Anesthetic Management and Bispectral Index in a Child with Miller–Dieker Syndrome: A Case Report
Miller–Dieker syndrome (MDS) is a genetic disorder characterized by classic lissencephaly, distinctive facial features, intellectual disability, seizures, and early death. The anesthetic management of patients with MDS should focus on airway manipulation with the risk of potentially difficult intuba...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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MDPI AG
2023-03-01
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| Series: | Children |
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| Online Access: | https://www.mdpi.com/2227-9067/10/4/631 |
| _version_ | 1797605964889718784 |
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| author | Sang Jin Park Jongyoon Baek Suyoun Chun Eun Kyung Choi |
| author_facet | Sang Jin Park Jongyoon Baek Suyoun Chun Eun Kyung Choi |
| author_sort | Sang Jin Park |
| collection | DOAJ |
| description | Miller–Dieker syndrome (MDS) is a genetic disorder characterized by classic lissencephaly, distinctive facial features, intellectual disability, seizures, and early death. The anesthetic management of patients with MDS should focus on airway manipulation with the risk of potentially difficult intubation, seizure control due to lissencephaly, and any other clinical complications. Herein, we report a case of anesthetic management in a child with MDS and describe relevant clinical features in a perioperative anesthetic setting. This case highlights the importance of difficult airway manipulation using a videolaryngoscope, seizure management with regard to anesthetics use, and the low validity of BIS monitoring in patients with MDS. |
| first_indexed | 2024-03-11T05:08:36Z |
| format | Article |
| id | doaj.art-ee92615dc79d4ea49f74232f28ac9886 |
| institution | Directory Open Access Journal |
| issn | 2227-9067 |
| language | English |
| last_indexed | 2024-03-11T05:08:36Z |
| publishDate | 2023-03-01 |
| publisher | MDPI AG |
| record_format | Article |
| series | Children |
| spelling | doaj.art-ee92615dc79d4ea49f74232f28ac98862023-11-17T18:45:29ZengMDPI AGChildren2227-90672023-03-0110463110.3390/children10040631Anesthetic Management and Bispectral Index in a Child with Miller–Dieker Syndrome: A Case ReportSang Jin Park0Jongyoon Baek1Suyoun Chun2Eun Kyung Choi3Department of Anesthesiology and Pain Medicine, Yeungnam University College of Medicine, Daegu 42415, Republic of KoreaDepartment of Anesthesiology and Pain Medicine, Yeungnam University College of Medicine, Daegu 42415, Republic of KoreaDepartment of Anesthesiology and Pain Medicine, Yeungnam University College of Medicine, Daegu 42415, Republic of KoreaDepartment of Anesthesiology and Pain Medicine, Yeungnam University College of Medicine, Daegu 42415, Republic of KoreaMiller–Dieker syndrome (MDS) is a genetic disorder characterized by classic lissencephaly, distinctive facial features, intellectual disability, seizures, and early death. The anesthetic management of patients with MDS should focus on airway manipulation with the risk of potentially difficult intubation, seizure control due to lissencephaly, and any other clinical complications. Herein, we report a case of anesthetic management in a child with MDS and describe relevant clinical features in a perioperative anesthetic setting. This case highlights the importance of difficult airway manipulation using a videolaryngoscope, seizure management with regard to anesthetics use, and the low validity of BIS monitoring in patients with MDS.https://www.mdpi.com/2227-9067/10/4/631Miller–Dieker syndromelissencephalybispectral indexdifficult airwayepilepsy |
| spellingShingle | Sang Jin Park Jongyoon Baek Suyoun Chun Eun Kyung Choi Anesthetic Management and Bispectral Index in a Child with Miller–Dieker Syndrome: A Case Report Children Miller–Dieker syndrome lissencephaly bispectral index difficult airway epilepsy |
| title | Anesthetic Management and Bispectral Index in a Child with Miller–Dieker Syndrome: A Case Report |
| title_full | Anesthetic Management and Bispectral Index in a Child with Miller–Dieker Syndrome: A Case Report |
| title_fullStr | Anesthetic Management and Bispectral Index in a Child with Miller–Dieker Syndrome: A Case Report |
| title_full_unstemmed | Anesthetic Management and Bispectral Index in a Child with Miller–Dieker Syndrome: A Case Report |
| title_short | Anesthetic Management and Bispectral Index in a Child with Miller–Dieker Syndrome: A Case Report |
| title_sort | anesthetic management and bispectral index in a child with miller dieker syndrome a case report |
| topic | Miller–Dieker syndrome lissencephaly bispectral index difficult airway epilepsy |
| url | https://www.mdpi.com/2227-9067/10/4/631 |
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