Anomalous Origin of Left Coronary Artery From Right Pulmonary Artery in Association With Scimitar Syndrome
This paper reports a unique case of anomalous origin of the left coronary artery from the right pulmonary artery associated with scimitar syndrome. The presence of pulmonary hypertension may have contributed to maintain coronary perfusion, which likely prevented early significant coronary steal. Thi...
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Format: | Article |
Language: | English |
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Elsevier
2020-02-01
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Series: | JACC: Case Reports |
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Online Access: | http://www.sciencedirect.com/science/article/pii/S2666084919305893 |
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author | Safwat A. Aly, MD Ramiro W. Lizano Santamaria, MD Shi-Joon Yoo, MD |
author_facet | Safwat A. Aly, MD Ramiro W. Lizano Santamaria, MD Shi-Joon Yoo, MD |
author_sort | Safwat A. Aly, MD |
collection | DOAJ |
description | This paper reports a unique case of anomalous origin of the left coronary artery from the right pulmonary artery associated with scimitar syndrome. The presence of pulmonary hypertension may have contributed to maintain coronary perfusion, which likely prevented early significant coronary steal. This study reports the clinical course, diagnosis challenges, and management strategy. (Level of Difficulty: Intermediate.) |
first_indexed | 2024-12-21T15:22:31Z |
format | Article |
id | doaj.art-e48bffdfbf3843f096bf40cd9c31c7e6 |
institution | Directory Open Access Journal |
issn | 2666-0849 |
language | English |
last_indexed | 2024-12-21T15:22:31Z |
publishDate | 2020-02-01 |
publisher | Elsevier |
record_format | Article |
series | JACC: Case Reports |
spelling | doaj.art-e48bffdfbf3843f096bf40cd9c31c7e62022-12-21T18:59:00ZengElsevierJACC: Case Reports2666-08492020-02-0122319323Anomalous Origin of Left Coronary Artery From Right Pulmonary Artery in Association With Scimitar SyndromeSafwat A. Aly, MD0Ramiro W. Lizano Santamaria, MD1Shi-Joon Yoo, MD2Address for correspondence: Dr. Safwat Aly, Pediatric Cardiology Division, The Hospital for Sick Children, University of Toronto, 555 University Avenue, Toronto, Ontario M4G1X8, Canada.; Department of Pediatrics, Division of Cardiology, the Hospital for Sick Children, University of Toronto, Toronto, Ontario, CanadaDepartment of Pediatrics, Division of Cardiology, the Hospital for Sick Children, University of Toronto, Toronto, Ontario, CanadaDepartment of Pediatrics, Division of Cardiology, the Hospital for Sick Children, University of Toronto, Toronto, Ontario, CanadaThis paper reports a unique case of anomalous origin of the left coronary artery from the right pulmonary artery associated with scimitar syndrome. The presence of pulmonary hypertension may have contributed to maintain coronary perfusion, which likely prevented early significant coronary steal. This study reports the clinical course, diagnosis challenges, and management strategy. (Level of Difficulty: Intermediate.)http://www.sciencedirect.com/science/article/pii/S2666084919305893ALCAPAAP collateralsFRAS1 mutationscimitar syndrome |
spellingShingle | Safwat A. Aly, MD Ramiro W. Lizano Santamaria, MD Shi-Joon Yoo, MD Anomalous Origin of Left Coronary Artery From Right Pulmonary Artery in Association With Scimitar Syndrome JACC: Case Reports ALCAPA AP collaterals FRAS1 mutation scimitar syndrome |
title | Anomalous Origin of Left Coronary Artery From Right Pulmonary Artery in Association With Scimitar Syndrome |
title_full | Anomalous Origin of Left Coronary Artery From Right Pulmonary Artery in Association With Scimitar Syndrome |
title_fullStr | Anomalous Origin of Left Coronary Artery From Right Pulmonary Artery in Association With Scimitar Syndrome |
title_full_unstemmed | Anomalous Origin of Left Coronary Artery From Right Pulmonary Artery in Association With Scimitar Syndrome |
title_short | Anomalous Origin of Left Coronary Artery From Right Pulmonary Artery in Association With Scimitar Syndrome |
title_sort | anomalous origin of left coronary artery from right pulmonary artery in association with scimitar syndrome |
topic | ALCAPA AP collaterals FRAS1 mutation scimitar syndrome |
url | http://www.sciencedirect.com/science/article/pii/S2666084919305893 |
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