The effect of CFTR modulators on a cystic fibrosis patient presenting with recurrent pancreatitis in the absence of respiratory symptoms: a case report

The effect of CFTR modulators on a cystic fibrosis patient presenting with recurrent pancreatitis in the absence of respiratory symptoms: a case report

Abstract Background Cystic fibrosis (CF) is a genetic disorder of the epithelial CFTR apical chloride channel resulting in multi-organ manifestations, including pancreatic exocrine secretion. In the pancreas, CFTR abnormality results in abnormally viscous secretions that obstruct proximal ducts lead...

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Những tác giả chính: J. Dixon Johns, Steven M. Rowe
Định dạng: Bài viết
Ngôn ngữ:English
Được phát hành: BMC 2019-07-01
Loạt:BMC Gastroenterology
Những chủ đề:
Recurrent pancreatitis
Cystic fibrosis
CFTR
Ivacaftor
Pancrelipase
Truy cập trực tuyến:http://link.springer.com/article/10.1186/s12876-019-1044-7

Internet

http://link.springer.com/article/10.1186/s12876-019-1044-7

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