Primary Epithelial-myoepithelial Carcinoma of Thymus: First Case Report of the World and Literature Review
Objective To analyze the clinical, imaging and pathological features of patients with epithelial-myoepithelial carcinoma(EMC). Methods The data of a patient with primary EMC of the thymus in Peking Union Medical College Hospital was retrospectively analyzed, and the relevant literature was review...
| Main Authors: | , , , , , , , |
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| Format: | Article |
| Language: | zho |
| Published: |
Editorial Office of Medical Journal of Peking Union Medical College Hospital
2022-09-01
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| Series: | Xiehe Yixue Zazhi |
| Subjects: | |
| Online Access: | https://xhyxzz.pumch.cn/en/article/doi/10.12290/xhyxzz.2022-0318 |
| _version_ | 1797996246738141184 |
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| author | WANG Xiang SHAO Yajuan SUN Guibin ZHOU Na ZHEN Hongnan CHEN Jie ZHAO Lin BAI Chunmei |
| author_facet | WANG Xiang SHAO Yajuan SUN Guibin ZHOU Na ZHEN Hongnan CHEN Jie ZHAO Lin BAI Chunmei |
| author_sort | WANG Xiang |
| collection | DOAJ |
| description | Objective To analyze the clinical, imaging and pathological features of patients with epithelial-myoepithelial carcinoma(EMC). Methods The data of a patient with primary EMC of the thymus in Peking Union Medical College Hospital was retrospectively analyzed, and the relevant literature was reviewed. Results The patient was a middle-aged male diagnosed with primary EMC of the thymus, and he was the first case currently reported at home and abroad. Even though the patient received comprehensive treatments including surgery, chemotherapy, radiotherapy and molecular targeted therapy, he still experienced disease progression, with a survival time of 22 months after surgery. Conclusions Primary EMC of the thymus is extremely rare and has atypical clinical manifestations. The diagnosis mainly depends on histopathological examination. Surgery is currently the major treatment and multidisciplinary treatment is very important to prolong the survival time of EMC patients. |
| first_indexed | 2024-04-11T10:14:37Z |
| format | Article |
| id | doaj.art-f23ec2a8db2a4f558ac14f0a17d027b5 |
| institution | Directory Open Access Journal |
| issn | 1674-9081 |
| language | zho |
| last_indexed | 2024-04-11T10:14:37Z |
| publishDate | 2022-09-01 |
| publisher | Editorial Office of Medical Journal of Peking Union Medical College Hospital |
| record_format | Article |
| series | Xiehe Yixue Zazhi |
| spelling | doaj.art-f23ec2a8db2a4f558ac14f0a17d027b52022-12-22T04:30:00ZzhoEditorial Office of Medical Journal of Peking Union Medical College HospitalXiehe Yixue Zazhi1674-90812022-09-0113586487010.12290/xhyxzz.2022-0318Primary Epithelial-myoepithelial Carcinoma of Thymus: First Case Report of the World and Literature ReviewWANG Xiang0SHAO Yajuan1SUN Guibin2ZHOU Na3ZHEN Hongnan4CHEN Jie5ZHAO Lin6BAI Chunmei7Department of Medical Oncology, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences & Peking Union Medical College, Beijing 100730, ChinaDepartment of Medical Oncology, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences & Peking Union Medical College, Beijing 100730, ChinaDepartment of Medical Oncology, Beijing Puren Hospital, Beijing 100062, ChinaDepartment of Medical Oncology, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences & Peking Union Medical College, Beijing 100730, ChinaDepartment of Radiology, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences & Peking Union Medical College, Beijing 100730, ChinaDepartment of Pathology, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences & Peking Union Medical College, Beijing 100730, ChinaDepartment of Medical Oncology, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences & Peking Union Medical College, Beijing 100730, ChinaDepartment of Medical Oncology, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences & Peking Union Medical College, Beijing 100730, ChinaObjective To analyze the clinical, imaging and pathological features of patients with epithelial-myoepithelial carcinoma(EMC). Methods The data of a patient with primary EMC of the thymus in Peking Union Medical College Hospital was retrospectively analyzed, and the relevant literature was reviewed. Results The patient was a middle-aged male diagnosed with primary EMC of the thymus, and he was the first case currently reported at home and abroad. Even though the patient received comprehensive treatments including surgery, chemotherapy, radiotherapy and molecular targeted therapy, he still experienced disease progression, with a survival time of 22 months after surgery. Conclusions Primary EMC of the thymus is extremely rare and has atypical clinical manifestations. The diagnosis mainly depends on histopathological examination. Surgery is currently the major treatment and multidisciplinary treatment is very important to prolong the survival time of EMC patients.https://xhyxzz.pumch.cn/en/article/doi/10.12290/xhyxzz.2022-0318epithelial-myoepithelial carcinomaprimary disease of thymusrare disease |
| spellingShingle | WANG Xiang SHAO Yajuan SUN Guibin ZHOU Na ZHEN Hongnan CHEN Jie ZHAO Lin BAI Chunmei Primary Epithelial-myoepithelial Carcinoma of Thymus: First Case Report of the World and Literature Review Xiehe Yixue Zazhi epithelial-myoepithelial carcinoma primary disease of thymus rare disease |
| title | Primary Epithelial-myoepithelial Carcinoma of Thymus: First Case Report of the World and Literature Review |
| title_full | Primary Epithelial-myoepithelial Carcinoma of Thymus: First Case Report of the World and Literature Review |
| title_fullStr | Primary Epithelial-myoepithelial Carcinoma of Thymus: First Case Report of the World and Literature Review |
| title_full_unstemmed | Primary Epithelial-myoepithelial Carcinoma of Thymus: First Case Report of the World and Literature Review |
| title_short | Primary Epithelial-myoepithelial Carcinoma of Thymus: First Case Report of the World and Literature Review |
| title_sort | primary epithelial myoepithelial carcinoma of thymus first case report of the world and literature review |
| topic | epithelial-myoepithelial carcinoma primary disease of thymus rare disease |
| url | https://xhyxzz.pumch.cn/en/article/doi/10.12290/xhyxzz.2022-0318 |
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