Portopulmonary hypertension in a child
The paper deals with portopulmonary hypertension (pulmonary arterial hypertension associated with portal hypertension). Pulmonary hypertension is a rare, prognostically unfavorable complication of portal hypertension, regardless of the etiological factor of the latter. The diagnostic criteria for po...
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | Russian |
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Ltd. “The National Academy of Pediatric Science and Innovation”
2016-11-01
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| Series: | Rossijskij Vestnik Perinatologii i Pediatrii |
| Subjects: | |
| Online Access: | https://www.ped-perinatology.ru/jour/article/view/398 |
| Summary: | The paper deals with portopulmonary hypertension (pulmonary arterial hypertension associated with portal hypertension). Pulmonary hypertension is a rare, prognostically unfavorable complication of portal hypertension, regardless of the etiological factor of the latter. The diagnostic criteria for portopulmonary hypertension are portal hypertension with or without liver disease; a resting mean pulmonary artery pressure >25 mm Hg; a normal pulmonary artery wedge pressure <15 mm Hg; and a pulmonary vascular resistance of more than 3 Wood units/m2. Objective: to describe of the development of the clinical picture, diagnosis, and treatment of portopulmonary hypertension in a patient during corrected portal hypertension. There are challenges in the diagnosis of portopulmonary hypertension because its symptoms are nonspecific. The most characteristic symptoms of the disease are dyspnea, fatigue, exercise intolerance, and syncope. |
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| ISSN: | 1027-4065 2500-2228 |