Surgical treatment of glaucoma associated with the Frank-Kamenetsky’s syndrome (а case report)
Purpose. To submit clinical features and the effectiveness of surgical treatment of patients with glaucoma associated with the Frank-Kamenetsky’s syndrome.Material and method. We examined two patients with the Frank-Kamenetsky’s syndrome. Microinvasive non-penetrating deep sclerectomy was performed...
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| Format: | Article |
| Language: | Russian |
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Publishing house "Ophthalmology"
2015-12-01
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| Series: | Офтальмохирургия |
| Subjects: | |
| Online Access: | https://www.ophthalmosurgery.ru/jour/article/view/182 |
| _version_ | 1797946740987396096 |
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| author | A. V. Sidorova A. V. Opletina K. G. Khliyan A. M. Demchinsky |
| author_facet | A. V. Sidorova A. V. Opletina K. G. Khliyan A. M. Demchinsky |
| author_sort | A. V. Sidorova |
| collection | DOAJ |
| description | Purpose. To submit clinical features and the effectiveness of surgical treatment of patients with glaucoma associated with the Frank-Kamenetsky’s syndrome.Material and method. We examined two patients with the Frank-Kamenetsky’s syndrome. Microinvasive non-penetrating deep sclerectomy was performed in both eyes of these patients.Results. The examination of patients detected the following features: x-linked recessive type of inheritance, decreased keratometry parameters with an axial length increase of the eye,specific changes in the anterior segment of the eye: posterior embryotoxon, bluish sclera, unusual iris structure, specific goniodisgenesis and glaucoma starting in adolescence. The combination of these features allowed us to diagnose the Frank-Kamenetsky’s syndrome. The operation and postoperative period were uncompli cated. The intraocular pressure was compensated during the entire follow-up periods.Conclusion. The described clinical cases demonstrate the clinical features of the Frank-Kamenetsky’s syndrome with a specific genetic link. A tolerance to the medical treatment with a fast progression is typical for this type of glaucoma. Surgical treatment allows to compensate the stable hydrodynamic indices ofintraocular pressure, to preserve and improve visual function in these patients. |
| first_indexed | 2024-04-10T21:15:51Z |
| format | Article |
| id | doaj.art-e84f7bf4723b49b1a85e1dfdbc46aaca |
| institution | Directory Open Access Journal |
| issn | 0235-4160 2312-4970 |
| language | Russian |
| last_indexed | 2024-04-10T21:15:51Z |
| publishDate | 2015-12-01 |
| publisher | Publishing house "Ophthalmology" |
| record_format | Article |
| series | Офтальмохирургия |
| spelling | doaj.art-e84f7bf4723b49b1a85e1dfdbc46aaca2023-01-20T12:34:50ZrusPublishing house "Ophthalmology"Офтальмохирургия0235-41602312-49702015-12-01031922180Surgical treatment of glaucoma associated with the Frank-Kamenetsky’s syndrome (а case report)A. V. Sidorova0A. V. Opletina1K. G. Khliyan2A. M. Demchinsky3The S. F yodorov Eye Micr osurgery F ederal State In stitution, MoscowThe S. F yodorov Eye Micr osurgery F ederal State In stitution, MoscowThe S. F yodorov Eye Micr osurgery F ederal State In stitution, MoscowThe S. F yodorov Eye Micr osurgery F ederal State In stitution, MoscowPurpose. To submit clinical features and the effectiveness of surgical treatment of patients with glaucoma associated with the Frank-Kamenetsky’s syndrome.Material and method. We examined two patients with the Frank-Kamenetsky’s syndrome. Microinvasive non-penetrating deep sclerectomy was performed in both eyes of these patients.Results. The examination of patients detected the following features: x-linked recessive type of inheritance, decreased keratometry parameters with an axial length increase of the eye,specific changes in the anterior segment of the eye: posterior embryotoxon, bluish sclera, unusual iris structure, specific goniodisgenesis and glaucoma starting in adolescence. The combination of these features allowed us to diagnose the Frank-Kamenetsky’s syndrome. The operation and postoperative period were uncompli cated. The intraocular pressure was compensated during the entire follow-up periods.Conclusion. The described clinical cases demonstrate the clinical features of the Frank-Kamenetsky’s syndrome with a specific genetic link. A tolerance to the medical treatment with a fast progression is typical for this type of glaucoma. Surgical treatment allows to compensate the stable hydrodynamic indices ofintraocular pressure, to preserve and improve visual function in these patients.https://www.ophthalmosurgery.ru/jour/article/view/182mesenchymaldystrophysyndromefrank-kamenetskyglaucomasurgerynon-penetrating deep sclerectomy |
| spellingShingle | A. V. Sidorova A. V. Opletina K. G. Khliyan A. M. Demchinsky Surgical treatment of glaucoma associated with the Frank-Kamenetsky’s syndrome (а case report) Офтальмохирургия mesenchymal dystrophy syndrome frank-kamenetsky glaucoma surgery non-penetrating deep sclerectomy |
| title | Surgical treatment of glaucoma associated with the Frank-Kamenetsky’s syndrome (а case report) |
| title_full | Surgical treatment of glaucoma associated with the Frank-Kamenetsky’s syndrome (а case report) |
| title_fullStr | Surgical treatment of glaucoma associated with the Frank-Kamenetsky’s syndrome (а case report) |
| title_full_unstemmed | Surgical treatment of glaucoma associated with the Frank-Kamenetsky’s syndrome (а case report) |
| title_short | Surgical treatment of glaucoma associated with the Frank-Kamenetsky’s syndrome (а case report) |
| title_sort | surgical treatment of glaucoma associated with the frank kamenetsky s syndrome а case report |
| topic | mesenchymal dystrophy syndrome frank-kamenetsky glaucoma surgery non-penetrating deep sclerectomy |
| url | https://www.ophthalmosurgery.ru/jour/article/view/182 |
| work_keys_str_mv | AT avsidorova surgicaltreatmentofglaucomaassociatedwiththefrankkamenetskyssyndromeacasereport AT avopletina surgicaltreatmentofglaucomaassociatedwiththefrankkamenetskyssyndromeacasereport AT kgkhliyan surgicaltreatmentofglaucomaassociatedwiththefrankkamenetskyssyndromeacasereport AT amdemchinsky surgicaltreatmentofglaucomaassociatedwiththefrankkamenetskyssyndromeacasereport |