Pseudohemangioma of the head - diagnostic difficulties in a pediatric patient with Ewing’s sarcoma of the scalp: case report

Introduction: Ewing’s sarcoma (ES) is the second most common malignant bone tumor of childhood and adolescence. Typically, ES affects the long bones, pelvis and the trunk. Primary location in the scalp is rare. Aim of study: The aim of our study is to focus on the case of a pediatric patient with E...

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Main Authors: Joanna Urszula Borowik, Kinga Justyna Kuśmierczuk, Wojciech Brodowski, Katarzyna Anna Kozak, Patryk Jawoszek, Agnieszka Zaucha-Prażmo
Format: Article
Language:English
Published: Kazimierz Wielki University 2019-09-01
Series:Journal of Education, Health and Sport
Subjects:
Online Access:http://www.ojs.ukw.edu.pl/index.php/johs/article/view/7455
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author Joanna Urszula Borowik
Kinga Justyna Kuśmierczuk
Wojciech Brodowski
Katarzyna Anna Kozak
Patryk Jawoszek
Agnieszka Zaucha-Prażmo
author_facet Joanna Urszula Borowik
Kinga Justyna Kuśmierczuk
Wojciech Brodowski
Katarzyna Anna Kozak
Patryk Jawoszek
Agnieszka Zaucha-Prażmo
author_sort Joanna Urszula Borowik
collection DOAJ
description Introduction: Ewing’s sarcoma (ES) is the second most common malignant bone tumor of childhood and adolescence. Typically, ES affects the long bones, pelvis and the trunk. Primary location in the scalp is rare. Aim of study: The aim of our study is to focus on the case of a pediatric patient with Ewing's sarcoma located in the scalp, which adopted a cavernous angioma mask, and to assess the available knowledge on the diagnosis and treatment of the extracostal ES located in the scalp. Material and methods: The research method was a case study. The research material was the patient's medical record, and the technique used was an analysis. An unsystematic review of Polish and English-language scientific literature was conducted. Electronic databases: PubMed, SCOPUS and Google Scholar were searched using the keywords: sarcoma, Ewing, hemangioma, pseudohemangioma, the head, the scalp. Results: When the girl was 6 months old, a tubercle appeared on her head. It was asymptomatic, but gradually increased. Imaging studies suggested the diagnosis of cavernous hemangioma. The tumor did not respond to treatment and still was growing. A decision was made to include resection. The upward tumor underwent histopathology with immunohistochemical assessment and genetic testing. The result pointed to extraskeletal Ewing’s sarcoma. Conclusions: Despite the few cases described in the literature, remember about atypical locations of primary Ewing sarcoma such as scalp. Making the right diagnosis was a challenge for the multi-specialist team of doctors. Histopathological examination supplemented by immunohistochemical assessment and genetic testing gave a definitive diagnosis and enabled proper treatment.
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spelling doaj.art-f07f74dd344e4eb182214b5a9f2317c92022-12-22T03:06:33ZengKazimierz Wielki UniversityJournal of Education, Health and Sport2391-83062019-09-019951352510.5281/zenodo.34170646553Pseudohemangioma of the head - diagnostic difficulties in a pediatric patient with Ewing’s sarcoma of the scalp: case reportJoanna Urszula Borowik0Kinga Justyna Kuśmierczuk1Wojciech Brodowski2Katarzyna Anna Kozak3Patryk Jawoszek4Agnieszka Zaucha-Prażmo5Students’ Research Group at the Department of Hematology, Oncology and Pediatric Transplantology, Medical University of Lublin, Profesor Antoni Gębala Street 6, 20-093 LublinStudents’ Research Group at the Department of Hematology, Oncology and Pediatric Transplantology, Medical University of Lublin, Profesor Antoni Gębala Street 6, 20-093 LublinStudents’ Research Group at the Department of Hematology, Oncology and Pediatric Transplantology, Medical University of Lublin, Profesor Antoni Gębala Street 6, 20-093 LublinStudents’ Research Group at the Department of Hematology, Oncology and Pediatric Transplantology, Medical University of Lublin, Profesor Antoni Gębala Street 6, 20-093 LublinStudents’ Research Group at the Department of Hematology, Oncology and Pediatric Transplantology, Medical University of Lublin, Profesor Antoni Gębala Street 6, 20-093 LublinDepartment of Hematology, Oncology and Pediatric Transplantology, Medical University of Lublin, Profesor Antoni Gębala Street 6, 20-093 LublinIntroduction: Ewing’s sarcoma (ES) is the second most common malignant bone tumor of childhood and adolescence. Typically, ES affects the long bones, pelvis and the trunk. Primary location in the scalp is rare. Aim of study: The aim of our study is to focus on the case of a pediatric patient with Ewing's sarcoma located in the scalp, which adopted a cavernous angioma mask, and to assess the available knowledge on the diagnosis and treatment of the extracostal ES located in the scalp. Material and methods: The research method was a case study. The research material was the patient's medical record, and the technique used was an analysis. An unsystematic review of Polish and English-language scientific literature was conducted. Electronic databases: PubMed, SCOPUS and Google Scholar were searched using the keywords: sarcoma, Ewing, hemangioma, pseudohemangioma, the head, the scalp. Results: When the girl was 6 months old, a tubercle appeared on her head. It was asymptomatic, but gradually increased. Imaging studies suggested the diagnosis of cavernous hemangioma. The tumor did not respond to treatment and still was growing. A decision was made to include resection. The upward tumor underwent histopathology with immunohistochemical assessment and genetic testing. The result pointed to extraskeletal Ewing’s sarcoma. Conclusions: Despite the few cases described in the literature, remember about atypical locations of primary Ewing sarcoma such as scalp. Making the right diagnosis was a challenge for the multi-specialist team of doctors. Histopathological examination supplemented by immunohistochemical assessment and genetic testing gave a definitive diagnosis and enabled proper treatment.http://www.ojs.ukw.edu.pl/index.php/johs/article/view/7455sarcomaewinghemangiomapseudohemangiomathe headthe scalp
spellingShingle Joanna Urszula Borowik
Kinga Justyna Kuśmierczuk
Wojciech Brodowski
Katarzyna Anna Kozak
Patryk Jawoszek
Agnieszka Zaucha-Prażmo
Pseudohemangioma of the head - diagnostic difficulties in a pediatric patient with Ewing’s sarcoma of the scalp: case report
Journal of Education, Health and Sport
sarcoma
ewing
hemangioma
pseudohemangioma
the head
the scalp
title Pseudohemangioma of the head - diagnostic difficulties in a pediatric patient with Ewing’s sarcoma of the scalp: case report
title_full Pseudohemangioma of the head - diagnostic difficulties in a pediatric patient with Ewing’s sarcoma of the scalp: case report
title_fullStr Pseudohemangioma of the head - diagnostic difficulties in a pediatric patient with Ewing’s sarcoma of the scalp: case report
title_full_unstemmed Pseudohemangioma of the head - diagnostic difficulties in a pediatric patient with Ewing’s sarcoma of the scalp: case report
title_short Pseudohemangioma of the head - diagnostic difficulties in a pediatric patient with Ewing’s sarcoma of the scalp: case report
title_sort pseudohemangioma of the head diagnostic difficulties in a pediatric patient with ewing s sarcoma of the scalp case report
topic sarcoma
ewing
hemangioma
pseudohemangioma
the head
the scalp
url http://www.ojs.ukw.edu.pl/index.php/johs/article/view/7455
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