Pulmonary Agenesis - A Zebra Like Disorder for Pulmonologists

Pulmonary agenesis is an extremely rare congenital anomaly defined as a complete absence of the lung parenchyma, bronchus, and pulmonary vessels. In case of complete unilateral agenesis, no pleural cavity can be found on the affected side. More than 50% of children with lung aplasia die within five...

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Main Authors: Monisha Anandhan, Amal Johnson, R Narasimhan
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2018-01-01
Series:Journal of Association of Pulmonologist of Tamil Nadu
Subjects:
Online Access:http://www.japt.in/article.asp?issn=2772-6355;year=2018;volume=1;issue=2;spage=83;epage=86;aulast=Anandhan;type=0
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author Monisha Anandhan
Amal Johnson
R Narasimhan
author_facet Monisha Anandhan
Amal Johnson
R Narasimhan
author_sort Monisha Anandhan
collection DOAJ
description Pulmonary agenesis is an extremely rare congenital anomaly defined as a complete absence of the lung parenchyma, bronchus, and pulmonary vessels. In case of complete unilateral agenesis, no pleural cavity can be found on the affected side. More than 50% of children with lung aplasia die within five years of birth but some individuals live a normal life span with their deformity and may be asymptomatic throughout life. Respiratory tract infections are the greatest danger in these individuals. We report a case of left lung aplasia with bronchiectasis in a young-aged adult who was treated for tuberculosis and was referred to our institute for persistent cough.
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spelling doaj.art-ece67ae037284ff393cb39c9febb73672023-08-23T08:59:12ZengWolters Kluwer Medknow PublicationsJournal of Association of Pulmonologist of Tamil Nadu2772-63552772-63632018-01-01128386Pulmonary Agenesis - A Zebra Like Disorder for PulmonologistsMonisha AnandhanAmal JohnsonR NarasimhanPulmonary agenesis is an extremely rare congenital anomaly defined as a complete absence of the lung parenchyma, bronchus, and pulmonary vessels. In case of complete unilateral agenesis, no pleural cavity can be found on the affected side. More than 50% of children with lung aplasia die within five years of birth but some individuals live a normal life span with their deformity and may be asymptomatic throughout life. Respiratory tract infections are the greatest danger in these individuals. We report a case of left lung aplasia with bronchiectasis in a young-aged adult who was treated for tuberculosis and was referred to our institute for persistent cough.http://www.japt.in/article.asp?issn=2772-6355;year=2018;volume=1;issue=2;spage=83;epage=86;aulast=Anandhan;type=0lung agenesisaplasiahypoplasia
spellingShingle Monisha Anandhan
Amal Johnson
R Narasimhan
Pulmonary Agenesis - A Zebra Like Disorder for Pulmonologists
Journal of Association of Pulmonologist of Tamil Nadu
lung agenesis
aplasia
hypoplasia
title Pulmonary Agenesis - A Zebra Like Disorder for Pulmonologists
title_full Pulmonary Agenesis - A Zebra Like Disorder for Pulmonologists
title_fullStr Pulmonary Agenesis - A Zebra Like Disorder for Pulmonologists
title_full_unstemmed Pulmonary Agenesis - A Zebra Like Disorder for Pulmonologists
title_short Pulmonary Agenesis - A Zebra Like Disorder for Pulmonologists
title_sort pulmonary agenesis a zebra like disorder for pulmonologists
topic lung agenesis
aplasia
hypoplasia
url http://www.japt.in/article.asp?issn=2772-6355;year=2018;volume=1;issue=2;spage=83;epage=86;aulast=Anandhan;type=0
work_keys_str_mv AT monishaanandhan pulmonaryagenesisazebralikedisorderforpulmonologists
AT amaljohnson pulmonaryagenesisazebralikedisorderforpulmonologists
AT rnarasimhan pulmonaryagenesisazebralikedisorderforpulmonologists