The specific features of the clinical picture and course of familial dilated cardiomyopathy
Aim. To study prevalence, clinical and hemodynamic features, and life prognosis in patients with familial dilated cardiomyopathy (DCM). Subjects and methods. Two hundred and forty-four patients with DCM were examined during the period 2000 to 2010. According to their medical history records and the...
| Main Authors: | , , |
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| Format: | Article |
| Language: | Russian |
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"Consilium Medicum" Publishing house
2012-10-01
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| Series: | Терапевтический архив |
| Subjects: | |
| Online Access: | https://ter-arkhiv.ru/0040-3660/article/view/31152 |
| _version_ | 1818129492324909056 |
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| author | N A Kurbanov R D Kurbanov T A Abdullaev |
| author_facet | N A Kurbanov R D Kurbanov T A Abdullaev |
| author_sort | N A Kurbanov |
| collection | DOAJ |
| description | Aim. To study prevalence, clinical and hemodynamic features, and life prognosis in patients with familial dilated cardiomyopathy (DCM). Subjects and methods. Two hundred and forty-four patients with DCM were examined during the period 2000 to 2010. According to their medical history records and the results of clinical and functional studies, familial cardiomyopathy was diagnosed in 29 (11.8%) of 244 patients. For comparative assessment, the authors formed two groups: 1) 29 patients with the familial form of DCM and 2) 83 patients with its sporadic form. Their examination included ECG, Holter ECG monitoring, 6-minute walk test, X-ray cardiometry, coronarography, and life prognosis assessment. Results. It has been established that the prevalence of the familial form of DCM accounts for 11.9% and is, unlike its non-familial form, associated with younger age; it is maternally inherited in one third of cases and characterized by the development of complete atrioventricular block in some patients. Conclusion. Investigating the life prognosis of the patients has shown that the familial form and age less than 30 years are characterized by a rapidly progressing course accompanied by a significant increase in death rates within the first 12 follow-up months. |
| first_indexed | 2024-12-11T07:50:00Z |
| format | Article |
| id | doaj.art-e712c037ed624adcace11eb9a2ed3a1b |
| institution | Directory Open Access Journal |
| issn | 0040-3660 2309-5342 |
| language | Russian |
| last_indexed | 2024-12-11T07:50:00Z |
| publishDate | 2012-10-01 |
| publisher | "Consilium Medicum" Publishing house |
| record_format | Article |
| series | Терапевтический архив |
| spelling | doaj.art-e712c037ed624adcace11eb9a2ed3a1b2022-12-22T01:15:22Zrus"Consilium Medicum" Publishing houseТерапевтический архив0040-36602309-53422012-10-018410798528168The specific features of the clinical picture and course of familial dilated cardiomyopathyN A KurbanovR D KurbanovT A AbdullaevAim. To study prevalence, clinical and hemodynamic features, and life prognosis in patients with familial dilated cardiomyopathy (DCM). Subjects and methods. Two hundred and forty-four patients with DCM were examined during the period 2000 to 2010. According to their medical history records and the results of clinical and functional studies, familial cardiomyopathy was diagnosed in 29 (11.8%) of 244 patients. For comparative assessment, the authors formed two groups: 1) 29 patients with the familial form of DCM and 2) 83 patients with its sporadic form. Their examination included ECG, Holter ECG monitoring, 6-minute walk test, X-ray cardiometry, coronarography, and life prognosis assessment. Results. It has been established that the prevalence of the familial form of DCM accounts for 11.9% and is, unlike its non-familial form, associated with younger age; it is maternally inherited in one third of cases and characterized by the development of complete atrioventricular block in some patients. Conclusion. Investigating the life prognosis of the patients has shown that the familial form and age less than 30 years are characterized by a rapidly progressing course accompanied by a significant increase in death rates within the first 12 follow-up months.https://ter-arkhiv.ru/0040-3660/article/view/31152familial dilated cardiomyopathyprevalenceclinical and hemodynamic featureslife prognosis |
| spellingShingle | N A Kurbanov R D Kurbanov T A Abdullaev The specific features of the clinical picture and course of familial dilated cardiomyopathy Терапевтический архив familial dilated cardiomyopathy prevalence clinical and hemodynamic features life prognosis |
| title | The specific features of the clinical picture and course of familial dilated cardiomyopathy |
| title_full | The specific features of the clinical picture and course of familial dilated cardiomyopathy |
| title_fullStr | The specific features of the clinical picture and course of familial dilated cardiomyopathy |
| title_full_unstemmed | The specific features of the clinical picture and course of familial dilated cardiomyopathy |
| title_short | The specific features of the clinical picture and course of familial dilated cardiomyopathy |
| title_sort | specific features of the clinical picture and course of familial dilated cardiomyopathy |
| topic | familial dilated cardiomyopathy prevalence clinical and hemodynamic features life prognosis |
| url | https://ter-arkhiv.ru/0040-3660/article/view/31152 |
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