Embryonal rhabdomyosarcoma of the biliary tree: A rare cause of obstructive jaundice in children which can mimic choledochal cysts
Jaundice in children is more often due to hepatic disease than obstruction. Differential considerations for obstructive jaundice in children include choledocholithiasis, choledochal cysts and rare neoplasms. Rhabdomyosarcoma, the most common soft tissue sarcoma in pediatric patients, typically invol...
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| Format: | Article |
| Language: | English |
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Thieme Medical and Scientific Publishers Pvt. Ltd.
2017-07-01
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| Series: | Indian Journal of Radiology and Imaging |
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| Online Access: | http://www.thieme-connect.de/DOI/DOI?10.4103/ijri.IJRI_460_16 |
| _version_ | 1823934875664646144 |
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| author | Dhara J Kinariwala Andrew Y Wang Patrick D Melmer William P McCullough |
| author_facet | Dhara J Kinariwala Andrew Y Wang Patrick D Melmer William P McCullough |
| author_sort | Dhara J Kinariwala |
| collection | DOAJ |
| description | Jaundice in children is more often due to hepatic disease than obstruction. Differential considerations for obstructive jaundice in children include choledocholithiasis, choledochal cysts and rare neoplasms. Rhabdomyosarcoma, the most common soft tissue sarcoma in pediatric patients, typically involves the head and neck, genitourinary system and extremities. Embryonal rhabdomyosarcoma of the biliary tree is a rare entity. We present a 3-year-old boy with abrupt onset obstructive jaundice. Although initial imaging suggested a dilated biliary system with fusiform common bile duct, sludge, and possible cholelithiasis, endoscopic retrograde cholangiopancreatogram (ERCP) diagnosed a common bile duct embryonal rhabdomyosarcoma and further imaging showed involvement of the cystic duct. This case illustrates the importance of considering malignant etiologies in cases of obstructive jaundice, particularly when imaging is not classic for common causes. |
| first_indexed | 2024-12-16T22:26:38Z |
| format | Article |
| id | doaj.art-de35d94104ac436993cbc5e69b89508c |
| institution | Directory Open Access Journal |
| issn | 0971-3026 1998-3808 |
| language | English |
| last_indexed | 2024-12-16T22:26:38Z |
| publishDate | 2017-07-01 |
| publisher | Thieme Medical and Scientific Publishers Pvt. Ltd. |
| record_format | Article |
| series | Indian Journal of Radiology and Imaging |
| spelling | doaj.art-de35d94104ac436993cbc5e69b89508c2022-12-21T22:13:51ZengThieme Medical and Scientific Publishers Pvt. Ltd.Indian Journal of Radiology and Imaging0971-30261998-38082017-07-01270330630910.4103/ijri.IJRI_460_16Embryonal rhabdomyosarcoma of the biliary tree: A rare cause of obstructive jaundice in children which can mimic choledochal cystsDhara J Kinariwala0Andrew Y Wang1Patrick D Melmer2William P McCullough3Division of Pediatric Imaging, Department of Radiology and Medical Imaging, Charlottesville, Virginia, USADivision of Gastroenterology and Hepatology, Department of Medicine, University of Virginia Health System, Charlottesville, Virginia, USADivision of Pediatric Imaging, Department of Radiology and Medical Imaging, Charlottesville, Virginia, USADivision of Pediatric Imaging, Department of Radiology and Medical Imaging, Charlottesville, Virginia, USAJaundice in children is more often due to hepatic disease than obstruction. Differential considerations for obstructive jaundice in children include choledocholithiasis, choledochal cysts and rare neoplasms. Rhabdomyosarcoma, the most common soft tissue sarcoma in pediatric patients, typically involves the head and neck, genitourinary system and extremities. Embryonal rhabdomyosarcoma of the biliary tree is a rare entity. We present a 3-year-old boy with abrupt onset obstructive jaundice. Although initial imaging suggested a dilated biliary system with fusiform common bile duct, sludge, and possible cholelithiasis, endoscopic retrograde cholangiopancreatogram (ERCP) diagnosed a common bile duct embryonal rhabdomyosarcoma and further imaging showed involvement of the cystic duct. This case illustrates the importance of considering malignant etiologies in cases of obstructive jaundice, particularly when imaging is not classic for common causes.http://www.thieme-connect.de/DOI/DOI?10.4103/ijri.IJRI_460_16biliary choledochal cystobstructive jaundicepediatricrhabdomyosarcoma |
| spellingShingle | Dhara J Kinariwala Andrew Y Wang Patrick D Melmer William P McCullough Embryonal rhabdomyosarcoma of the biliary tree: A rare cause of obstructive jaundice in children which can mimic choledochal cysts Indian Journal of Radiology and Imaging biliary choledochal cyst obstructive jaundice pediatric rhabdomyosarcoma |
| title | Embryonal rhabdomyosarcoma of the biliary tree: A rare cause of obstructive jaundice in children which can mimic choledochal cysts |
| title_full | Embryonal rhabdomyosarcoma of the biliary tree: A rare cause of obstructive jaundice in children which can mimic choledochal cysts |
| title_fullStr | Embryonal rhabdomyosarcoma of the biliary tree: A rare cause of obstructive jaundice in children which can mimic choledochal cysts |
| title_full_unstemmed | Embryonal rhabdomyosarcoma of the biliary tree: A rare cause of obstructive jaundice in children which can mimic choledochal cysts |
| title_short | Embryonal rhabdomyosarcoma of the biliary tree: A rare cause of obstructive jaundice in children which can mimic choledochal cysts |
| title_sort | embryonal rhabdomyosarcoma of the biliary tree a rare cause of obstructive jaundice in children which can mimic choledochal cysts |
| topic | biliary choledochal cyst obstructive jaundice pediatric rhabdomyosarcoma |
| url | http://www.thieme-connect.de/DOI/DOI?10.4103/ijri.IJRI_460_16 |
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