Localization of nervonic acid β-oxidation in human and rodent peroxisomes: impaired oxidation in Zellweger syndrome and X-linked adrenoleukodystrophy
Studies with purified subcellular organelles from rat liver indicate that nervonic acid (C24:1) is β-oxidized preferentially in peroxisomes. Lack of effect by etomoxir, inhibitor of mitochondrial β-oxidation, on β-oxidation of lignoceric acid (C24:0), a peroxisomal function, and that of nervonic aci...
Main Authors: | Rajat Sandhir, Mushfiquddin Khan, Amarjit Chahal, Inderjit Singh |
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Format: | Article |
Language: | English |
Published: |
Elsevier
1998-11-01
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Series: | Journal of Lipid Research |
Subjects: | |
Online Access: | http://www.sciencedirect.com/science/article/pii/S0022227520324718 |
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