Olmsted Syndrome
Olmsted syndrome is a rare congential palmoplantar keratoderma with progressive periorificial hyperkeratotic lesions, alopecia areata, deafness, lental and nail changes. Only a few cases of this syndrome have been reported so far. Our case is a seven year old boy with massive palmoplantar keratoderm...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Wolters Kluwer Medknow Publications
2002-01-01
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| Series: | Indian Journal of Dermatology |
| Online Access: | http://www.e-ijd.org/article.asp?issn=0019-5154;year=2002;volume=47;issue=4;spage=242;epage=244;aulast=Mukhopadhyay;type=0 |
| _version_ | 1819010730178904064 |
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| author | Mukhopadhyay Piyali Biswas Nibir Dutta R.N Pal S |
| author_facet | Mukhopadhyay Piyali Biswas Nibir Dutta R.N Pal S |
| author_sort | Mukhopadhyay Piyali |
| collection | DOAJ |
| description | Olmsted syndrome is a rare congential palmoplantar keratoderma with progressive periorificial hyperkeratotic lesions, alopecia areata, deafness, lental and nail changes. Only a few cases of this syndrome have been reported so far. Our case is a seven year old boy with massive palmoplantar keratoderma, perianal and periorifical hyperkeratotic plaques and autoamputation of digits. Alopecia areata, hyperkeratosis of elbows and knees and nail changes were also present. His physical and mental developments were normal. Routine laboratory tests were normal. The case is being reported for its rarity. |
| first_indexed | 2024-12-21T01:16:54Z |
| format | Article |
| id | doaj.art-ea1c67aec05841deaa43b9ded3870564 |
| institution | Directory Open Access Journal |
| issn | 0019-5154 1998-3611 |
| language | English |
| last_indexed | 2024-12-21T01:16:54Z |
| publishDate | 2002-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Indian Journal of Dermatology |
| spelling | doaj.art-ea1c67aec05841deaa43b9ded38705642022-12-21T19:20:46ZengWolters Kluwer Medknow PublicationsIndian Journal of Dermatology0019-51541998-36112002-01-01474242244Olmsted SyndromeMukhopadhyay PiyaliBiswas NibirDutta R.NPal SOlmsted syndrome is a rare congential palmoplantar keratoderma with progressive periorificial hyperkeratotic lesions, alopecia areata, deafness, lental and nail changes. Only a few cases of this syndrome have been reported so far. Our case is a seven year old boy with massive palmoplantar keratoderma, perianal and periorifical hyperkeratotic plaques and autoamputation of digits. Alopecia areata, hyperkeratosis of elbows and knees and nail changes were also present. His physical and mental developments were normal. Routine laboratory tests were normal. The case is being reported for its rarity.http://www.e-ijd.org/article.asp?issn=0019-5154;year=2002;volume=47;issue=4;spage=242;epage=244;aulast=Mukhopadhyay;type=0 |
| spellingShingle | Mukhopadhyay Piyali Biswas Nibir Dutta R.N Pal S Olmsted Syndrome Indian Journal of Dermatology |
| title | Olmsted Syndrome |
| title_full | Olmsted Syndrome |
| title_fullStr | Olmsted Syndrome |
| title_full_unstemmed | Olmsted Syndrome |
| title_short | Olmsted Syndrome |
| title_sort | olmsted syndrome |
| url | http://www.e-ijd.org/article.asp?issn=0019-5154;year=2002;volume=47;issue=4;spage=242;epage=244;aulast=Mukhopadhyay;type=0 |
| work_keys_str_mv | AT mukhopadhyaypiyali olmstedsyndrome AT biswasnibir olmstedsyndrome AT duttarn olmstedsyndrome AT pals olmstedsyndrome |