Pigment dispersion syndrome associated with spontaneous subluxation of crystalline lens
Pigment dispersion syndrome (PDS) is an ocular condition characterized by a dispersion of iris pigment throughout the eye. This pigment is deposited in a characteristic manner on the corneal endothelium as Krukenberg's spindle, anterior surface of the iris, in the trabecular meshwork, on the le...
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2017-01-01
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| Series: | Oman Journal of Ophthalmology |
| Subjects: | |
| Online Access: | http://www.ojoonline.org/article.asp?issn=0974-620X;year=2017;volume=10;issue=1;spage=52;epage=53;aulast=Veerwal |
| _version_ | 1819078498790146048 |
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| author | Vikas Veerwal Jawahar Lal Goyal Parul Jain Ritu Arora |
| author_facet | Vikas Veerwal Jawahar Lal Goyal Parul Jain Ritu Arora |
| author_sort | Vikas Veerwal |
| collection | DOAJ |
| description | Pigment dispersion syndrome (PDS) is an ocular condition characterized by a dispersion of iris pigment throughout the eye. This pigment is deposited in a characteristic manner on the corneal endothelium as Krukenberg's spindle, anterior surface of the iris, in the trabecular meshwork, on the lens and zonule and occasionally on the anterior hyaloid face. Even with deposition of pigment on zonular fibers, no zonular weakness, or zonular dehiscence has been reported in these cases. We report a unique case of PDS with bilateral spontaneous subluxation of crystalline lens. With characteristic findings of pigment distribution in both his eyes, the patient had concave iris configuration with heavily pigmented trabecular meshwork confirming the diagnosis of PDS. The patient had bilateral 180° temporal subluxation of crystalline lens in both his eyes. The usual cause of lens subluxation such as Marfan's Syndrome and Ehler's Danlos Syndrome was ruled out. The patient underwent right eye followed by left eye intracapsular cataract extraction with ab-interno technique with postoperative best-corrected visual acuity (BCVA) of 6/9 in both eyes. Spontaneous subluxation of crystalline lens in isolated PDS is not known to occur and has been reported by means of this case. We recommend a thorough assessment of zonular status in all cases of PDS. |
| first_indexed | 2024-12-21T19:14:03Z |
| format | Article |
| id | doaj.art-ecac19f3a15045ec992a1fc113788da6 |
| institution | Directory Open Access Journal |
| issn | 0974-620X |
| language | English |
| last_indexed | 2024-12-21T19:14:03Z |
| publishDate | 2017-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Oman Journal of Ophthalmology |
| spelling | doaj.art-ecac19f3a15045ec992a1fc113788da62022-12-21T18:53:07ZengWolters Kluwer Medknow PublicationsOman Journal of Ophthalmology0974-620X2017-01-01101525310.4103/0974-620X.200683Pigment dispersion syndrome associated with spontaneous subluxation of crystalline lensVikas VeerwalJawahar Lal GoyalParul JainRitu AroraPigment dispersion syndrome (PDS) is an ocular condition characterized by a dispersion of iris pigment throughout the eye. This pigment is deposited in a characteristic manner on the corneal endothelium as Krukenberg's spindle, anterior surface of the iris, in the trabecular meshwork, on the lens and zonule and occasionally on the anterior hyaloid face. Even with deposition of pigment on zonular fibers, no zonular weakness, or zonular dehiscence has been reported in these cases. We report a unique case of PDS with bilateral spontaneous subluxation of crystalline lens. With characteristic findings of pigment distribution in both his eyes, the patient had concave iris configuration with heavily pigmented trabecular meshwork confirming the diagnosis of PDS. The patient had bilateral 180° temporal subluxation of crystalline lens in both his eyes. The usual cause of lens subluxation such as Marfan's Syndrome and Ehler's Danlos Syndrome was ruled out. The patient underwent right eye followed by left eye intracapsular cataract extraction with ab-interno technique with postoperative best-corrected visual acuity (BCVA) of 6/9 in both eyes. Spontaneous subluxation of crystalline lens in isolated PDS is not known to occur and has been reported by means of this case. We recommend a thorough assessment of zonular status in all cases of PDS.http://www.ojoonline.org/article.asp?issn=0974-620X;year=2017;volume=10;issue=1;spage=52;epage=53;aulast=VeerwalConcave iris configurationKrukenberg's spindlelens subluxationpigment dispersion syndromeZentmayer's line |
| spellingShingle | Vikas Veerwal Jawahar Lal Goyal Parul Jain Ritu Arora Pigment dispersion syndrome associated with spontaneous subluxation of crystalline lens Oman Journal of Ophthalmology Concave iris configuration Krukenberg's spindle lens subluxation pigment dispersion syndrome Zentmayer's line |
| title | Pigment dispersion syndrome associated with spontaneous subluxation of crystalline lens |
| title_full | Pigment dispersion syndrome associated with spontaneous subluxation of crystalline lens |
| title_fullStr | Pigment dispersion syndrome associated with spontaneous subluxation of crystalline lens |
| title_full_unstemmed | Pigment dispersion syndrome associated with spontaneous subluxation of crystalline lens |
| title_short | Pigment dispersion syndrome associated with spontaneous subluxation of crystalline lens |
| title_sort | pigment dispersion syndrome associated with spontaneous subluxation of crystalline lens |
| topic | Concave iris configuration Krukenberg's spindle lens subluxation pigment dispersion syndrome Zentmayer's line |
| url | http://www.ojoonline.org/article.asp?issn=0974-620X;year=2017;volume=10;issue=1;spage=52;epage=53;aulast=Veerwal |
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