An extremely rare cause of Eisenmenger syndrome

Persistent Truncus Arteriosus (PTA) is an extremely rare defect accounting for under 1% of all congenital heart disease, and over 85% of patients succumb to heart failure in infancy. We report a case of van Praagh type A3 PTA, which represents its rarest variant and accounts for only 8–10% of all pa...

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Main Authors: Milind S. Phadke, Girish R. Sabnis, Devendra V. Patil, Charan P. Lanjewar, Prafulla G. Kerkar
Format: Article
Language:English
Published: Elsevier 2014-11-01
Series:Indian Heart Journal
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S0019483214006968
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author Milind S. Phadke
Girish R. Sabnis
Devendra V. Patil
Charan P. Lanjewar
Prafulla G. Kerkar
author_facet Milind S. Phadke
Girish R. Sabnis
Devendra V. Patil
Charan P. Lanjewar
Prafulla G. Kerkar
author_sort Milind S. Phadke
collection DOAJ
description Persistent Truncus Arteriosus (PTA) is an extremely rare defect accounting for under 1% of all congenital heart disease, and over 85% of patients succumb to heart failure in infancy. We report a case of van Praagh type A3 PTA, which represents its rarest variant and accounts for only 8–10% of all patients with PTA. The presence of ductal stenosis in such cases is further exceedingly rare.
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spelling doaj.art-e5066db119874d3e90e9d8cb7f56f4c82022-12-21T18:46:36ZengElsevierIndian Heart Journal0019-48322014-11-0166673773910.1016/j.ihj.2014.10.397An extremely rare cause of Eisenmenger syndromeMilind S. Phadke0Girish R. Sabnis1Devendra V. Patil2Charan P. Lanjewar3Prafulla G. Kerkar4Assistant Professor, Department of Cardiology, Seth G S Medical College & The King Edward VII Memorial Hospital, Mumbai, IndiaResident, Department of Cardiology, Seth G S Medical College & The King Edward VII Memorial Hospital, Mumbai, IndiaResident, Department of Cardiology, CVTC Building, Seth G S Medical College & The King Edward VII Memorial Hospital, Mumbai 400012, MH, IndiaAssociate Professor, Department of Cardiology, Seth G S Medical College & The King Edward VII Memorial Hospital, Mumbai, IndiaProfessor & Head, Department of Cardiology, Seth G S Medical College & The King Edward VII Memorial Hospital, Mumbai, IndiaPersistent Truncus Arteriosus (PTA) is an extremely rare defect accounting for under 1% of all congenital heart disease, and over 85% of patients succumb to heart failure in infancy. We report a case of van Praagh type A3 PTA, which represents its rarest variant and accounts for only 8–10% of all patients with PTA. The presence of ductal stenosis in such cases is further exceedingly rare.http://www.sciencedirect.com/science/article/pii/S0019483214006968Persistent truncus arteriosusvan Praagh type A3Eisenmenger syndrome
spellingShingle Milind S. Phadke
Girish R. Sabnis
Devendra V. Patil
Charan P. Lanjewar
Prafulla G. Kerkar
An extremely rare cause of Eisenmenger syndrome
Indian Heart Journal
Persistent truncus arteriosus
van Praagh type A3
Eisenmenger syndrome
title An extremely rare cause of Eisenmenger syndrome
title_full An extremely rare cause of Eisenmenger syndrome
title_fullStr An extremely rare cause of Eisenmenger syndrome
title_full_unstemmed An extremely rare cause of Eisenmenger syndrome
title_short An extremely rare cause of Eisenmenger syndrome
title_sort extremely rare cause of eisenmenger syndrome
topic Persistent truncus arteriosus
van Praagh type A3
Eisenmenger syndrome
url http://www.sciencedirect.com/science/article/pii/S0019483214006968
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