A surgical management of melanotic prognoma tumor of Infancy – A case report
Abstract- Melanotic neuroectodermal tumor of infancy (MNTI) is a rare condition that typically presents within the first 6 months of life. It rarely metastasizes but is locally aggressive. Melanotic neuroectodermal tumor of infancy has been reported under several other names including retinal an...
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| Format: | Article |
| Language: | English |
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Tehran University of Medical Sciences
2023-09-01
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| Series: | Basic & Clinical Cancer Research |
| Subjects: | |
| Online Access: | https://bccr.tums.ac.ir/index.php/bccrj/article/view/448 |
| _version_ | 1827792752760324096 |
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| author | Dr jitendra Hazarey Shilpa Hazare Shilpa Hazare Dr. Isha Hazarey Dr. Pritish Bhansali Dr. Vishal Mahant Dr. Rashiqua Sadiya |
| author_facet | Dr jitendra Hazarey Shilpa Hazare Shilpa Hazare Dr. Isha Hazarey Dr. Pritish Bhansali Dr. Vishal Mahant Dr. Rashiqua Sadiya |
| author_sort | Dr jitendra Hazarey |
| collection | DOAJ |
| description |
Abstract-
Melanotic neuroectodermal tumor of infancy (MNTI) is a rare condition that typically presents within the first 6 months of life. It rarely metastasizes but is locally aggressive. Melanotic neuroectodermal tumor of infancy has been reported under several other names including retinal anlage tumor and melanotic progonoma. Most commonly, melanotic neuroectodermal tumor of infancy originates in the maxilla. Tumor in previously reported cases are known to originate from different structures. Recommended treatment of MNTI consists of complete excision with wide tissue margins, although success has been reported after incomplete resection too. For those patients in whom surgical resection is not a preferred option, various chemotherapy approaches have been reported with mixed results ranging from failure to sustained tumor regression. In the present case report we have case of MNTI in one year infant which is successfully treated with subtotal excision.
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| first_indexed | 2024-03-11T18:07:45Z |
| format | Article |
| id | doaj.art-dfe26d1b6904453fadd9d10f87edd5fc |
| institution | Directory Open Access Journal |
| issn | 2228-6527 2228-5466 |
| language | English |
| last_indexed | 2024-03-11T18:07:45Z |
| publishDate | 2023-09-01 |
| publisher | Tehran University of Medical Sciences |
| record_format | Article |
| series | Basic & Clinical Cancer Research |
| spelling | doaj.art-dfe26d1b6904453fadd9d10f87edd5fc2023-10-17T05:05:06ZengTehran University of Medical SciencesBasic & Clinical Cancer Research2228-65272228-54662023-09-01143A surgical management of melanotic prognoma tumor of Infancy – A case reportDr jitendra Hazarey0Shilpa Hazare1Shilpa Hazare2Dr. Isha Hazarey3Dr. Pritish Bhansali4Dr. Vishal Mahant5Dr. Rashiqua Sadiya6MBBS MS, MChMBBS, MS, DCH, DNBMBBS, MS, DCH, DNBJawaharlal Nehru Medical College, Sawangi, WardhaResident Doctor at Dept. of Pediatric,MBBS, DCH Consultant at Dept. Of PediatricsBAMS Resident Doctor at Dept. of Pediatrics, Abstract- Melanotic neuroectodermal tumor of infancy (MNTI) is a rare condition that typically presents within the first 6 months of life. It rarely metastasizes but is locally aggressive. Melanotic neuroectodermal tumor of infancy has been reported under several other names including retinal anlage tumor and melanotic progonoma. Most commonly, melanotic neuroectodermal tumor of infancy originates in the maxilla. Tumor in previously reported cases are known to originate from different structures. Recommended treatment of MNTI consists of complete excision with wide tissue margins, although success has been reported after incomplete resection too. For those patients in whom surgical resection is not a preferred option, various chemotherapy approaches have been reported with mixed results ranging from failure to sustained tumor regression. In the present case report we have case of MNTI in one year infant which is successfully treated with subtotal excision. https://bccr.tums.ac.ir/index.php/bccrj/article/view/448case reportLump in the maxillamaxilla tumormarginal mandibulectomymelanotic neuroectodermal tumor of infancy. |
| spellingShingle | Dr jitendra Hazarey Shilpa Hazare Shilpa Hazare Dr. Isha Hazarey Dr. Pritish Bhansali Dr. Vishal Mahant Dr. Rashiqua Sadiya A surgical management of melanotic prognoma tumor of Infancy – A case report Basic & Clinical Cancer Research case report Lump in the maxilla maxilla tumor marginal mandibulectomy melanotic neuroectodermal tumor of infancy. |
| title | A surgical management of melanotic prognoma tumor of Infancy – A case report |
| title_full | A surgical management of melanotic prognoma tumor of Infancy – A case report |
| title_fullStr | A surgical management of melanotic prognoma tumor of Infancy – A case report |
| title_full_unstemmed | A surgical management of melanotic prognoma tumor of Infancy – A case report |
| title_short | A surgical management of melanotic prognoma tumor of Infancy – A case report |
| title_sort | surgical management of melanotic prognoma tumor of infancy a case report |
| topic | case report Lump in the maxilla maxilla tumor marginal mandibulectomy melanotic neuroectodermal tumor of infancy. |
| url | https://bccr.tums.ac.ir/index.php/bccrj/article/view/448 |
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