Anomalous Origin of Left Coronary Artery From Right Pulmonary Artery in Association With Scimitar Syndrome

This paper reports a unique case of anomalous origin of the left coronary artery from the right pulmonary artery associated with scimitar syndrome. The presence of pulmonary hypertension may have contributed to maintain coronary perfusion, which likely prevented early significant coronary steal. Thi...

Full description

Bibliographic Details
Main Authors: Safwat A. Aly, MD, Ramiro W. Lizano Santamaria, MD, Shi-Joon Yoo, MD
Format: Article
Language:English
Published: Elsevier 2020-02-01
Series:JACC: Case Reports
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2666084919305893
_version_ 1819063931780464640
author Safwat A. Aly, MD
Ramiro W. Lizano Santamaria, MD
Shi-Joon Yoo, MD
author_facet Safwat A. Aly, MD
Ramiro W. Lizano Santamaria, MD
Shi-Joon Yoo, MD
author_sort Safwat A. Aly, MD
collection DOAJ
description This paper reports a unique case of anomalous origin of the left coronary artery from the right pulmonary artery associated with scimitar syndrome. The presence of pulmonary hypertension may have contributed to maintain coronary perfusion, which likely prevented early significant coronary steal. This study reports the clinical course, diagnosis challenges, and management strategy. (Level of Difficulty: Intermediate.)
first_indexed 2024-12-21T15:22:31Z
format Article
id doaj.art-e48bffdfbf3843f096bf40cd9c31c7e6
institution Directory Open Access Journal
issn 2666-0849
language English
last_indexed 2024-12-21T15:22:31Z
publishDate 2020-02-01
publisher Elsevier
record_format Article
series JACC: Case Reports
spelling doaj.art-e48bffdfbf3843f096bf40cd9c31c7e62022-12-21T18:59:00ZengElsevierJACC: Case Reports2666-08492020-02-0122319323Anomalous Origin of Left Coronary Artery From Right Pulmonary Artery in Association With Scimitar SyndromeSafwat A. Aly, MD0Ramiro W. Lizano Santamaria, MD1Shi-Joon Yoo, MD2Address for correspondence: Dr. Safwat Aly, Pediatric Cardiology Division, The Hospital for Sick Children, University of Toronto, 555 University Avenue, Toronto, Ontario M4G1X8, Canada.; Department of Pediatrics, Division of Cardiology, the Hospital for Sick Children, University of Toronto, Toronto, Ontario, CanadaDepartment of Pediatrics, Division of Cardiology, the Hospital for Sick Children, University of Toronto, Toronto, Ontario, CanadaDepartment of Pediatrics, Division of Cardiology, the Hospital for Sick Children, University of Toronto, Toronto, Ontario, CanadaThis paper reports a unique case of anomalous origin of the left coronary artery from the right pulmonary artery associated with scimitar syndrome. The presence of pulmonary hypertension may have contributed to maintain coronary perfusion, which likely prevented early significant coronary steal. This study reports the clinical course, diagnosis challenges, and management strategy. (Level of Difficulty: Intermediate.)http://www.sciencedirect.com/science/article/pii/S2666084919305893ALCAPAAP collateralsFRAS1 mutationscimitar syndrome
spellingShingle Safwat A. Aly, MD
Ramiro W. Lizano Santamaria, MD
Shi-Joon Yoo, MD
Anomalous Origin of Left Coronary Artery From Right Pulmonary Artery in Association With Scimitar Syndrome
JACC: Case Reports
ALCAPA
AP collaterals
FRAS1 mutation
scimitar syndrome
title Anomalous Origin of Left Coronary Artery From Right Pulmonary Artery in Association With Scimitar Syndrome
title_full Anomalous Origin of Left Coronary Artery From Right Pulmonary Artery in Association With Scimitar Syndrome
title_fullStr Anomalous Origin of Left Coronary Artery From Right Pulmonary Artery in Association With Scimitar Syndrome
title_full_unstemmed Anomalous Origin of Left Coronary Artery From Right Pulmonary Artery in Association With Scimitar Syndrome
title_short Anomalous Origin of Left Coronary Artery From Right Pulmonary Artery in Association With Scimitar Syndrome
title_sort anomalous origin of left coronary artery from right pulmonary artery in association with scimitar syndrome
topic ALCAPA
AP collaterals
FRAS1 mutation
scimitar syndrome
url http://www.sciencedirect.com/science/article/pii/S2666084919305893
work_keys_str_mv AT safwataalymd anomalousoriginofleftcoronaryarteryfromrightpulmonaryarteryinassociationwithscimitarsyndrome
AT ramirowlizanosantamariamd anomalousoriginofleftcoronaryarteryfromrightpulmonaryarteryinassociationwithscimitarsyndrome
AT shijoonyoomd anomalousoriginofleftcoronaryarteryfromrightpulmonaryarteryinassociationwithscimitarsyndrome