Purely extradural spinal nerve root hemangioblastomas
Spinal nerve root hemangioblastomas present mostly as intradural-extradurally. Purely extradural spinal nerve root hemangioblastoma is a very rare entity. In this study, we aimed to analyze epidemiological perspectives of purely extradural spinal nerve root hemangioblastomas presented in English med...
| Main Authors: | , , , , , , |
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2016-01-01
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| Series: | Journal of Craniovertebral Junction and Spine |
| Subjects: | |
| Online Access: | http://www.jcvjs.com/article.asp?issn=0974-8237;year=2016;volume=7;issue=4;spage=197;epage=200;aulast=Aytar |
| _version_ | 1818151472684072960 |
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| author | Murat Hamit Aytar Ulaş Yener Murat Sakir Ekşi Behram Kaya Serdar Özgen Aydin Sav Ahmet Alanay |
| author_facet | Murat Hamit Aytar Ulaş Yener Murat Sakir Ekşi Behram Kaya Serdar Özgen Aydin Sav Ahmet Alanay |
| author_sort | Murat Hamit Aytar |
| collection | DOAJ |
| description | Spinal nerve root hemangioblastomas present mostly as intradural-extradurally. Purely extradural spinal nerve root hemangioblastoma is a very rare entity. In this study, we aimed to analyze epidemiological perspectives of purely extradural spinal nerve root hemangioblastomas presented in English medical literature in addition to our own exemplary case. PubMed/MEDLINE was searched using the terms “hemangioblastoma,” “extradural,” “spinal,” and “nerve root.” Demographical variables of age, gender, concomitant presence of von Hippel–Lindau (VHL) disease; spinal imaging and/or intraoperative findings for tumor location were surveyed from retrieved articles. There are 38 patients with purely extradural spinal nerve root hemangioblastoma. The median age is 45 years (range = 24–72 years). Female:male ratio is 0.6. Spinal levels for purely extradural spinal nerve root hemangioblastomas, in order of decreasing frequency, are thoracic (48.6%), cervical (13.5%), lumbar (13.5%), lumbosacral (10.8%), sacral (8.1%), and thoracolumbar (5.4%). Concomitant presence of VHL disease is 45%. Purely extradural spinal nerve root hemangioblastomas are very rare and can be confused with other more common extradural spinal cord tumors. Concomitant presence of VHL disease is observed in less than half of the patients with purely extradural spinal nerve root hemangioblastomas. Surgery is the first-line treatment in these tumors. |
| first_indexed | 2024-12-11T13:39:22Z |
| format | Article |
| id | doaj.art-f33c62c30f2140c4b7c9507fec7313f0 |
| institution | Directory Open Access Journal |
| issn | 0974-8237 |
| language | English |
| last_indexed | 2024-12-11T13:39:22Z |
| publishDate | 2016-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Journal of Craniovertebral Junction and Spine |
| spelling | doaj.art-f33c62c30f2140c4b7c9507fec7313f02022-12-22T01:04:51ZengWolters Kluwer Medknow PublicationsJournal of Craniovertebral Junction and Spine0974-82372016-01-017419720010.4103/0974-8237.193255Purely extradural spinal nerve root hemangioblastomasMurat Hamit AytarUlaş YenerMurat Sakir EkşiBehram KayaSerdar ÖzgenAydin SavAhmet AlanaySpinal nerve root hemangioblastomas present mostly as intradural-extradurally. Purely extradural spinal nerve root hemangioblastoma is a very rare entity. In this study, we aimed to analyze epidemiological perspectives of purely extradural spinal nerve root hemangioblastomas presented in English medical literature in addition to our own exemplary case. PubMed/MEDLINE was searched using the terms “hemangioblastoma,” “extradural,” “spinal,” and “nerve root.” Demographical variables of age, gender, concomitant presence of von Hippel–Lindau (VHL) disease; spinal imaging and/or intraoperative findings for tumor location were surveyed from retrieved articles. There are 38 patients with purely extradural spinal nerve root hemangioblastoma. The median age is 45 years (range = 24–72 years). Female:male ratio is 0.6. Spinal levels for purely extradural spinal nerve root hemangioblastomas, in order of decreasing frequency, are thoracic (48.6%), cervical (13.5%), lumbar (13.5%), lumbosacral (10.8%), sacral (8.1%), and thoracolumbar (5.4%). Concomitant presence of VHL disease is 45%. Purely extradural spinal nerve root hemangioblastomas are very rare and can be confused with other more common extradural spinal cord tumors. Concomitant presence of VHL disease is observed in less than half of the patients with purely extradural spinal nerve root hemangioblastomas. Surgery is the first-line treatment in these tumors.http://www.jcvjs.com/article.asp?issn=0974-8237;year=2016;volume=7;issue=4;spage=197;epage=200;aulast=AytarExtradural; hemangioblastoma; spine; surgery; von Hippel–Lindau. |
| spellingShingle | Murat Hamit Aytar Ulaş Yener Murat Sakir Ekşi Behram Kaya Serdar Özgen Aydin Sav Ahmet Alanay Purely extradural spinal nerve root hemangioblastomas Journal of Craniovertebral Junction and Spine Extradural; hemangioblastoma; spine; surgery; von Hippel–Lindau. |
| title | Purely extradural spinal nerve root hemangioblastomas |
| title_full | Purely extradural spinal nerve root hemangioblastomas |
| title_fullStr | Purely extradural spinal nerve root hemangioblastomas |
| title_full_unstemmed | Purely extradural spinal nerve root hemangioblastomas |
| title_short | Purely extradural spinal nerve root hemangioblastomas |
| title_sort | purely extradural spinal nerve root hemangioblastomas |
| topic | Extradural; hemangioblastoma; spine; surgery; von Hippel–Lindau. |
| url | http://www.jcvjs.com/article.asp?issn=0974-8237;year=2016;volume=7;issue=4;spage=197;epage=200;aulast=Aytar |
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