Management of a Kaposiform haemangioendothelioma of the kidney with Kasabach-Meritt phenomenon without chemotherapy
Kaposiform haemangioendothelioma (KHE) is a benign vascular tumour. While it is not associated with distant spread, it can be locally aggressive and associated with Kasabach-Merritt syndrome (KMS). There were only 2 prior reports of KHE isolated to the kidney, with both having been managed with neoa...
| Main Authors: | , , , , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Elsevier
2016-10-01
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| Series: | Pediatric Hematology Oncology Journal |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S2468124517300013 |
| Summary: | Kaposiform haemangioendothelioma (KHE) is a benign vascular tumour. While it is not associated with distant spread, it can be locally aggressive and associated with Kasabach-Merritt syndrome (KMS). There were only 2 prior reports of KHE isolated to the kidney, with both having been managed with neoadjuvant chemotherapy. We present a case report of renal KHE in a paediatric patient managed instead with upfront surgical resection, and discuss the close interdisciplinary diagnostic and management approach undertaken to facilitate this, and the considerations in the approach. |
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| ISSN: | 2468-1245 |