Pediatric granular cell tumor of vulva: A rare benign tumor

We present a rare case of a school-aged girl with granular cell tumor of the vulva. The patient presented with a right labial swelling of unknown duration. Initial diagnostic workup with ultrasound suggested a gonadal structure in the right labia, which was read as ovarian herniation through the Can...

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Main Authors: Shannon M. Howard, Bhairav Shah, Kristl V. Tomlin
Format: Article
Language:English
Published: Elsevier 2021-01-01
Series:Journal of Pediatric Surgery Case Reports
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2213576620303511
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author Shannon M. Howard
Bhairav Shah
Kristl V. Tomlin
author_facet Shannon M. Howard
Bhairav Shah
Kristl V. Tomlin
author_sort Shannon M. Howard
collection DOAJ
description We present a rare case of a school-aged girl with granular cell tumor of the vulva. The patient presented with a right labial swelling of unknown duration. Initial diagnostic workup with ultrasound suggested a gonadal structure in the right labia, which was read as ovarian herniation through the Canal of Nuck into the right labia majora. Given concerns for a concurrent Mullerian dysgenesis syndrome predisposing the patient to ovarian herniation, the patient was scheduled for a diagnostic laparoscopy and hernia repair with possible excision of vulvar mass. Laparoscopy revealed normal reproductive anatomy with two visualized normal appearing pelvic ovaries. Subsequent excision of the mass was determined to be granular cell tumor by pathology. There are fewer than 20 reported cases of pediatric vulvar granular cell tumors in the literature and no reports of granular cell tumors presenting as ovarian structure on imaging. This case highlights the importance of including this rare tumor in the differential diagnosis for vulvar mass which may be misread as ovary on ultrasound.
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spelling doaj.art-f2e4c99b9df647c993f35e8fa8f9aa752022-12-21T18:53:14ZengElsevierJournal of Pediatric Surgery Case Reports2213-57662021-01-0164101717Pediatric granular cell tumor of vulva: A rare benign tumorShannon M. Howard0Bhairav Shah1Kristl V. Tomlin2University of South Carolina School of Medicine, MS4, USA; Corresponding author.University of South Carolina School of Medicine/Prisma Health Midlands, Dept of Pediatric Surgery, USAUniversity of South Carolina School of Medicine/Prisma Health Midlands, Dept of OBGYN, USAWe present a rare case of a school-aged girl with granular cell tumor of the vulva. The patient presented with a right labial swelling of unknown duration. Initial diagnostic workup with ultrasound suggested a gonadal structure in the right labia, which was read as ovarian herniation through the Canal of Nuck into the right labia majora. Given concerns for a concurrent Mullerian dysgenesis syndrome predisposing the patient to ovarian herniation, the patient was scheduled for a diagnostic laparoscopy and hernia repair with possible excision of vulvar mass. Laparoscopy revealed normal reproductive anatomy with two visualized normal appearing pelvic ovaries. Subsequent excision of the mass was determined to be granular cell tumor by pathology. There are fewer than 20 reported cases of pediatric vulvar granular cell tumors in the literature and no reports of granular cell tumors presenting as ovarian structure on imaging. This case highlights the importance of including this rare tumor in the differential diagnosis for vulvar mass which may be misread as ovary on ultrasound.http://www.sciencedirect.com/science/article/pii/S2213576620303511Granular cell tumorVulvar massGranular cell myoblastomaAbrikossof tumor
spellingShingle Shannon M. Howard
Bhairav Shah
Kristl V. Tomlin
Pediatric granular cell tumor of vulva: A rare benign tumor
Journal of Pediatric Surgery Case Reports
Granular cell tumor
Vulvar mass
Granular cell myoblastoma
Abrikossof tumor
title Pediatric granular cell tumor of vulva: A rare benign tumor
title_full Pediatric granular cell tumor of vulva: A rare benign tumor
title_fullStr Pediatric granular cell tumor of vulva: A rare benign tumor
title_full_unstemmed Pediatric granular cell tumor of vulva: A rare benign tumor
title_short Pediatric granular cell tumor of vulva: A rare benign tumor
title_sort pediatric granular cell tumor of vulva a rare benign tumor
topic Granular cell tumor
Vulvar mass
Granular cell myoblastoma
Abrikossof tumor
url http://www.sciencedirect.com/science/article/pii/S2213576620303511
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