prune belly syndrome: current perspectives |
| title_full | Prune belly syndrome: current perspectives |
| title_fullStr | Prune belly syndrome: current perspectives |
| title_full_unstemmed | Prune belly syndrome: current perspectives |
| title_short | Prune belly syndrome: current perspectives |
| title_sort | prune belly syndrome current perspectives |
| topic | Prune belly syndrome cryptorchidism abdominal wall abdominoplasty hypotonia |
| url | https://www.dovepress.com/prune-belly-syndrome-current-perspectives-peer-reviewed-article-PHMT |
| work_keys_str_mv | AT arlenam prunebellysyndromecurrentperspectives AT nawafc prunebellysyndromecurrentperspectives AT kirschaj prunebellysyndromecurrentperspectives |