Congenital maxillomandibular fusion: Case series and review of the literature congenital syngnathia treatment approach
Congenital fusion of maxilla and mandible is a rare anomaly of uncertain etiology. It is broadly divided into two categories i.e. synechiae (soft tissue fusion) and synganthia (bony fusion). It has been proposed that defective stapedial artery during gestation or loss of neural crest cells may be ma...
| Main Authors: | , , , , , , , , , |
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| Format: | Article |
| Language: | English |
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Elsevier
2022-04-01
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| Series: | Advances in Oral and Maxillofacial Surgery |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S2667147622000012 |
| _version_ | 1828341576272707584 |
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| author | Othman Altuwairgi Abdulsalam Aljabab Ali Makrami Ahmed Alomar Yasir Alturkistany Abu Bakarsharwani Bushra Alhazmi laila layqah Ghufran Alayfan Waleed Baharoon |
| author_facet | Othman Altuwairgi Abdulsalam Aljabab Ali Makrami Ahmed Alomar Yasir Alturkistany Abu Bakarsharwani Bushra Alhazmi laila layqah Ghufran Alayfan Waleed Baharoon |
| author_sort | Othman Altuwairgi |
| collection | DOAJ |
| description | Congenital fusion of maxilla and mandible is a rare anomaly of uncertain etiology. It is broadly divided into two categories i.e. synechiae (soft tissue fusion) and synganthia (bony fusion). It has been proposed that defective stapedial artery during gestation or loss of neural crest cells may be major contributing factors, yet exact pathogenesis is still unknown. Surgery is the preferred mode of treatment but associated with high recurrence rates. Few cases involving the fusion of the mandible to the zygomatic complex have been reported. Herein, we present a series of 3patients with complete maxillomandibular syngnathia and hypoplastic mandible managed surgically at two local hospitals in Saudi Arabia. |
| first_indexed | 2024-04-13T23:15:46Z |
| format | Article |
| id | doaj.art-f7e5c19a54e74c0a92ada0532003ea2c |
| institution | Directory Open Access Journal |
| issn | 2667-1476 |
| language | English |
| last_indexed | 2024-04-13T23:15:46Z |
| publishDate | 2022-04-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Advances in Oral and Maxillofacial Surgery |
| spelling | doaj.art-f7e5c19a54e74c0a92ada0532003ea2c2022-12-22T02:25:26ZengElsevierAdvances in Oral and Maxillofacial Surgery2667-14762022-04-016100251Congenital maxillomandibular fusion: Case series and review of the literature congenital syngnathia treatment approachOthman Altuwairgi0Abdulsalam Aljabab1Ali Makrami2Ahmed Alomar3Yasir Alturkistany4Abu Bakarsharwani5Bushra Alhazmi6laila layqah7Ghufran Alayfan8Waleed Baharoon9Maryland University, Maryland Baltimore, USA; Alfiysal University & Post- Graduate Director for OMFS, Riyadh, Saudi Arabia; Consultant of Oral and Maxillofacial Surgery&Aesthetic and Reconstruction Surgery, National Guard Health Affairs, Riyadh, Saudi Arabia; Corresponding author. Maryland University, Maryland Baltimore, USA.Consultant of Oral and Maxillofacial Surgery& Head and Neck Surgical Oncology, King Fahad Medical City, Riyadh, Saudi ArabiaConsultant of Oral and Maxillofacial Surgery, King Fahad Central Hospital, Jazan, Saudi ArabiaAssistant Consultant of Oral and Maxillofacial Surgery, King Khalid University Hospital, Riyadh, Saudi ArabiaConsultant of Oral and Maxillofacial Surgery & Microvascular Reconstructive Head and Neck Surgery, King Fahad Medical City, Riyadh, Saudi ArabiaConsultant of Oral and Maxillofacial Surgery, King Fahad Central Hospital, Jazan, Saudi ArabiaCollege of Medicine, King Saud Bin Abdulaziz University for Health Sciences, Riyadh, Saudi ArabiaKing Abdullah International Medical Research Center, 1Ministry of National Guard-Health Affairs, Riyadh, Saudi ArabiaCollege of Dentistry, Princess Nourah Bint Abdulrahman University, Riyadh, Saudi ArabiaCollege of Dentistry, King Saud Bin Abdulaziz University for Health Sciences, Riyadh, Saudi ArabiaCongenital fusion of maxilla and mandible is a rare anomaly of uncertain etiology. It is broadly divided into two categories i.e. synechiae (soft tissue fusion) and synganthia (bony fusion). It has been proposed that defective stapedial artery during gestation or loss of neural crest cells may be major contributing factors, yet exact pathogenesis is still unknown. Surgery is the preferred mode of treatment but associated with high recurrence rates. Few cases involving the fusion of the mandible to the zygomatic complex have been reported. Herein, we present a series of 3patients with complete maxillomandibular syngnathia and hypoplastic mandible managed surgically at two local hospitals in Saudi Arabia.http://www.sciencedirect.com/science/article/pii/S2667147622000012MaxillomandibularCongenitalSyngnathia |
| spellingShingle | Othman Altuwairgi Abdulsalam Aljabab Ali Makrami Ahmed Alomar Yasir Alturkistany Abu Bakarsharwani Bushra Alhazmi laila layqah Ghufran Alayfan Waleed Baharoon Congenital maxillomandibular fusion: Case series and review of the literature congenital syngnathia treatment approach Advances in Oral and Maxillofacial Surgery Maxillomandibular Congenital Syngnathia |
| title | Congenital maxillomandibular fusion: Case series and review of the literature congenital syngnathia treatment approach |
| title_full | Congenital maxillomandibular fusion: Case series and review of the literature congenital syngnathia treatment approach |
| title_fullStr | Congenital maxillomandibular fusion: Case series and review of the literature congenital syngnathia treatment approach |
| title_full_unstemmed | Congenital maxillomandibular fusion: Case series and review of the literature congenital syngnathia treatment approach |
| title_short | Congenital maxillomandibular fusion: Case series and review of the literature congenital syngnathia treatment approach |
| title_sort | congenital maxillomandibular fusion case series and review of the literature congenital syngnathia treatment approach |
| topic | Maxillomandibular Congenital Syngnathia |
| url | http://www.sciencedirect.com/science/article/pii/S2667147622000012 |
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