… And if this was a Zinner's syndrome?
A two year-old male was seen to our Emergency Department for acute abdominal pain, urinary retention and worsening constipation. A first level diagnostic imaging showed a pelvic cystic mass between bladder and rectum. Left kidney was absent. Further workup with MRI and endoscopy demonstrated the cys...
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
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Elsevier
2014-12-01
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| Series: | Journal of Pediatric Surgery Case Reports |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S2213576614001511 |
| _version_ | 1818273124938940416 |
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| author | Massimiliano Silveri Antonio Zaccara Mauro Colajacomo Ennio Matarazzo Francesca Diomedi Camassei Mario De Gennaro |
| author_facet | Massimiliano Silveri Antonio Zaccara Mauro Colajacomo Ennio Matarazzo Francesca Diomedi Camassei Mario De Gennaro |
| author_sort | Massimiliano Silveri |
| collection | DOAJ |
| description | A two year-old male was seen to our Emergency Department for acute abdominal pain, urinary retention and worsening constipation. A first level diagnostic imaging showed a pelvic cystic mass between bladder and rectum. Left kidney was absent. Further workup with MRI and endoscopy demonstrated the cyst to be of urogenital origin. Rapid increase in size and clinical symptoms prompted surgery. Pathology and surgical specimen showed the mass to be a left seminal vesicle cyst secondary to a malformation of the eiaculatory duct and embriologically related to ipsilateral renal agenesis. Such findings were consistent with the diagnosis of Zinner's syndrome (a clinical triad consisting of seminal vesicle cyst, ejaculatory duct obstruction and ipsilateral renal agenesis). Since the symptoms related to the seminal vesicle cyst coincide with the onset of a sexually active life, the majority of cases are generally observed and treated in the second and third decade. To our knowledge, this is the first case description in pediatric age. |
| first_indexed | 2024-12-12T21:52:59Z |
| format | Article |
| id | doaj.art-dd849f3082f84c96b73403e317a93bff |
| institution | Directory Open Access Journal |
| issn | 2213-5766 |
| language | English |
| last_indexed | 2024-12-12T21:52:59Z |
| publishDate | 2014-12-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Journal of Pediatric Surgery Case Reports |
| spelling | doaj.art-dd849f3082f84c96b73403e317a93bff2022-12-22T00:10:44ZengElsevierJournal of Pediatric Surgery Case Reports2213-57662014-12-0121253053210.1016/j.epsc.2014.10.018… And if this was a Zinner's syndrome?Massimiliano Silveri0Antonio Zaccara1Mauro Colajacomo2Ennio Matarazzo3Francesca Diomedi Camassei4Mario De Gennaro5Department of Surgery, Bambino Gesù Children's Research Hospital, Rome, ItalyDepartment of Urology and Nephrology, Bambino Gesù Children's Research Hospital, Rome, ItalyDepartment of Imaging, Bambino Gesù Children's Research Hospital, Rome, ItalyDepartment of Urology and Nephrology, Bambino Gesù Children's Research Hospital, Rome, ItalyDepartment of Pathology, Bambino Gesù Children's Research Hospital, Rome, ItalyDepartment of Urology and Nephrology, Bambino Gesù Children's Research Hospital, Rome, ItalyA two year-old male was seen to our Emergency Department for acute abdominal pain, urinary retention and worsening constipation. A first level diagnostic imaging showed a pelvic cystic mass between bladder and rectum. Left kidney was absent. Further workup with MRI and endoscopy demonstrated the cyst to be of urogenital origin. Rapid increase in size and clinical symptoms prompted surgery. Pathology and surgical specimen showed the mass to be a left seminal vesicle cyst secondary to a malformation of the eiaculatory duct and embriologically related to ipsilateral renal agenesis. Such findings were consistent with the diagnosis of Zinner's syndrome (a clinical triad consisting of seminal vesicle cyst, ejaculatory duct obstruction and ipsilateral renal agenesis). Since the symptoms related to the seminal vesicle cyst coincide with the onset of a sexually active life, the majority of cases are generally observed and treated in the second and third decade. To our knowledge, this is the first case description in pediatric age.http://www.sciencedirect.com/science/article/pii/S2213576614001511Zinner's syndromeSeminal vesicle cystRenal agenesis |
| spellingShingle | Massimiliano Silveri Antonio Zaccara Mauro Colajacomo Ennio Matarazzo Francesca Diomedi Camassei Mario De Gennaro … And if this was a Zinner's syndrome? Journal of Pediatric Surgery Case Reports Zinner's syndrome Seminal vesicle cyst Renal agenesis |
| title | … And if this was a Zinner's syndrome? |
| title_full | … And if this was a Zinner's syndrome? |
| title_fullStr | … And if this was a Zinner's syndrome? |
| title_full_unstemmed | … And if this was a Zinner's syndrome? |
| title_short | … And if this was a Zinner's syndrome? |
| title_sort | and if this was a zinner s syndrome |
| topic | Zinner's syndrome Seminal vesicle cyst Renal agenesis |
| url | http://www.sciencedirect.com/science/article/pii/S2213576614001511 |
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