Immunoproliferative Small Intestine Disease (IPSID): A Case Report

Immunoproliferative small intestinal disease (IPSID) is the syndrome associated with Mediterranean lymphoma (a rare form of non-Hodgkin’s lymphoma). Many of the patients diagnosed with secretory IPSID have variable level of abnormal immunoglobulins in serum or other bodily fluids, identified as trun...

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Main Authors: Farid Imanzadeh, Aliakbar Sayarri, Pantea Tajik
Format: Article
Language:English
Published: Mashhad University of Medical Sciences 2015-03-01
Series:International Journal of Pediatrics
Subjects:
Online Access:http://ijp.mums.ac.ir/pdf_4056_5b95c2cc866403ca2a4203a81ef85882.html
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author Farid Imanzadeh
Aliakbar Sayarri
Pantea Tajik
author_facet Farid Imanzadeh
Aliakbar Sayarri
Pantea Tajik
author_sort Farid Imanzadeh
collection DOAJ
description Immunoproliferative small intestinal disease (IPSID) is the syndrome associated with Mediterranean lymphoma (a rare form of non-Hodgkin’s lymphoma). Many of the patients diagnosed with secretory IPSID have variable level of abnormal immunoglobulins in serum or other bodily fluids, identified as truncated alpha heavy chain globulins. Most cases are characterized by a loss of ability to synthesize light chains. As such, IPSID has been classified as a heavy chain disorder B-cell lymphoma. We present here the case of a 12-year-old boy admitted in our department for edema, abdominal pain and FTT, in whom we suspected the diagnosis of IPSID.
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spelling doaj.art-e0391eefaac14c45be18934b1201f9652022-12-22T04:00:13ZengMashhad University of Medical SciencesInternational Journal of Pediatrics2345-50472345-50552015-03-0132.189924056Immunoproliferative Small Intestine Disease (IPSID): A Case ReportFarid Imanzadeh0Aliakbar Sayarri1Pantea Tajik2Professor of Children Gastroenterology, Gastroenterology Unit, Mofid Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran.Professor of Children Gastroenterology, Gastroenterology Unit, Mofid Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran.Fellow of Children Gastroenterology, Gastroenterology Unit, Mofid Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran.Immunoproliferative small intestinal disease (IPSID) is the syndrome associated with Mediterranean lymphoma (a rare form of non-Hodgkin’s lymphoma). Many of the patients diagnosed with secretory IPSID have variable level of abnormal immunoglobulins in serum or other bodily fluids, identified as truncated alpha heavy chain globulins. Most cases are characterized by a loss of ability to synthesize light chains. As such, IPSID has been classified as a heavy chain disorder B-cell lymphoma. We present here the case of a 12-year-old boy admitted in our department for edema, abdominal pain and FTT, in whom we suspected the diagnosis of IPSID.http://ijp.mums.ac.ir/pdf_4056_5b95c2cc866403ca2a4203a81ef85882.htmlImmunoproliferative Small Intestine DiseaseCase ReportEvaluation
spellingShingle Farid Imanzadeh
Aliakbar Sayarri
Pantea Tajik
Immunoproliferative Small Intestine Disease (IPSID): A Case Report
International Journal of Pediatrics
Immunoproliferative Small Intestine Disease
Case Report
Evaluation
title Immunoproliferative Small Intestine Disease (IPSID): A Case Report
title_full Immunoproliferative Small Intestine Disease (IPSID): A Case Report
title_fullStr Immunoproliferative Small Intestine Disease (IPSID): A Case Report
title_full_unstemmed Immunoproliferative Small Intestine Disease (IPSID): A Case Report
title_short Immunoproliferative Small Intestine Disease (IPSID): A Case Report
title_sort immunoproliferative small intestine disease ipsid a case report
topic Immunoproliferative Small Intestine Disease
Case Report
Evaluation
url http://ijp.mums.ac.ir/pdf_4056_5b95c2cc866403ca2a4203a81ef85882.html
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AT aliakbarsayarri immunoproliferativesmallintestinediseaseipsidacasereport
AT panteatajik immunoproliferativesmallintestinediseaseipsidacasereport