The Need for Earlier Diagnosis of Obstructed Hemivagina and Ipsilateral Renal Agenesis/Anomaly (OHVIRA) Syndrome in Case of Renal Agenesis in Girls—Case Report and Review of the Literature
Obstructed hemivagina and ipsilateral renal agenesis/anomaly (OHVIRA) syndrome is a very rare condition affecting girls. The time of diagnosis varies, from cases of prenatal diagnosis up to adulthood, including pregnancy or delivery. Most commonly, it is recognised during puberty and usually as an a...
| Main Authors: | , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
MDPI AG
2023-11-01
|
| Series: | Journal of Clinical Medicine |
| Subjects: | |
| Online Access: | https://www.mdpi.com/2077-0383/12/23/7284 |
| _version_ | 1797400012876939264 |
|---|---|
| author | Agnieszka Lecka-Ambroziak Lidia Skobejko-Włodarska Hanna Ruta |
| author_facet | Agnieszka Lecka-Ambroziak Lidia Skobejko-Włodarska Hanna Ruta |
| author_sort | Agnieszka Lecka-Ambroziak |
| collection | DOAJ |
| description | Obstructed hemivagina and ipsilateral renal agenesis/anomaly (OHVIRA) syndrome is a very rare condition affecting girls. The time of diagnosis varies, from cases of prenatal diagnosis up to adulthood, including pregnancy or delivery. Most commonly, it is recognised during puberty and usually as an acute condition. We present a case report of an adolescent girl who underwent the treatment because of acute abdominal pain. The case is interesting due to a previous diagnosis of one-side renal agenesis. It appears to be useful to perform a diagnostic pelvic imaging at the time of diagnosis of renal agenesis or to plan to perform it at the beginning of puberty, to prevent the need for urgent surgery. This management may allow the planning of proper follow-up, minimising the risk of possible complications. |
| first_indexed | 2024-03-09T01:49:23Z |
| format | Article |
| id | doaj.art-ebe1e8593aa54c5fa15627b914866177 |
| institution | Directory Open Access Journal |
| issn | 2077-0383 |
| language | English |
| last_indexed | 2024-03-09T01:49:23Z |
| publishDate | 2023-11-01 |
| publisher | MDPI AG |
| record_format | Article |
| series | Journal of Clinical Medicine |
| spelling | doaj.art-ebe1e8593aa54c5fa15627b9148661772023-12-08T15:19:08ZengMDPI AGJournal of Clinical Medicine2077-03832023-11-011223728410.3390/jcm12237284The Need for Earlier Diagnosis of Obstructed Hemivagina and Ipsilateral Renal Agenesis/Anomaly (OHVIRA) Syndrome in Case of Renal Agenesis in Girls—Case Report and Review of the LiteratureAgnieszka Lecka-Ambroziak0Lidia Skobejko-Włodarska1Hanna Ruta2Department of Endocrinology and Diabetology, The Children’s Memorial Health Institute, 04-730 Warsaw, PolandDepartment of Urology, The Children’s Memorial Health Institute, 04-730 Warsaw, PolandGynaecology Outpatient Clinic, The Children’s Memorial Health Institute, 04-730 Warsaw, PolandObstructed hemivagina and ipsilateral renal agenesis/anomaly (OHVIRA) syndrome is a very rare condition affecting girls. The time of diagnosis varies, from cases of prenatal diagnosis up to adulthood, including pregnancy or delivery. Most commonly, it is recognised during puberty and usually as an acute condition. We present a case report of an adolescent girl who underwent the treatment because of acute abdominal pain. The case is interesting due to a previous diagnosis of one-side renal agenesis. It appears to be useful to perform a diagnostic pelvic imaging at the time of diagnosis of renal agenesis or to plan to perform it at the beginning of puberty, to prevent the need for urgent surgery. This management may allow the planning of proper follow-up, minimising the risk of possible complications.https://www.mdpi.com/2077-0383/12/23/7284OHVIRA syndromerenal agenesisMüllerian ducts anomaliesendometriosis |
| spellingShingle | Agnieszka Lecka-Ambroziak Lidia Skobejko-Włodarska Hanna Ruta The Need for Earlier Diagnosis of Obstructed Hemivagina and Ipsilateral Renal Agenesis/Anomaly (OHVIRA) Syndrome in Case of Renal Agenesis in Girls—Case Report and Review of the Literature Journal of Clinical Medicine OHVIRA syndrome renal agenesis Müllerian ducts anomalies endometriosis |
| title | The Need for Earlier Diagnosis of Obstructed Hemivagina and Ipsilateral Renal Agenesis/Anomaly (OHVIRA) Syndrome in Case of Renal Agenesis in Girls—Case Report and Review of the Literature |
| title_full | The Need for Earlier Diagnosis of Obstructed Hemivagina and Ipsilateral Renal Agenesis/Anomaly (OHVIRA) Syndrome in Case of Renal Agenesis in Girls—Case Report and Review of the Literature |
| title_fullStr | The Need for Earlier Diagnosis of Obstructed Hemivagina and Ipsilateral Renal Agenesis/Anomaly (OHVIRA) Syndrome in Case of Renal Agenesis in Girls—Case Report and Review of the Literature |
| title_full_unstemmed | The Need for Earlier Diagnosis of Obstructed Hemivagina and Ipsilateral Renal Agenesis/Anomaly (OHVIRA) Syndrome in Case of Renal Agenesis in Girls—Case Report and Review of the Literature |
| title_short | The Need for Earlier Diagnosis of Obstructed Hemivagina and Ipsilateral Renal Agenesis/Anomaly (OHVIRA) Syndrome in Case of Renal Agenesis in Girls—Case Report and Review of the Literature |
| title_sort | need for earlier diagnosis of obstructed hemivagina and ipsilateral renal agenesis anomaly ohvira syndrome in case of renal agenesis in girls case report and review of the literature |
| topic | OHVIRA syndrome renal agenesis Müllerian ducts anomalies endometriosis |
| url | https://www.mdpi.com/2077-0383/12/23/7284 |
| work_keys_str_mv | AT agnieszkaleckaambroziak theneedforearlierdiagnosisofobstructedhemivaginaandipsilateralrenalagenesisanomalyohvirasyndromeincaseofrenalagenesisingirlscasereportandreviewoftheliterature AT lidiaskobejkowłodarska theneedforearlierdiagnosisofobstructedhemivaginaandipsilateralrenalagenesisanomalyohvirasyndromeincaseofrenalagenesisingirlscasereportandreviewoftheliterature AT hannaruta theneedforearlierdiagnosisofobstructedhemivaginaandipsilateralrenalagenesisanomalyohvirasyndromeincaseofrenalagenesisingirlscasereportandreviewoftheliterature AT agnieszkaleckaambroziak needforearlierdiagnosisofobstructedhemivaginaandipsilateralrenalagenesisanomalyohvirasyndromeincaseofrenalagenesisingirlscasereportandreviewoftheliterature AT lidiaskobejkowłodarska needforearlierdiagnosisofobstructedhemivaginaandipsilateralrenalagenesisanomalyohvirasyndromeincaseofrenalagenesisingirlscasereportandreviewoftheliterature AT hannaruta needforearlierdiagnosisofobstructedhemivaginaandipsilateralrenalagenesisanomalyohvirasyndromeincaseofrenalagenesisingirlscasereportandreviewoftheliterature |