Positive impact of eculizumab therapy on surgery for Budd- Chiari syndrome in a patient with paroxysmal nocturnal hemoglobinuria and a longterm history of thrombosis

Positive impact of eculizumab therapy on surgery for Budd- Chiari syndrome in a patient with paroxysmal nocturnal hemoglobinuria and a longterm history of thrombosis

Paroxysmal nocturnal hemoglobinuria (PNH) is associated with severe end-organ damage and a high risk of thrombosis. Budd- Chiari syndrome, which develops after thrombotic occlusion of major hepatic blood vessels, is relatively common in PNH and has been associated with increased mortality. We report...

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Bibliographic Details
Main Authors: Silvia De-la-Iglesia, Hugo Luzardo, Angelina Lemes, Melissa Torres, Maria Teresa Gómez-Casares, Naylen Cruz, Teresa Molero
Format: Article
Language:English
Published: MDPI AG 2016-09-01
Series:Hematology Reports
Subjects:
Paroxysmal nocturnal haemoglobinuria (PNH)
Budd-Chiari syndrome
thrombosis
eculizumab
surgery
Online Access:http://www.pagepress.org/journals/index.php/hr/article/view/6562

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