Nutritional status of adults with phenylketonuria on pegvaliase: A 15-month prospective study

Nutritional status of adults with phenylketonuria on pegvaliase: A 15-month prospective study

Background: Pegvaliase has allowed many adults with phenylketonuria (PKU) to achieve acceptable blood Phe control while eating an unrestricted diet. However, little is known about potential differences in nutritional status and eating behaviors after transitioning from a phenylalanine (Phe)-restrict...

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Bibliographic Details
Main Authors:	Krista Viau, Leslie Martell, Ann Wessel, Fran Rohr, Suzanne Hollander, Melissa S. Putman, Stephanie Sacharow
Format:	Article
Language:	English
Published:	Elsevier 2023-12-01
Series:	Molecular Genetics and Metabolism Reports
Subjects:	Phenylketonuria Pegvaliase Nutritional status Protein intake Body composition Eating behaviors
Online Access:	http://www.sciencedirect.com/science/article/pii/S2214426923000617

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