Advances in the Diagnosis, Treatment and Prognosis of Lymphangioleiomyomatosis
Lymphangioleiomyomatosis (LAM) is a rare, multisystemic, low-grade neoplasm character-ized by diffuse cystic lesions in the lung.In recent years, emerging imaging examination such as 68Ga-NEB PET-CT scan provides efficient and precise non-invasive diagnostic methods to detect lymphatic circulation a...
| Main Authors: | , , , , , , , , |
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| Format: | Article |
| Language: | zho |
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Editorial Office of Journal of Rare Diseases
2022-01-01
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| Series: | 罕见病研究 |
| Subjects: | |
| Online Access: | https://jrd.chard.org.cn/article/doi/10.12376/j.issn.2097-0501.2022.01.007 |
| _version_ | 1797369835524456448 |
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| author | CHENG Chongsheng LIU Song YANG Yanli HOU Guozhu CHENH Wuying ZHANG Tengyue HU Danjing TIAN Xinlun XU Kaifeng |
| author_facet | CHENG Chongsheng LIU Song YANG Yanli HOU Guozhu CHENH Wuying ZHANG Tengyue HU Danjing TIAN Xinlun XU Kaifeng |
| author_sort | CHENG Chongsheng |
| collection | DOAJ |
| description | Lymphangioleiomyomatosis (LAM) is a rare, multisystemic, low-grade neoplasm character-ized by diffuse cystic lesions in the lung.In recent years, emerging imaging examination such as 68Ga-NEB PET-CT scan provides efficient and precise non-invasive diagnostic methods to detect lymphatic circulation abnormalities in LAM patients. The long-term efficacy and safety of sirolimus for LAM has accumulated further evidence, and genetic profiling studies have unveiled more information of genetic mechanisms. Prognosis of LAM has been much improved. We briefly reviewed the research advances of LAM in China and other countires. |
| first_indexed | 2024-03-08T17:52:38Z |
| format | Article |
| id | doaj.art-f020358105574bb0948269dfacaab995 |
| institution | Directory Open Access Journal |
| issn | 2097-0501 |
| language | zho |
| last_indexed | 2024-03-08T17:52:38Z |
| publishDate | 2022-01-01 |
| publisher | Editorial Office of Journal of Rare Diseases |
| record_format | Article |
| series | 罕见病研究 |
| spelling | doaj.art-f020358105574bb0948269dfacaab9952024-01-02T07:19:31ZzhoEditorial Office of Journal of Rare Diseases罕见病研究2097-05012022-01-0111384410.12376/j.issn.2097-0501.2022.01.007Advances in the Diagnosis, Treatment and Prognosis of LymphangioleiomyomatosisCHENG ChongshengLIU SongYANG YanliHOU GuozhuCHENH WuyingZHANG TengyueHU DanjingTIAN XinlunXU KaifengLymphangioleiomyomatosis (LAM) is a rare, multisystemic, low-grade neoplasm character-ized by diffuse cystic lesions in the lung.In recent years, emerging imaging examination such as 68Ga-NEB PET-CT scan provides efficient and precise non-invasive diagnostic methods to detect lymphatic circulation abnormalities in LAM patients. The long-term efficacy and safety of sirolimus for LAM has accumulated further evidence, and genetic profiling studies have unveiled more information of genetic mechanisms. Prognosis of LAM has been much improved. We briefly reviewed the research advances of LAM in China and other countires.https://jrd.chard.org.cn/article/doi/10.12376/j.issn.2097-0501.2022.01.007lymphangioleiomyomatosisdiagnosistreatment |
| spellingShingle | CHENG Chongsheng LIU Song YANG Yanli HOU Guozhu CHENH Wuying ZHANG Tengyue HU Danjing TIAN Xinlun XU Kaifeng Advances in the Diagnosis, Treatment and Prognosis of Lymphangioleiomyomatosis 罕见病研究 lymphangioleiomyomatosis diagnosis treatment |
| title | Advances in the Diagnosis, Treatment and Prognosis of Lymphangioleiomyomatosis |
| title_full | Advances in the Diagnosis, Treatment and Prognosis of Lymphangioleiomyomatosis |
| title_fullStr | Advances in the Diagnosis, Treatment and Prognosis of Lymphangioleiomyomatosis |
| title_full_unstemmed | Advances in the Diagnosis, Treatment and Prognosis of Lymphangioleiomyomatosis |
| title_short | Advances in the Diagnosis, Treatment and Prognosis of Lymphangioleiomyomatosis |
| title_sort | advances in the diagnosis treatment and prognosis of lymphangioleiomyomatosis |
| topic | lymphangioleiomyomatosis diagnosis treatment |
| url | https://jrd.chard.org.cn/article/doi/10.12376/j.issn.2097-0501.2022.01.007 |
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