Leiomyosarcoma with rhabdoid differentiation arising from leiomyoma: A rare entity

Leiomyosarcoma (LMS) arising in a leiomyoma (LM) is a rare event. Still rare is rhabdomyoblastic differentiation in leiomyosacoma. We present such a case of LMS uterus with rhabdomyoblastic differentiation arising in an LM in a 60-year-old menopausal woman who presented with lower abdominal pain. An...

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Main Authors: Pooja Chauhan, Kavita Mardi, Ganga Rawat, Nidhi Raina
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2017-01-01
Series:Archives of Medicine and Health Sciences
Subjects:
Online Access:http://www.amhsjournal.org/article.asp?issn=2321-4848;year=2017;volume=5;issue=2;spage=252;epage=254;aulast=Chauhan
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author Pooja Chauhan
Kavita Mardi
Ganga Rawat
Nidhi Raina
author_facet Pooja Chauhan
Kavita Mardi
Ganga Rawat
Nidhi Raina
author_sort Pooja Chauhan
collection DOAJ
description Leiomyosarcoma (LMS) arising in a leiomyoma (LM) is a rare event. Still rare is rhabdomyoblastic differentiation in leiomyosacoma. We present such a case of LMS uterus with rhabdomyoblastic differentiation arising in an LM in a 60-year-old menopausal woman who presented with lower abdominal pain. An ultrasound scan was suggestive of uterine fibroid. Total abdominal hysterectomy was performed for presumed LM. Grossly, fibroid had variegated appearance along with focal areas having whorling pattern and histopathology showed leiomyosarcomatous change in a benign LM with rhabdomyoblastic differentiation. This is a rare complication of LM and precise diagnosis of LMS is essential since it has an aggressive behavior.
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spelling doaj.art-e94dd0f345c94145ac29a8feb810f64c2022-12-22T02:51:24ZengWolters Kluwer Medknow PublicationsArchives of Medicine and Health Sciences2321-48482017-01-015225225410.4103/amhs.amhs_81_17Leiomyosarcoma with rhabdoid differentiation arising from leiomyoma: A rare entityPooja ChauhanKavita MardiGanga RawatNidhi RainaLeiomyosarcoma (LMS) arising in a leiomyoma (LM) is a rare event. Still rare is rhabdomyoblastic differentiation in leiomyosacoma. We present such a case of LMS uterus with rhabdomyoblastic differentiation arising in an LM in a 60-year-old menopausal woman who presented with lower abdominal pain. An ultrasound scan was suggestive of uterine fibroid. Total abdominal hysterectomy was performed for presumed LM. Grossly, fibroid had variegated appearance along with focal areas having whorling pattern and histopathology showed leiomyosarcomatous change in a benign LM with rhabdomyoblastic differentiation. This is a rare complication of LM and precise diagnosis of LMS is essential since it has an aggressive behavior.http://www.amhsjournal.org/article.asp?issn=2321-4848;year=2017;volume=5;issue=2;spage=252;epage=254;aulast=ChauhanLeiomyomaleiomyosarcomarhabdomyoblastic differentiationuterus
spellingShingle Pooja Chauhan
Kavita Mardi
Ganga Rawat
Nidhi Raina
Leiomyosarcoma with rhabdoid differentiation arising from leiomyoma: A rare entity
Archives of Medicine and Health Sciences
Leiomyoma
leiomyosarcoma
rhabdomyoblastic differentiation
uterus
title Leiomyosarcoma with rhabdoid differentiation arising from leiomyoma: A rare entity
title_full Leiomyosarcoma with rhabdoid differentiation arising from leiomyoma: A rare entity
title_fullStr Leiomyosarcoma with rhabdoid differentiation arising from leiomyoma: A rare entity
title_full_unstemmed Leiomyosarcoma with rhabdoid differentiation arising from leiomyoma: A rare entity
title_short Leiomyosarcoma with rhabdoid differentiation arising from leiomyoma: A rare entity
title_sort leiomyosarcoma with rhabdoid differentiation arising from leiomyoma a rare entity
topic Leiomyoma
leiomyosarcoma
rhabdomyoblastic differentiation
uterus
url http://www.amhsjournal.org/article.asp?issn=2321-4848;year=2017;volume=5;issue=2;spage=252;epage=254;aulast=Chauhan
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AT kavitamardi leiomyosarcomawithrhabdoiddifferentiationarisingfromleiomyomaarareentity
AT gangarawat leiomyosarcomawithrhabdoiddifferentiationarisingfromleiomyomaarareentity
AT nidhiraina leiomyosarcomawithrhabdoiddifferentiationarisingfromleiomyomaarareentity