Balloon pulmonary angioplasty – efficient therapy of chronic thromboembolic pulmonary hypertension in the patient with advanced sarcoidosis – a case report
Abstract Background Approximately a quarter of patients with advanced sarcoidosis develop pulmonary hypertension (PH), which affects their prognosis. We report unusual case of confirmed chronic thromboembolic pulmonary hypertension (CTEPH) in a patient with stage IV sarcoidosis successfully treated...
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| Format: | Article |
| Language: | English |
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BMC
2018-08-01
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| Series: | BMC Pulmonary Medicine |
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| Online Access: | http://link.springer.com/article/10.1186/s12890-018-0695-4 |
| _version_ | 1818892197444976640 |
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| author | Andrzej Labyk Dominik Wretowski Sabina Zybińska-Oksiutowicz Aleksandra Furdyna Katarzyna Ciesielska Dorota Piotrowska-Kownacka Olga Dzikowska –Diduch Barbara Lichodziejewska Andrzej Biederman Piotr Pruszczyk Marek Roik |
| author_facet | Andrzej Labyk Dominik Wretowski Sabina Zybińska-Oksiutowicz Aleksandra Furdyna Katarzyna Ciesielska Dorota Piotrowska-Kownacka Olga Dzikowska –Diduch Barbara Lichodziejewska Andrzej Biederman Piotr Pruszczyk Marek Roik |
| author_sort | Andrzej Labyk |
| collection | DOAJ |
| description | Abstract Background Approximately a quarter of patients with advanced sarcoidosis develop pulmonary hypertension (PH), which affects their prognosis. We report unusual case of confirmed chronic thromboembolic pulmonary hypertension (CTEPH) in a patient with stage IV sarcoidosis successfully treated with balloon pulmonary angioplasty (BPA). Case presentation A 65 years old male with a history of colitis ulcerosa, and pulmonary sarcoidosis diagnosed in 10 years before, on long term oral steroids, with a history of deep vein thrombosis and acute pulmonary embolism chronically anticoagulated was referred to our center due to severe dyspnea. On admission he presented WHO functional class IV, mean pulmonary artery pressure (mPAP) in right heart catheterization (RHC) was elevated to 54 mmHg. Diagnosis of CTEPH was definitely confirmed with typical V/Q scan, and with selective pulmonary angiography (PAG) completes by intravascular imagining (intravascular ultrasound, optical coherent tomography). The patient was deemed inoperable by CTEPH team and two sessions of BPA with multimodal approach resulted in significant clinical and haemodynamical improvement to WHO class II and mPAP decrease to 27 mmHg. Conclusions Balloon pulmonary angioplasty, rapidly developing method of treatment of inoperable CTEPH patients, is also extremely useful therapeutic tool in complex PH patients. |
| first_indexed | 2024-12-19T17:52:52Z |
| format | Article |
| id | doaj.art-eb92ce1da41a43ab82ca3d892c06357c |
| institution | Directory Open Access Journal |
| issn | 1471-2466 |
| language | English |
| last_indexed | 2024-12-19T17:52:52Z |
| publishDate | 2018-08-01 |
| publisher | BMC |
| record_format | Article |
| series | BMC Pulmonary Medicine |
| spelling | doaj.art-eb92ce1da41a43ab82ca3d892c06357c2022-12-21T20:11:53ZengBMCBMC Pulmonary Medicine1471-24662018-08-011811510.1186/s12890-018-0695-4Balloon pulmonary angioplasty – efficient therapy of chronic thromboembolic pulmonary hypertension in the patient with advanced sarcoidosis – a case reportAndrzej Labyk0Dominik Wretowski1Sabina Zybińska-Oksiutowicz2Aleksandra Furdyna3Katarzyna Ciesielska4Dorota Piotrowska-Kownacka5Olga Dzikowska –Diduch6Barbara Lichodziejewska7Andrzej Biederman8Piotr Pruszczyk9Marek Roik10Center for Diagnostics and Treatment of Venous Thromboembolism, Department of Internal Medicine and Cardiology, Warsaw Medical University, Infant Jesus HospitalCenter for Diagnostics and Treatment of Venous Thromboembolism, Department of Internal Medicine and Cardiology, Warsaw Medical University, Infant Jesus HospitalCenter for Diagnostics and Treatment of Venous Thromboembolism, Department of Internal Medicine and Cardiology, Warsaw Medical University, Infant Jesus HospitalCenter for Diagnostics and Treatment of Venous Thromboembolism, Department of Internal Medicine and Cardiology, Warsaw Medical University, Infant Jesus HospitalCenter for Diagnostics and Treatment of Venous Thromboembolism, Department of Internal Medicine and Cardiology, Warsaw Medical University, Infant Jesus HospitalDepartment of Radiology, Infant Jesus HospitalCenter for Diagnostics and Treatment of Venous Thromboembolism, Department of Internal Medicine and Cardiology, Warsaw Medical University, Infant Jesus HospitalCenter for Diagnostics and Treatment of Venous Thromboembolism, Department of Internal Medicine and Cardiology, Warsaw Medical University, Infant Jesus HospitalCardiac Surgery Department Medicover HospitalCenter for Diagnostics and Treatment of Venous Thromboembolism, Department of Internal Medicine and Cardiology, Warsaw Medical University, Infant Jesus HospitalCenter for Diagnostics and Treatment of Venous Thromboembolism, Department of Internal Medicine and Cardiology, Warsaw Medical University, Infant Jesus HospitalAbstract Background Approximately a quarter of patients with advanced sarcoidosis develop pulmonary hypertension (PH), which affects their prognosis. We report unusual case of confirmed chronic thromboembolic pulmonary hypertension (CTEPH) in a patient with stage IV sarcoidosis successfully treated with balloon pulmonary angioplasty (BPA). Case presentation A 65 years old male with a history of colitis ulcerosa, and pulmonary sarcoidosis diagnosed in 10 years before, on long term oral steroids, with a history of deep vein thrombosis and acute pulmonary embolism chronically anticoagulated was referred to our center due to severe dyspnea. On admission he presented WHO functional class IV, mean pulmonary artery pressure (mPAP) in right heart catheterization (RHC) was elevated to 54 mmHg. Diagnosis of CTEPH was definitely confirmed with typical V/Q scan, and with selective pulmonary angiography (PAG) completes by intravascular imagining (intravascular ultrasound, optical coherent tomography). The patient was deemed inoperable by CTEPH team and two sessions of BPA with multimodal approach resulted in significant clinical and haemodynamical improvement to WHO class II and mPAP decrease to 27 mmHg. Conclusions Balloon pulmonary angioplasty, rapidly developing method of treatment of inoperable CTEPH patients, is also extremely useful therapeutic tool in complex PH patients.http://link.springer.com/article/10.1186/s12890-018-0695-4SarcoidosisChronic thromboembolic pulmonary hypertensionBalloon pulmonary angioplasty |
| spellingShingle | Andrzej Labyk Dominik Wretowski Sabina Zybińska-Oksiutowicz Aleksandra Furdyna Katarzyna Ciesielska Dorota Piotrowska-Kownacka Olga Dzikowska –Diduch Barbara Lichodziejewska Andrzej Biederman Piotr Pruszczyk Marek Roik Balloon pulmonary angioplasty – efficient therapy of chronic thromboembolic pulmonary hypertension in the patient with advanced sarcoidosis – a case report BMC Pulmonary Medicine Sarcoidosis Chronic thromboembolic pulmonary hypertension Balloon pulmonary angioplasty |
| title | Balloon pulmonary angioplasty – efficient therapy of chronic thromboembolic pulmonary hypertension in the patient with advanced sarcoidosis – a case report |
| title_full | Balloon pulmonary angioplasty – efficient therapy of chronic thromboembolic pulmonary hypertension in the patient with advanced sarcoidosis – a case report |
| title_fullStr | Balloon pulmonary angioplasty – efficient therapy of chronic thromboembolic pulmonary hypertension in the patient with advanced sarcoidosis – a case report |
| title_full_unstemmed | Balloon pulmonary angioplasty – efficient therapy of chronic thromboembolic pulmonary hypertension in the patient with advanced sarcoidosis – a case report |
| title_short | Balloon pulmonary angioplasty – efficient therapy of chronic thromboembolic pulmonary hypertension in the patient with advanced sarcoidosis – a case report |
| title_sort | balloon pulmonary angioplasty efficient therapy of chronic thromboembolic pulmonary hypertension in the patient with advanced sarcoidosis a case report |
| topic | Sarcoidosis Chronic thromboembolic pulmonary hypertension Balloon pulmonary angioplasty |
| url | http://link.springer.com/article/10.1186/s12890-018-0695-4 |
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