Occult Spontaneous Ocular Perforation Presenting as Conjunctival Chemosis in a Patient with Marfan’s Syndrome
We report a case of occult spontaneous ocular perforation presenting as conjunctival chemosis in a patient with Marfan’s syndrome (MFS). A 38-year-old female with MFS presented with bilateral conjunctival chemosis since 6 months. Best-corrected visual acuity was 20/20 in both eyes. On slit-lamp exam...
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| Format: | Article |
| Language: | English |
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Karger Publishers
2019-10-01
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| Series: | Case Reports in Ophthalmology |
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| Online Access: | https://www.karger.com/Article/FullText/503440 |
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| author | Nafsika Voulgari Clarice Giacuzzo Ann Schalenbourg George D. Kymionis |
| author_facet | Nafsika Voulgari Clarice Giacuzzo Ann Schalenbourg George D. Kymionis |
| author_sort | Nafsika Voulgari |
| collection | DOAJ |
| description | We report a case of occult spontaneous ocular perforation presenting as conjunctival chemosis in a patient with Marfan’s syndrome (MFS). A 38-year-old female with MFS presented with bilateral conjunctival chemosis since 6 months. Best-corrected visual acuity was 20/20 in both eyes. On slit-lamp examination, a diffuse conjunctival chemosis was observed in both eyes without any signs of ocular hypotony (decreased visual acuity, low intraocular pressure, shallow anterior chamber, pupil distortion, hypotony maculopathy, and chorioretinal folds). Anterior-segment optical coherence tomography revealed a corneoscleral fistula at the left nasal limbus, without any similar finding in the right eye. A scleral patch was performed at the site of the perforation. At 3 month’s follow-up, the left chemosis had regressed, with a stable best-corrected visual acuity in both eyes. However, on ultrasound biomicroscopy, another fistula at the right superior limbus was found, and the patient was referred for treatment with a scleral patch. In conclusion,conjunctival chemosis in a patient with MFS should raise the suspicion of an occult spontaneous ocular perforation. |
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| id | doaj.art-f666e100f7094d8f90b9da4517c085c0 |
| institution | Directory Open Access Journal |
| issn | 1663-2699 |
| language | English |
| last_indexed | 2024-04-13T01:43:33Z |
| publishDate | 2019-10-01 |
| publisher | Karger Publishers |
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| series | Case Reports in Ophthalmology |
| spelling | doaj.art-f666e100f7094d8f90b9da4517c085c02022-12-22T03:08:07ZengKarger PublishersCase Reports in Ophthalmology1663-26992019-10-0110334434810.1159/000503440503440Occult Spontaneous Ocular Perforation Presenting as Conjunctival Chemosis in a Patient with Marfan’s SyndromeNafsika VoulgariClarice GiacuzzoAnn SchalenbourgGeorge D. KymionisWe report a case of occult spontaneous ocular perforation presenting as conjunctival chemosis in a patient with Marfan’s syndrome (MFS). A 38-year-old female with MFS presented with bilateral conjunctival chemosis since 6 months. Best-corrected visual acuity was 20/20 in both eyes. On slit-lamp examination, a diffuse conjunctival chemosis was observed in both eyes without any signs of ocular hypotony (decreased visual acuity, low intraocular pressure, shallow anterior chamber, pupil distortion, hypotony maculopathy, and chorioretinal folds). Anterior-segment optical coherence tomography revealed a corneoscleral fistula at the left nasal limbus, without any similar finding in the right eye. A scleral patch was performed at the site of the perforation. At 3 month’s follow-up, the left chemosis had regressed, with a stable best-corrected visual acuity in both eyes. However, on ultrasound biomicroscopy, another fistula at the right superior limbus was found, and the patient was referred for treatment with a scleral patch. In conclusion,conjunctival chemosis in a patient with MFS should raise the suspicion of an occult spontaneous ocular perforation.https://www.karger.com/Article/FullText/503440occult ocular perforationconjunctival chemosismarfan’s syndrome |
| spellingShingle | Nafsika Voulgari Clarice Giacuzzo Ann Schalenbourg George D. Kymionis Occult Spontaneous Ocular Perforation Presenting as Conjunctival Chemosis in a Patient with Marfan’s Syndrome Case Reports in Ophthalmology occult ocular perforation conjunctival chemosis marfan’s syndrome |
| title | Occult Spontaneous Ocular Perforation Presenting as Conjunctival Chemosis in a Patient with Marfan’s Syndrome |
| title_full | Occult Spontaneous Ocular Perforation Presenting as Conjunctival Chemosis in a Patient with Marfan’s Syndrome |
| title_fullStr | Occult Spontaneous Ocular Perforation Presenting as Conjunctival Chemosis in a Patient with Marfan’s Syndrome |
| title_full_unstemmed | Occult Spontaneous Ocular Perforation Presenting as Conjunctival Chemosis in a Patient with Marfan’s Syndrome |
| title_short | Occult Spontaneous Ocular Perforation Presenting as Conjunctival Chemosis in a Patient with Marfan’s Syndrome |
| title_sort | occult spontaneous ocular perforation presenting as conjunctival chemosis in a patient with marfan s syndrome |
| topic | occult ocular perforation conjunctival chemosis marfan’s syndrome |
| url | https://www.karger.com/Article/FullText/503440 |
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