Immunoproliferative Small Intestine Disease (IPSID): A Case Report
Immunoproliferative small intestinal disease (IPSID) is the syndrome associated with Mediterranean lymphoma (a rare form of non-Hodgkin’s lymphoma). Many of the patients diagnosed with secretory IPSID have variable level of abnormal immunoglobulins in serum or other bodily fluids, identified as trun...
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Format: | Article |
Language: | English |
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Mashhad University of Medical Sciences
2015-03-01
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Series: | International Journal of Pediatrics |
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Online Access: | http://ijp.mums.ac.ir/pdf_4056_5b95c2cc866403ca2a4203a81ef85882.html |
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author | Farid Imanzadeh Aliakbar Sayarri Pantea Tajik |
author_facet | Farid Imanzadeh Aliakbar Sayarri Pantea Tajik |
author_sort | Farid Imanzadeh |
collection | DOAJ |
description | Immunoproliferative small intestinal disease (IPSID) is the syndrome associated with Mediterranean lymphoma (a rare form of non-Hodgkin’s lymphoma). Many of the patients diagnosed with secretory IPSID have variable level of abnormal immunoglobulins in serum or other bodily fluids, identified as truncated alpha heavy chain globulins. Most cases are characterized by a loss of ability to synthesize light chains. As such, IPSID has been classified as a heavy chain disorder B-cell lymphoma. We present here the case of a 12-year-old boy admitted in our department for edema, abdominal pain and FTT, in whom we suspected the diagnosis of IPSID. |
first_indexed | 2024-04-11T22:20:30Z |
format | Article |
id | doaj.art-e0391eefaac14c45be18934b1201f965 |
institution | Directory Open Access Journal |
issn | 2345-5047 2345-5055 |
language | English |
last_indexed | 2024-04-11T22:20:30Z |
publishDate | 2015-03-01 |
publisher | Mashhad University of Medical Sciences |
record_format | Article |
series | International Journal of Pediatrics |
spelling | doaj.art-e0391eefaac14c45be18934b1201f9652022-12-22T04:00:13ZengMashhad University of Medical SciencesInternational Journal of Pediatrics2345-50472345-50552015-03-0132.189924056Immunoproliferative Small Intestine Disease (IPSID): A Case ReportFarid Imanzadeh0Aliakbar Sayarri1Pantea Tajik2Professor of Children Gastroenterology, Gastroenterology Unit, Mofid Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran.Professor of Children Gastroenterology, Gastroenterology Unit, Mofid Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran.Fellow of Children Gastroenterology, Gastroenterology Unit, Mofid Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran.Immunoproliferative small intestinal disease (IPSID) is the syndrome associated with Mediterranean lymphoma (a rare form of non-Hodgkin’s lymphoma). Many of the patients diagnosed with secretory IPSID have variable level of abnormal immunoglobulins in serum or other bodily fluids, identified as truncated alpha heavy chain globulins. Most cases are characterized by a loss of ability to synthesize light chains. As such, IPSID has been classified as a heavy chain disorder B-cell lymphoma. We present here the case of a 12-year-old boy admitted in our department for edema, abdominal pain and FTT, in whom we suspected the diagnosis of IPSID.http://ijp.mums.ac.ir/pdf_4056_5b95c2cc866403ca2a4203a81ef85882.htmlImmunoproliferative Small Intestine DiseaseCase ReportEvaluation |
spellingShingle | Farid Imanzadeh Aliakbar Sayarri Pantea Tajik Immunoproliferative Small Intestine Disease (IPSID): A Case Report International Journal of Pediatrics Immunoproliferative Small Intestine Disease Case Report Evaluation |
title | Immunoproliferative Small Intestine Disease (IPSID): A Case Report |
title_full | Immunoproliferative Small Intestine Disease (IPSID): A Case Report |
title_fullStr | Immunoproliferative Small Intestine Disease (IPSID): A Case Report |
title_full_unstemmed | Immunoproliferative Small Intestine Disease (IPSID): A Case Report |
title_short | Immunoproliferative Small Intestine Disease (IPSID): A Case Report |
title_sort | immunoproliferative small intestine disease ipsid a case report |
topic | Immunoproliferative Small Intestine Disease Case Report Evaluation |
url | http://ijp.mums.ac.ir/pdf_4056_5b95c2cc866403ca2a4203a81ef85882.html |
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