Pulmonary Agenesis - A Zebra Like Disorder for Pulmonologists
Pulmonary agenesis is an extremely rare congenital anomaly defined as a complete absence of the lung parenchyma, bronchus, and pulmonary vessels. In case of complete unilateral agenesis, no pleural cavity can be found on the affected side. More than 50% of children with lung aplasia die within five...
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Format: | Article |
Language: | English |
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Wolters Kluwer Medknow Publications
2018-01-01
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Series: | Journal of Association of Pulmonologist of Tamil Nadu |
Subjects: | |
Online Access: | http://www.japt.in/article.asp?issn=2772-6355;year=2018;volume=1;issue=2;spage=83;epage=86;aulast=Anandhan;type=0 |
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author | Monisha Anandhan Amal Johnson R Narasimhan |
author_facet | Monisha Anandhan Amal Johnson R Narasimhan |
author_sort | Monisha Anandhan |
collection | DOAJ |
description | Pulmonary agenesis is an extremely rare congenital anomaly defined as a complete absence of the lung parenchyma, bronchus, and pulmonary vessels. In case of complete unilateral agenesis, no pleural cavity can be found on the affected side. More than 50% of children with lung aplasia die within five years of birth but some individuals live a normal life span with their deformity and may be asymptomatic throughout life. Respiratory tract infections are the greatest danger in these individuals. We report a case of left lung aplasia with bronchiectasis in a young-aged adult who was treated for tuberculosis and was referred to our institute for persistent cough. |
first_indexed | 2024-03-12T13:46:35Z |
format | Article |
id | doaj.art-ece67ae037284ff393cb39c9febb7367 |
institution | Directory Open Access Journal |
issn | 2772-6355 2772-6363 |
language | English |
last_indexed | 2024-03-12T13:46:35Z |
publishDate | 2018-01-01 |
publisher | Wolters Kluwer Medknow Publications |
record_format | Article |
series | Journal of Association of Pulmonologist of Tamil Nadu |
spelling | doaj.art-ece67ae037284ff393cb39c9febb73672023-08-23T08:59:12ZengWolters Kluwer Medknow PublicationsJournal of Association of Pulmonologist of Tamil Nadu2772-63552772-63632018-01-01128386Pulmonary Agenesis - A Zebra Like Disorder for PulmonologistsMonisha AnandhanAmal JohnsonR NarasimhanPulmonary agenesis is an extremely rare congenital anomaly defined as a complete absence of the lung parenchyma, bronchus, and pulmonary vessels. In case of complete unilateral agenesis, no pleural cavity can be found on the affected side. More than 50% of children with lung aplasia die within five years of birth but some individuals live a normal life span with their deformity and may be asymptomatic throughout life. Respiratory tract infections are the greatest danger in these individuals. We report a case of left lung aplasia with bronchiectasis in a young-aged adult who was treated for tuberculosis and was referred to our institute for persistent cough.http://www.japt.in/article.asp?issn=2772-6355;year=2018;volume=1;issue=2;spage=83;epage=86;aulast=Anandhan;type=0lung agenesisaplasiahypoplasia |
spellingShingle | Monisha Anandhan Amal Johnson R Narasimhan Pulmonary Agenesis - A Zebra Like Disorder for Pulmonologists Journal of Association of Pulmonologist of Tamil Nadu lung agenesis aplasia hypoplasia |
title | Pulmonary Agenesis - A Zebra Like Disorder for Pulmonologists |
title_full | Pulmonary Agenesis - A Zebra Like Disorder for Pulmonologists |
title_fullStr | Pulmonary Agenesis - A Zebra Like Disorder for Pulmonologists |
title_full_unstemmed | Pulmonary Agenesis - A Zebra Like Disorder for Pulmonologists |
title_short | Pulmonary Agenesis - A Zebra Like Disorder for Pulmonologists |
title_sort | pulmonary agenesis a zebra like disorder for pulmonologists |
topic | lung agenesis aplasia hypoplasia |
url | http://www.japt.in/article.asp?issn=2772-6355;year=2018;volume=1;issue=2;spage=83;epage=86;aulast=Anandhan;type=0 |
work_keys_str_mv | AT monishaanandhan pulmonaryagenesisazebralikedisorderforpulmonologists AT amaljohnson pulmonaryagenesisazebralikedisorderforpulmonologists AT rnarasimhan pulmonaryagenesisazebralikedisorderforpulmonologists |