Left Ventricular Non-Compaction Associated with WPW Syndrome

Noncompaction of the ventricular myocardium is an embryonic cardiomyopathy that is increasingly being recognized. Noncompaction of LV myocardium, right ventricular myocardium, or both can occur in isolation, in congenital heart diseases, in valvular heart diseases, in neuromuscular disorders, skelet...

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Main Authors: Maryam Esmaeilzadeh, Rozita Jalalian, ParidokhtNakhostin Davari
Format: Article
Language:English
Published: Tehran University of Medical Sciences 2006-04-01
Series:Journal of Tehran University Heart Center
Subjects:
Online Access:https://jthc.tums.ac.ir/index.php/jthc/article/view/20
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author Maryam Esmaeilzadeh
Rozita Jalalian
ParidokhtNakhostin Davari
author_facet Maryam Esmaeilzadeh
Rozita Jalalian
ParidokhtNakhostin Davari
author_sort Maryam Esmaeilzadeh
collection DOAJ
description Noncompaction of the ventricular myocardium is an embryonic cardiomyopathy that is increasingly being recognized. Noncompaction of LV myocardium, right ventricular myocardium, or both can occur in isolation, in congenital heart diseases, in valvular heart diseases, in neuromuscular disorders, skeletal abnormalities and in endocrinologic abnormalities. Clinical manifestations of ventricular non-compaction include congestive heart failure, arrhythmia, sudden cardiac death and embolic events. This report is illustrative of non-compaction left ventricle associated with WPW syndrome in a 12-year-old girl presented with aborted sudden cardiac death and heart failure.
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2008-2371
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spelling doaj.art-f278214a838e4945a10781f49090153d2022-12-22T03:18:32ZengTehran University of Medical SciencesJournal of Tehran University Heart Center1735-86202008-23712006-04-011218Left Ventricular Non-Compaction Associated with WPW SyndromeMaryam Esmaeilzadeh0Rozita Jalalian1ParidokhtNakhostin Davari2Shahid Rajaei Cardiovascular Medical Center, Iran University of Medical Sciences, Tehran, Iran.Shahid Rajaei Cardiovascular Medical Center, Iran University of Medical Sciences, Tehran, Iran.Shahid Rajaei Cardiovascular Medical Center, Iran University of Medical Sciences, Tehran, Iran.Noncompaction of the ventricular myocardium is an embryonic cardiomyopathy that is increasingly being recognized. Noncompaction of LV myocardium, right ventricular myocardium, or both can occur in isolation, in congenital heart diseases, in valvular heart diseases, in neuromuscular disorders, skeletal abnormalities and in endocrinologic abnormalities. Clinical manifestations of ventricular non-compaction include congestive heart failure, arrhythmia, sudden cardiac death and embolic events. This report is illustrative of non-compaction left ventricle associated with WPW syndrome in a 12-year-old girl presented with aborted sudden cardiac death and heart failure.https://jthc.tums.ac.ir/index.php/jthc/article/view/20EchocardiographyLeft ventricular non-compactionWPW syndrome
spellingShingle Maryam Esmaeilzadeh
Rozita Jalalian
ParidokhtNakhostin Davari
Left Ventricular Non-Compaction Associated with WPW Syndrome
Journal of Tehran University Heart Center
Echocardiography
Left ventricular non-compaction
WPW syndrome
title Left Ventricular Non-Compaction Associated with WPW Syndrome
title_full Left Ventricular Non-Compaction Associated with WPW Syndrome
title_fullStr Left Ventricular Non-Compaction Associated with WPW Syndrome
title_full_unstemmed Left Ventricular Non-Compaction Associated with WPW Syndrome
title_short Left Ventricular Non-Compaction Associated with WPW Syndrome
title_sort left ventricular non compaction associated with wpw syndrome
topic Echocardiography
Left ventricular non-compaction
WPW syndrome
url https://jthc.tums.ac.ir/index.php/jthc/article/view/20
work_keys_str_mv AT maryamesmaeilzadeh leftventricularnoncompactionassociatedwithwpwsyndrome
AT rozitajalalian leftventricularnoncompactionassociatedwithwpwsyndrome
AT paridokhtnakhostindavari leftventricularnoncompactionassociatedwithwpwsyndrome