Prosthodontic Management of a Patient with Ectodermal Dysplasia: Case Report
Mohammad Bashir Nejabi,1 Abdurrahman Anwari,2 Hassina Shadab,3 Nargis Mtawakel,1 Fariha Omarzad,1 Mohammad Eissa Ahmadi3 1Prosthodontics Department, Kabul University of Medical Sciences (KUMS), Kabul, Afghanistan; 2Operative/ Restorative Dentistry and Endodontics Department, Kabul University of Medi...
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| Format: | Article |
| Language: | English |
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Dove Medical Press
2023-08-01
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| Series: | Clinical, Cosmetic and Investigational Dentistry |
| Subjects: | |
| Online Access: | https://www.dovepress.com/prosthodontic-management-of-a-patient-with-ectodermal-dysplasia-case-r-peer-reviewed-fulltext-article-CCIDE |
| _version_ | 1827872556780093440 |
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| author | Nejabi MB Anwari A Shadab H Mtawakel N Omarzad F Ahmadi ME |
| author_facet | Nejabi MB Anwari A Shadab H Mtawakel N Omarzad F Ahmadi ME |
| author_sort | Nejabi MB |
| collection | DOAJ |
| description | Mohammad Bashir Nejabi,1 Abdurrahman Anwari,2 Hassina Shadab,3 Nargis Mtawakel,1 Fariha Omarzad,1 Mohammad Eissa Ahmadi3 1Prosthodontics Department, Kabul University of Medical Sciences (KUMS), Kabul, Afghanistan; 2Operative/ Restorative Dentistry and Endodontics Department, Kabul University of Medical Sciences (KUMS), Kabul, Afghanistan; 3Periodontics Department, Kabul University of Medical Sciences (KUMS), Kabul, AfghanistanCorrespondence: Abdurrahman Anwari, Operative/ Restorative Dentistry and Endodontics Department, Kabul University of Medical Sciences (KUMS), Jamal Mena, 3rd District, Kabul, Afghanistan, Tel +93795125522, Email yammamyama@gmail.comAbstract: Ectodermal dysplasia (ED) is an inherited disorder that affects the ectoderm of a developing embryo and impacts structures that originate from it. It typically presents as a triad of missing teeth (anodontia/hypodontia), sparse hair (atrichosis/hypotrichosis), and lack of sweat glands (hypohidrosis), often accompanied by nail dystrophy and palmoplantar hyperkeratosis. There are two main types of this condition: X-linked anhidrotic or hypohidrotic and hidrotic (autosomal type). The oral manifestation of ED may include anodontia or hypodontia, with or without cleft lip and palate. Tooth loss leads to a decrease in the height of the alveolar ridges, resulting in a reduction of the vertical dimension of the lower face, disappearance of the vermilion border, and prominent lips. As a result, the affected person’s face may resemble that of an elderly individual. The current case report aims to illustrate the prosthodontic rehabilitation of 16-year-old male patient with ectodermal dysplasia and complete anodontia, visiting Dentistry Teaching Hospital, Kabul, Afghanistan. Fortunately, this patient was acceptably managed with the collaboration of several disciplines.Keywords: prosthodontic management, ectodermal dysplasia, anodontia, case report |
| first_indexed | 2024-03-12T16:25:52Z |
| format | Article |
| id | doaj.art-dd0048237de34dd1a8525a0d88512111 |
| institution | Directory Open Access Journal |
| issn | 1179-1357 |
| language | English |
| last_indexed | 2024-03-12T16:25:52Z |
| publishDate | 2023-08-01 |
| publisher | Dove Medical Press |
| record_format | Article |
| series | Clinical, Cosmetic and Investigational Dentistry |
| spelling | doaj.art-dd0048237de34dd1a8525a0d885121112023-08-08T19:52:16ZengDove Medical PressClinical, Cosmetic and Investigational Dentistry1179-13572023-08-01Volume 1513314185710Prosthodontic Management of a Patient with Ectodermal Dysplasia: Case ReportNejabi MBAnwari AShadab HMtawakel NOmarzad FAhmadi MEMohammad Bashir Nejabi,1 Abdurrahman Anwari,2 Hassina Shadab,3 Nargis Mtawakel,1 Fariha Omarzad,1 Mohammad Eissa Ahmadi3 1Prosthodontics Department, Kabul University of Medical Sciences (KUMS), Kabul, Afghanistan; 2Operative/ Restorative Dentistry and Endodontics Department, Kabul University of Medical Sciences (KUMS), Kabul, Afghanistan; 3Periodontics Department, Kabul University of Medical Sciences (KUMS), Kabul, AfghanistanCorrespondence: Abdurrahman Anwari, Operative/ Restorative Dentistry and Endodontics Department, Kabul University of Medical Sciences (KUMS), Jamal Mena, 3rd District, Kabul, Afghanistan, Tel +93795125522, Email yammamyama@gmail.comAbstract: Ectodermal dysplasia (ED) is an inherited disorder that affects the ectoderm of a developing embryo and impacts structures that originate from it. It typically presents as a triad of missing teeth (anodontia/hypodontia), sparse hair (atrichosis/hypotrichosis), and lack of sweat glands (hypohidrosis), often accompanied by nail dystrophy and palmoplantar hyperkeratosis. There are two main types of this condition: X-linked anhidrotic or hypohidrotic and hidrotic (autosomal type). The oral manifestation of ED may include anodontia or hypodontia, with or without cleft lip and palate. Tooth loss leads to a decrease in the height of the alveolar ridges, resulting in a reduction of the vertical dimension of the lower face, disappearance of the vermilion border, and prominent lips. As a result, the affected person’s face may resemble that of an elderly individual. The current case report aims to illustrate the prosthodontic rehabilitation of 16-year-old male patient with ectodermal dysplasia and complete anodontia, visiting Dentistry Teaching Hospital, Kabul, Afghanistan. Fortunately, this patient was acceptably managed with the collaboration of several disciplines.Keywords: prosthodontic management, ectodermal dysplasia, anodontia, case reporthttps://www.dovepress.com/prosthodontic-management-of-a-patient-with-ectodermal-dysplasia-case-r-peer-reviewed-fulltext-article-CCIDEprosthodontic managementectodermal dysplasiaanodontiacase report |
| spellingShingle | Nejabi MB Anwari A Shadab H Mtawakel N Omarzad F Ahmadi ME Prosthodontic Management of a Patient with Ectodermal Dysplasia: Case Report Clinical, Cosmetic and Investigational Dentistry prosthodontic management ectodermal dysplasia anodontia case report |
| title | Prosthodontic Management of a Patient with Ectodermal Dysplasia: Case Report |
| title_full | Prosthodontic Management of a Patient with Ectodermal Dysplasia: Case Report |
| title_fullStr | Prosthodontic Management of a Patient with Ectodermal Dysplasia: Case Report |
| title_full_unstemmed | Prosthodontic Management of a Patient with Ectodermal Dysplasia: Case Report |
| title_short | Prosthodontic Management of a Patient with Ectodermal Dysplasia: Case Report |
| title_sort | prosthodontic management of a patient with ectodermal dysplasia case report |
| topic | prosthodontic management ectodermal dysplasia anodontia case report |
| url | https://www.dovepress.com/prosthodontic-management-of-a-patient-with-ectodermal-dysplasia-case-r-peer-reviewed-fulltext-article-CCIDE |
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