Airway management of a child with frontometaphyseal dysplasia (Gorlin Cohen syndrome)
Frontometaphyseal dysplasia (FMD), also called Gorlin-Cohen syndrome, is a rare hereditary X-linked dominant craniotubular bone disorder. The presentation describes the airway management of a 2-year-old child suffering from FMD with significant retrognathia, posted for major long bone corrective ost...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2014-01-01
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| Series: | Journal of Anaesthesiology Clinical Pharmacology |
| Subjects: | |
| Online Access: | http://www.joacp.org/article.asp?issn=0970-9185;year=2014;volume=30;issue=2;spage=279;epage=280;aulast=Ganigara |
| _version_ | 1818015730575081472 |
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| author | Anuradha Ganigara Madhavi Nishtala Yabagodu Rama Vakoda Chandrika Kunigal Ravishankar Chandrakala |
| author_facet | Anuradha Ganigara Madhavi Nishtala Yabagodu Rama Vakoda Chandrika Kunigal Ravishankar Chandrakala |
| author_sort | Anuradha Ganigara |
| collection | DOAJ |
| description | Frontometaphyseal dysplasia (FMD), also called Gorlin-Cohen syndrome, is a rare hereditary X-linked dominant craniotubular bone disorder. The presentation describes the airway management of a 2-year-old child suffering from FMD with significant retrognathia, posted for major long bone corrective osteotomy. Induction with a combination of dexmedetomidine and ketamine preceded a successful endotracheal intubation under spontaneous ventilation. |
| first_indexed | 2024-04-14T07:01:54Z |
| format | Article |
| id | doaj.art-e548732ee5c44dd79d968452033682bb |
| institution | Directory Open Access Journal |
| issn | 0970-9185 |
| language | English |
| last_indexed | 2024-04-14T07:01:54Z |
| publishDate | 2014-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Journal of Anaesthesiology Clinical Pharmacology |
| spelling | doaj.art-e548732ee5c44dd79d968452033682bb2022-12-22T02:06:44ZengWolters Kluwer Medknow PublicationsJournal of Anaesthesiology Clinical Pharmacology0970-91852014-01-0130227928010.4103/0970-9185.130100Airway management of a child with frontometaphyseal dysplasia (Gorlin Cohen syndrome)Anuradha GanigaraMadhavi NishtalaYabagodu Rama Vakoda ChandrikaKunigal Ravishankar ChandrakalaFrontometaphyseal dysplasia (FMD), also called Gorlin-Cohen syndrome, is a rare hereditary X-linked dominant craniotubular bone disorder. The presentation describes the airway management of a 2-year-old child suffering from FMD with significant retrognathia, posted for major long bone corrective osteotomy. Induction with a combination of dexmedetomidine and ketamine preceded a successful endotracheal intubation under spontaneous ventilation.http://www.joacp.org/article.asp?issn=0970-9185;year=2014;volume=30;issue=2;spage=279;epage=280;aulast=GanigaraDexmedetomidinedifficult airwayfrontometaphyseal dysplasiaketamine |
| spellingShingle | Anuradha Ganigara Madhavi Nishtala Yabagodu Rama Vakoda Chandrika Kunigal Ravishankar Chandrakala Airway management of a child with frontometaphyseal dysplasia (Gorlin Cohen syndrome) Journal of Anaesthesiology Clinical Pharmacology Dexmedetomidine difficult airway frontometaphyseal dysplasia ketamine |
| title | Airway management of a child with frontometaphyseal dysplasia (Gorlin Cohen syndrome) |
| title_full | Airway management of a child with frontometaphyseal dysplasia (Gorlin Cohen syndrome) |
| title_fullStr | Airway management of a child with frontometaphyseal dysplasia (Gorlin Cohen syndrome) |
| title_full_unstemmed | Airway management of a child with frontometaphyseal dysplasia (Gorlin Cohen syndrome) |
| title_short | Airway management of a child with frontometaphyseal dysplasia (Gorlin Cohen syndrome) |
| title_sort | airway management of a child with frontometaphyseal dysplasia gorlin cohen syndrome |
| topic | Dexmedetomidine difficult airway frontometaphyseal dysplasia ketamine |
| url | http://www.joacp.org/article.asp?issn=0970-9185;year=2014;volume=30;issue=2;spage=279;epage=280;aulast=Ganigara |
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