Gorlin-Goltz Syndrome – A Rare Case Entity in Young Child
Gorlin-Goltz syndrome (GGS) is an infrequent multisystemic disease with an autosomal dominant trait, which depicted presence of numerous basal cell carcinoma in conjunction with multiorgan abnormalities. This syndrome may be diagnosed early by a dentist by routine radiographic exams in the first dec...
| Main Authors: | , , , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Karolinum Press
2024-02-01
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| Series: | Prague Medical Report |
| Online Access: | https://pmr.lf1.cuni.cz/125/1/0069/ |
| Summary: | Gorlin-Goltz syndrome (GGS) is an infrequent multisystemic disease with an autosomal dominant trait, which depicted presence of numerous basal cell carcinoma in conjunction with multiorgan abnormalities. This syndrome may be diagnosed early by a dentist by routine radiographic exams in the first decade of life, since the keratocystic odontogenic tumour are usually one of the first manifestations of the syndrome. This article includes a case report of the GGS with regard to its history, incidence, etiology, features, investigations, diagnostic criteria, keratocystic odontogenic tumour and treatment modalities. |
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| ISSN: | 1214-6994 2336-2936 |