Evans syndrome and its link with systemic lupus erythematosus
Evans syndrome is a rare syndrome associated with the presence of autoimmune hemolytic anemia and simultaneous or sequential development of thrombocytopenia. It was first described by Evan and Duane in 1951. It is one of the rare presenting features of autoimmune disorders, especially systemic lupus...
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2016-01-01
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| Series: | Saudi Journal of Kidney Diseases and Transplantation |
| Online Access: | http://www.sjkdt.org/article.asp?issn=1319-2442;year=2016;volume=27;issue=1;spage=147;epage=149;aulast=Mendonca |
| _version_ | 1818948668134260736 |
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| author | Satish Mendonca Sachin Srivastava Rajan Kapoor Devika Gupta Pooja Gupta M L Sharma |
| author_facet | Satish Mendonca Sachin Srivastava Rajan Kapoor Devika Gupta Pooja Gupta M L Sharma |
| author_sort | Satish Mendonca |
| collection | DOAJ |
| description | Evans syndrome is a rare syndrome associated with the presence of autoimmune hemolytic anemia and simultaneous or sequential development of thrombocytopenia. It was first described by Evan and Duane in 1951. It is one of the rare presenting features of autoimmune disorders, especially systemic lupus erythematosus (SLE), and sometimes may even precede the onset of disease. Primary Evans syndrome with no cause is very rare and is seen in children. Here, we describe a case of secondary Evans syndrome with severe hemolytic anemia leading to acute kidney injury and recovery thereafter only to develop lupus nephritis a few months later. This is one of the rare presentations of SLE and there are only anecdotal case reports. |
| first_indexed | 2024-12-20T08:50:27Z |
| format | Article |
| id | doaj.art-ecfb0ae57b6d4afcb256faf6b3fc2459 |
| institution | Directory Open Access Journal |
| issn | 1319-2442 |
| language | English |
| last_indexed | 2024-12-20T08:50:27Z |
| publishDate | 2016-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Saudi Journal of Kidney Diseases and Transplantation |
| spelling | doaj.art-ecfb0ae57b6d4afcb256faf6b3fc24592022-12-21T19:46:08ZengWolters Kluwer Medknow PublicationsSaudi Journal of Kidney Diseases and Transplantation1319-24422016-01-0127114714910.4103/1319-2442.174177Evans syndrome and its link with systemic lupus erythematosusSatish MendoncaSachin SrivastavaRajan KapoorDevika GuptaPooja GuptaM L SharmaEvans syndrome is a rare syndrome associated with the presence of autoimmune hemolytic anemia and simultaneous or sequential development of thrombocytopenia. It was first described by Evan and Duane in 1951. It is one of the rare presenting features of autoimmune disorders, especially systemic lupus erythematosus (SLE), and sometimes may even precede the onset of disease. Primary Evans syndrome with no cause is very rare and is seen in children. Here, we describe a case of secondary Evans syndrome with severe hemolytic anemia leading to acute kidney injury and recovery thereafter only to develop lupus nephritis a few months later. This is one of the rare presentations of SLE and there are only anecdotal case reports.http://www.sjkdt.org/article.asp?issn=1319-2442;year=2016;volume=27;issue=1;spage=147;epage=149;aulast=Mendonca |
| spellingShingle | Satish Mendonca Sachin Srivastava Rajan Kapoor Devika Gupta Pooja Gupta M L Sharma Evans syndrome and its link with systemic lupus erythematosus Saudi Journal of Kidney Diseases and Transplantation |
| title | Evans syndrome and its link with systemic lupus erythematosus |
| title_full | Evans syndrome and its link with systemic lupus erythematosus |
| title_fullStr | Evans syndrome and its link with systemic lupus erythematosus |
| title_full_unstemmed | Evans syndrome and its link with systemic lupus erythematosus |
| title_short | Evans syndrome and its link with systemic lupus erythematosus |
| title_sort | evans syndrome and its link with systemic lupus erythematosus |
| url | http://www.sjkdt.org/article.asp?issn=1319-2442;year=2016;volume=27;issue=1;spage=147;epage=149;aulast=Mendonca |
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