The effect of CFTR modulators on a cystic fibrosis patient presenting with recurrent pancreatitis in the absence of respiratory symptoms: a case report
Abstract Background Cystic fibrosis (CF) is a genetic disorder of the epithelial CFTR apical chloride channel resulting in multi-organ manifestations, including pancreatic exocrine secretion. In the pancreas, CFTR abnormality results in abnormally viscous secretions that obstruct proximal ducts lead...
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格式: | 文件 |
语言: | English |
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BMC
2019-07-01
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丛编: | BMC Gastroenterology |
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在线阅读: | http://link.springer.com/article/10.1186/s12876-019-1044-7 |