An extremely rare cause of Eisenmenger syndrome
Persistent Truncus Arteriosus (PTA) is an extremely rare defect accounting for under 1% of all congenital heart disease, and over 85% of patients succumb to heart failure in infancy. We report a case of van Praagh type A3 PTA, which represents its rarest variant and accounts for only 8–10% of all pa...
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Format: | Article |
Language: | English |
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Elsevier
2014-11-01
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Series: | Indian Heart Journal |
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Online Access: | http://www.sciencedirect.com/science/article/pii/S0019483214006968 |
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author | Milind S. Phadke Girish R. Sabnis Devendra V. Patil Charan P. Lanjewar Prafulla G. Kerkar |
author_facet | Milind S. Phadke Girish R. Sabnis Devendra V. Patil Charan P. Lanjewar Prafulla G. Kerkar |
author_sort | Milind S. Phadke |
collection | DOAJ |
description | Persistent Truncus Arteriosus (PTA) is an extremely rare defect accounting for under 1% of all congenital heart disease, and over 85% of patients succumb to heart failure in infancy. We report a case of van Praagh type A3 PTA, which represents its rarest variant and accounts for only 8–10% of all patients with PTA. The presence of ductal stenosis in such cases is further exceedingly rare. |
first_indexed | 2024-12-21T23:27:09Z |
format | Article |
id | doaj.art-e5066db119874d3e90e9d8cb7f56f4c8 |
institution | Directory Open Access Journal |
issn | 0019-4832 |
language | English |
last_indexed | 2024-12-21T23:27:09Z |
publishDate | 2014-11-01 |
publisher | Elsevier |
record_format | Article |
series | Indian Heart Journal |
spelling | doaj.art-e5066db119874d3e90e9d8cb7f56f4c82022-12-21T18:46:36ZengElsevierIndian Heart Journal0019-48322014-11-0166673773910.1016/j.ihj.2014.10.397An extremely rare cause of Eisenmenger syndromeMilind S. Phadke0Girish R. Sabnis1Devendra V. Patil2Charan P. Lanjewar3Prafulla G. Kerkar4Assistant Professor, Department of Cardiology, Seth G S Medical College & The King Edward VII Memorial Hospital, Mumbai, IndiaResident, Department of Cardiology, Seth G S Medical College & The King Edward VII Memorial Hospital, Mumbai, IndiaResident, Department of Cardiology, CVTC Building, Seth G S Medical College & The King Edward VII Memorial Hospital, Mumbai 400012, MH, IndiaAssociate Professor, Department of Cardiology, Seth G S Medical College & The King Edward VII Memorial Hospital, Mumbai, IndiaProfessor & Head, Department of Cardiology, Seth G S Medical College & The King Edward VII Memorial Hospital, Mumbai, IndiaPersistent Truncus Arteriosus (PTA) is an extremely rare defect accounting for under 1% of all congenital heart disease, and over 85% of patients succumb to heart failure in infancy. We report a case of van Praagh type A3 PTA, which represents its rarest variant and accounts for only 8–10% of all patients with PTA. The presence of ductal stenosis in such cases is further exceedingly rare.http://www.sciencedirect.com/science/article/pii/S0019483214006968Persistent truncus arteriosusvan Praagh type A3Eisenmenger syndrome |
spellingShingle | Milind S. Phadke Girish R. Sabnis Devendra V. Patil Charan P. Lanjewar Prafulla G. Kerkar An extremely rare cause of Eisenmenger syndrome Indian Heart Journal Persistent truncus arteriosus van Praagh type A3 Eisenmenger syndrome |
title | An extremely rare cause of Eisenmenger syndrome |
title_full | An extremely rare cause of Eisenmenger syndrome |
title_fullStr | An extremely rare cause of Eisenmenger syndrome |
title_full_unstemmed | An extremely rare cause of Eisenmenger syndrome |
title_short | An extremely rare cause of Eisenmenger syndrome |
title_sort | extremely rare cause of eisenmenger syndrome |
topic | Persistent truncus arteriosus van Praagh type A3 Eisenmenger syndrome |
url | http://www.sciencedirect.com/science/article/pii/S0019483214006968 |
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