Catheter Ablation of Reentrant Left Ventricular Tachycardia Associated with Fabry disease: A Case Report
A 51-year-old man, who was diagnosed with Fabry disease resulting from a kidney biopsy for proteinuria and renal failure in 2002, was admitted to our hospital for sustained ventricular tachycardia (VT). In the electrophysiological study, VT (cycle length: 310 ms) was successfully induced by right ve...
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| Format: | Article |
| Language: | English |
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Wiley
2010-01-01
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| Series: | Journal of Arrhythmia |
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| Online Access: | http://www.sciencedirect.com/science/article/pii/S1880427610800092 |
| _version_ | 1818353289166585856 |
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| author | Emi Nakano, MD Tomoo Harada, MD Kyoko Soejima, MD Toshio Sasaki, MD Koichi Mizuno, MD Fumihiko Miyake, MD |
| author_facet | Emi Nakano, MD Tomoo Harada, MD Kyoko Soejima, MD Toshio Sasaki, MD Koichi Mizuno, MD Fumihiko Miyake, MD |
| author_sort | Emi Nakano, MD |
| collection | DOAJ |
| description | A 51-year-old man, who was diagnosed with Fabry disease resulting from a kidney biopsy for proteinuria and renal failure in 2002, was admitted to our hospital for sustained ventricular tachycardia (VT). In the electrophysiological study, VT (cycle length: 310 ms) was successfully induced by right ventricle programmed stimulation and the twelve-lead electrocardiogram showed a right bundle branch block configuration with right axis deviation. The mechanism of the VT was considered to be reentry by entrainment phenomenon. An electro-anatomical mapping system identified a low voltage area located close to the left ventricular anterior-apical wall. During VT an isolated pre-potential was recorded 42 ms prior to the QRS onset near the border zone which was located between the low and normal voltage areas. At this mapping site entrainment with fusion and a post-pacing interval that matched the VT cycle length were observed. A radiofrequency energy delivery at this site terminated the VT after 35 seconds. The entrainment mapping could be useful for identifying a critical reentry circuit path. This case is the first description of reentrant VT originating from the thickened left ventricle wall in a patient with Fabry disease. |
| first_indexed | 2024-12-13T19:07:10Z |
| format | Article |
| id | doaj.art-e290a04098d24cc5adcfe02a7d0e77da |
| institution | Directory Open Access Journal |
| issn | 1880-4276 |
| language | English |
| last_indexed | 2024-12-13T19:07:10Z |
| publishDate | 2010-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Journal of Arrhythmia |
| spelling | doaj.art-e290a04098d24cc5adcfe02a7d0e77da2022-12-21T23:34:30ZengWileyJournal of Arrhythmia1880-42762010-01-0126320921510.1016/S1880-4276(10)80009-2Catheter Ablation of Reentrant Left Ventricular Tachycardia Associated with Fabry disease: A Case ReportEmi Nakano, MD0Tomoo Harada, MD1Kyoko Soejima, MD2Toshio Sasaki, MD3Koichi Mizuno, MD4Fumihiko Miyake, MD5Cardiovascular Division, Kawasaki Municipal Tama HospitalCardiovascular Division, Kawasaki Municipal Tama HospitalCardiovascular Division, Kawasaki Municipal Tama HospitalCardiovascular Division, Kawasaki Municipal Tama HospitalCardiovascular Division, Kawasaki Municipal Tama HospitalCardiovascular Division, St. Marianna University School of MedicineA 51-year-old man, who was diagnosed with Fabry disease resulting from a kidney biopsy for proteinuria and renal failure in 2002, was admitted to our hospital for sustained ventricular tachycardia (VT). In the electrophysiological study, VT (cycle length: 310 ms) was successfully induced by right ventricle programmed stimulation and the twelve-lead electrocardiogram showed a right bundle branch block configuration with right axis deviation. The mechanism of the VT was considered to be reentry by entrainment phenomenon. An electro-anatomical mapping system identified a low voltage area located close to the left ventricular anterior-apical wall. During VT an isolated pre-potential was recorded 42 ms prior to the QRS onset near the border zone which was located between the low and normal voltage areas. At this mapping site entrainment with fusion and a post-pacing interval that matched the VT cycle length were observed. A radiofrequency energy delivery at this site terminated the VT after 35 seconds. The entrainment mapping could be useful for identifying a critical reentry circuit path. This case is the first description of reentrant VT originating from the thickened left ventricle wall in a patient with Fabry disease.http://www.sciencedirect.com/science/article/pii/S1880427610800092Fabry diseaseVentricular tachycardiaCatheter ablationReentry |
| spellingShingle | Emi Nakano, MD Tomoo Harada, MD Kyoko Soejima, MD Toshio Sasaki, MD Koichi Mizuno, MD Fumihiko Miyake, MD Catheter Ablation of Reentrant Left Ventricular Tachycardia Associated with Fabry disease: A Case Report Journal of Arrhythmia Fabry disease Ventricular tachycardia Catheter ablation Reentry |
| title | Catheter Ablation of Reentrant Left Ventricular Tachycardia Associated with Fabry disease: A Case Report |
| title_full | Catheter Ablation of Reentrant Left Ventricular Tachycardia Associated with Fabry disease: A Case Report |
| title_fullStr | Catheter Ablation of Reentrant Left Ventricular Tachycardia Associated with Fabry disease: A Case Report |
| title_full_unstemmed | Catheter Ablation of Reentrant Left Ventricular Tachycardia Associated with Fabry disease: A Case Report |
| title_short | Catheter Ablation of Reentrant Left Ventricular Tachycardia Associated with Fabry disease: A Case Report |
| title_sort | catheter ablation of reentrant left ventricular tachycardia associated with fabry disease a case report |
| topic | Fabry disease Ventricular tachycardia Catheter ablation Reentry |
| url | http://www.sciencedirect.com/science/article/pii/S1880427610800092 |
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